The cardiolipin transacylase, tafazzin, associates with two distinct respiratory components providing insight into Barth syndrome
about
Acyl coenzyme A thioesterase Them5/Acot15 is involved in cardiolipin remodeling and fatty liver developmentMaking heads or tails of phospholipids in mitochondriaCharacterization of tafazzin splice variants from humans and fruit fliesCardiolipin membrane domains in prokaryotes and eukaryotesSuccessful management of Barth syndrome: a systematic review highlighting the importance of a flexible and multidisciplinary approachDeacylation on the matrix side of the mitochondrial inner membrane regulates cardiolipin remodeling.The genetic interactome of prohibitins: coordinated control of cardiolipin and phosphatidylethanolamine by conserved regulators in mitochondria.LPS impairs oxygen utilization in epithelia by triggering degradation of the mitochondrial enzyme Alcat1Cardiolipin fingerprinting of leukocytes by MALDI-TOF/MS as a screening tool for Barth syndromeDefining functional classes of Barth syndrome mutation in humansBiosynthesis, remodeling and turnover of mitochondrial cardiolipinCardiolipin remodeling: a regulatory hub for modulating cardiolipin metabolism and functionThe complexity of cardiolipin in health and diseaseThe topology and regulation of cardiolipin biosynthesis and remodeling in yeastCardiolipin, a critical determinant of mitochondrial carrier protein assembly and function.Barth syndrome mutations that cause tafazzin complex lability.Mitochondrial cardiolipin involved in outer-membrane protein biogenesis: implications for Barth syndrome.Yeast as a system for modeling mitochondrial disease mechanisms and discovering therapies.Yeast Coq9 controls deamination of coenzyme Q intermediates that derive from para-aminobenzoic acid.Saccharomyces cerevisiae porin pore forms complexes with mitochondrial outer membrane proteins Om14p and Om45pTafazzins from Drosophila and mammalian cells assemble in large protein complexes with a short half-life.New clinical and molecular insights on Barth syndromeSeven functional classes of Barth syndrome mutationThe physical state of lipid substrates provides transacylation specificity for tafazzinThe role of cardiolipin in the structural organization of mitochondrial membranes.The power of yeast to model diseases of the powerhouse of the cell.The Taz1p transacylase is imported and sorted into the outer mitochondrial membrane via a membrane anchor domain.Unremodeled and remodeled cardiolipin are functionally indistinguishable in yeast.Formation and regulation of mitochondrial membranes.The clinical maze of mitochondrial neurologyNew developments on the functions of coenzyme Q in mitochondria.ORP5/ORP8 localize to endoplasmic reticulum-mitochondria contacts and are involved in mitochondrial function.Interaction of MDM33 with mitochondrial inner membrane homeostasis pathways in yeast.The mitochondrial quality control protein Yme1 is necessary to prevent defective mitophagy in a yeast model of Barth syndrome.Mitochondria influence CDR1 efflux pump activity, Hog1-mediated oxidative stress pathway, iron homeostasis, and ergosterol levels in Candida albicans.Deletion of the cardiolipin-specific phospholipase Cld1 rescues growth and life span defects in the tafazzin mutant: implications for Barth syndrome.Overexpression of mitochondrial oxodicarboxylate carrier (ODC1) preserves oxidative phosphorylation in a yeast model of Barth syndrome.Tafazzin knockdown causes hypertrophy of neonatal ventricular myocytes.Barth syndrome cardiomyopathy.Conserved Lipid and Small-Molecule Modulation of COQ8 Reveals Regulation of the Ancient Kinase-like UbiB Family.
P2860
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P2860
The cardiolipin transacylase, tafazzin, associates with two distinct respiratory components providing insight into Barth syndrome
description
2008 nî lūn-bûn
@nan
2008 թուականի Դեկտեմբերին հրատարակուած գիտական յօդուած
@hyw
2008 թվականի դեկտեմբերին հրատարակված գիտական հոդված
@hy
2008年の論文
@ja
2008年論文
@yue
2008年論文
@zh-hant
2008年論文
@zh-hk
2008年論文
@zh-mo
2008年論文
@zh-tw
2008年论文
@wuu
name
The cardiolipin transacylase, ...... ng insight into Barth syndrome
@ast
The cardiolipin transacylase, ...... ng insight into Barth syndrome
@en
The cardiolipin transacylase, ...... ng insight into Barth syndrome
@nl
type
label
The cardiolipin transacylase, ...... ng insight into Barth syndrome
@ast
The cardiolipin transacylase, ...... ng insight into Barth syndrome
@en
The cardiolipin transacylase, ...... ng insight into Barth syndrome
@nl
prefLabel
The cardiolipin transacylase, ...... ng insight into Barth syndrome
@ast
The cardiolipin transacylase, ...... ng insight into Barth syndrome
@en
The cardiolipin transacylase, ...... ng insight into Barth syndrome
@nl
P2093
P2860
P356
P1476
The cardiolipin transacylase, ...... ng insight into Barth syndrome
@en
P2093
Carla M Koehler
J Michael McCaffery
Joseph A Loo
Pinmanee Boontheung
Steven M Claypool
P2860
P304
P356
10.1091/MBC.E08-09-0896
P407
P577
2008-12-01T00:00:00Z