about
The glucose-6-phosphatase systemHistidine 167 is the phosphate acceptor in glucose-6-phosphatase-beta forming a phosphohistidine enzyme intermediate during catalysisGlycogen storage disease type I and G6Pase-β deficiency: etiology and therapyA potential new role for muscle in blood glucose homeostasisBone marrow-derived cells require a functional glucose 6-phosphate transporter for normal myeloid functionsCloning and characterization of cDNAs encoding a candidate glycogen storage disease type 1b protein in rodentsEfficient large-scale generation of functional hepatocytes from mouse embryonic stem cells grown in a rotating bioreactor with exogenous growth factors and hormonesNew lessons in the regulation of glucose metabolism taught by the glucose 6-phosphatase system.Three novel mutations of the G6PC gene identified in Chinese patients with glycogen storage disease type IaAdenovirus-mediated gene therapy in a mouse model of glycogen storage disease type 1a.Recombinant AAV-directed gene therapy for type I glycogen storage diseases.A detailed characterization of the adult mouse model of glycogen storage disease Ia.Impaired neutrophil activity and increased susceptibility to bacterial infection in mice lacking glucose-6-phosphatase-beta.Neutrophil stress and apoptosis underlie myeloid dysfunction in glycogen storage disease type IbAngiotensin mediates renal fibrosis in the nephropathy of glycogen storage disease type IaMutations in the glucose-6-phosphatase-alpha (G6PC) gene that cause type Ia glycogen storage diseaseGene therapy for type I glycogen storage diseasesGlucose-6-phosphate transporter gene therapy corrects metabolic and myeloid abnormalities in glycogen storage disease type Ib mice.Neutrophilia and elevated serum cytokines are implicated in glycogen storage disease type Ia.Necrotic foci, elevated chemokines and infiltrating neutrophils in the liver of glycogen storage disease type Ia.Generation of mice with a conditional allele for G6pc.The upstream enhancer elements of the G6PC promoter are critical for optimal G6PC expression in murine glycogen storage disease type Ia.Mouse A6-positive hepatic oval cells derived from embryonic stem cells.A population of c-Kit(low)(CD45/TER119)- hepatic cell progenitors of 11-day postcoitus mouse embryo liver reconstitutes cell-depleted liver organoids.Long-term correction of murine glycogen storage disease type Ia by recombinant adeno-associated virus-1-mediated gene transfer.A glucose-6-phosphate hydrolase, widely expressed outside the liver, can explain age-dependent resolution of hypoglycemia in glycogen storage disease type Ia.High-ratio differentiation of embryonic stem cells into hepatocytes in vitro.Hepatocyte-like cells from directed differentiation of mouse bone marrow cells in vitro.New primary culture systems to study the differentiation and proliferation of mouse fetal hepatoblasts.
P2860
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P2860
description
1998 nî lūn-bûn
@nan
1998年の論文
@ja
1998年学术文章
@wuu
1998年学术文章
@zh
1998年学术文章
@zh-cn
1998年学术文章
@zh-hans
1998年学术文章
@zh-my
1998年学术文章
@zh-sg
1998年學術文章
@yue
1998年學術文章
@zh-hant
name
Ontogeny of the murine glucose-6-phosphatase system.
@en
Ontogeny of the murine glucose-6-phosphatase system.
@nl
type
label
Ontogeny of the murine glucose-6-phosphatase system.
@en
Ontogeny of the murine glucose-6-phosphatase system.
@nl
prefLabel
Ontogeny of the murine glucose-6-phosphatase system.
@en
Ontogeny of the murine glucose-6-phosphatase system.
@nl
P2093
P356
P1476
Ontogeny of the murine glucose-6-phosphatase system.
@en
P2093
P356
10.1006/ABBI.1998.0849
P407
P577
1998-10-01T00:00:00Z