A pool of extramitochondrial frataxin that promotes cell survival
about
Characterization of the human HSC20, an unusual DnaJ type III protein, involved in iron-sulfur cluster biogenesisIn vivo maturation of human frataxinIron-dependent regulation of frataxin expression: implications for treatment of Friedreich ataxiaHuman iron-sulfur cluster assembly, cellular iron homeostasis, and diseaseFriedreich's Ataxia: A Neuronal Point of View on the Oxidative Stress HypothesisOverexpression of frataxin in the mitochondria increases resistance to oxidative stress and extends lifespan in DrosophilaCell biology. Metabolic control of cell deathFrataxin is essential for extramitochondrial Fe-S cluster proteins in mammalian tissuesDyclonine rescues frataxin deficiency in animal models and buccal cells of patients with Friedreich's ataxia.The in vivo mitochondrial two-step maturation of human frataxin.Iron-binding activity of human iron-sulfur cluster assembly protein hIscA1Friedreich ataxia: molecular mechanisms, redox considerations, and therapeutic opportunities.Erythropoiesis and iron sulfur cluster biogenesis.Novel frataxin isoforms may contribute to the pathological mechanism of Friedreich ataxiaIron-sulfur cluster biogenesis and human diseaseFriedreich ataxia: failure of GABA-ergic and glycinergic synaptic transmission in the dentate nucleus.Frataxin participates to the hypoxia-induced response in tumorsThe pathogenesis of cardiomyopathy in Friedreich ataxia.Highly specific ubiquitin-competing molecules effectively promote frataxin accumulation and partially rescue the aconitase defect in Friedreich ataxia cells.Frataxin Is Localized to Both the Chloroplast and Mitochondrion and Is Involved in Chloroplast Fe-S Protein Function in ArabidopsisCaenorhabditis elegans as a model system to study intercompartmental proteostasis: Interrelation of mitochondrial function, longevity, and neurodegenerative diseases.Autophagy induction extends lifespan and reduces lipid content in response to frataxin silencing in C. elegans.Advancements in the pathophysiology of Friedreich's Ataxia and new prospects for treatments.Dorsal root ganglia in Friedreich ataxia: satellite cell proliferation and inflammation.Mitochondrial localization of human frataxin is necessary but processing is not for rescuing frataxin deficiency in Trypanosoma brucei.Friedreich ataxia: new pathways.The neuropathology of late-onset Friedreich's ataxia.Mutations in LYRM4, encoding iron-sulfur cluster biogenesis factor ISD11, cause deficiency of multiple respiratory chain complexesE3 Ligase RNF126 Directly Ubiquitinates Frataxin, Promoting Its Degradation: Identification of a Potential Therapeutic Target for Friedreich Ataxia.Iron-dependent functions of mitochondria--relation to neurodegeneration.Frataxin knockdown causes loss of cytoplasmic iron-sulfur cluster functions, redox alterations and induction of heme transcripts.Frataxin, a conserved mitochondrial protein, in the hydrogenosome of Trichomonas vaginalis.Friedreich Ataxia: Developmental Failure of the Dorsal Root Entry Zone.Iron-Sulfur Protein Assembly in Human Cells.Src inhibitors modulate frataxin protein levels.Distinct iron binding property of two putative iron donors for the iron-sulfur cluster assembly: IscA and the bacterial frataxin ortholog CyaY under physiological and oxidative stress conditions.Drosophila melanogaster Models of Friedreich's Ataxia.
P2860
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P2860
A pool of extramitochondrial frataxin that promotes cell survival
description
2006 nî lūn-bûn
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2006 թուականի Յունիսին հրատարակուած գիտական յօդուած
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2006 թվականի հունիսին հրատարակված գիտական հոդված
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2006年の論文
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2006年学术文章
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2006年学术文章
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2006年学术文章
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2006年学术文章
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2006年学术文章
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2006年學術文章
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name
A pool of extramitochondrial frataxin that promotes cell survival
@ast
A pool of extramitochondrial frataxin that promotes cell survival
@en
A pool of extramitochondrial frataxin that promotes cell survival
@en-gb
A pool of extramitochondrial frataxin that promotes cell survival
@nl
type
label
A pool of extramitochondrial frataxin that promotes cell survival
@ast
A pool of extramitochondrial frataxin that promotes cell survival
@en
A pool of extramitochondrial frataxin that promotes cell survival
@en-gb
A pool of extramitochondrial frataxin that promotes cell survival
@nl
prefLabel
A pool of extramitochondrial frataxin that promotes cell survival
@ast
A pool of extramitochondrial frataxin that promotes cell survival
@en
A pool of extramitochondrial frataxin that promotes cell survival
@en-gb
A pool of extramitochondrial frataxin that promotes cell survival
@nl
P2860
P50
P3181
P356
P1476
A pool of extramitochondrial frataxin that promotes cell survival
@en
P2093
Barbara Tomassini
Roberto Testi
P2860
P304
16750-16756
P3181
P356
10.1074/JBC.M511960200
P407
P577
2006-04-11T00:00:00Z