Whirlin, a cytoskeletal scaffolding protein, stabilizes the paranodal region and axonal cytoskeleton in myelinated axons
about
The PDZ-domain protein Whirlin facilitates mechanosensory signaling in mammalian proprioceptorsA study of whirlin isoforms in the mouse vestibular system suggests potential vestibular dysfunction in DFNB31-deficient patientsUsher syndrome: Hearing loss, retinal degeneration and associated abnormalities.Postnatal Loss of Neuronal and Glial Neurofascins Differentially Affects Node of Ranvier Maintenance and Myelinated Axon Function.Gene Therapy Restores Balance and Auditory Functions in a Mouse Model of Usher Syndrome.Regulation of synaptic development and function by the Drosophila PDZ protein Dyschronic.MALDI imaging mass spectrometry to investigate endogenous peptides in an animal model of Usher's disease.Axonal domain disorganization in Caspr1 and Caspr2 mutant myelinated axons affects neuromuscular junction integrity, leading to muscle atrophy.Whirlin increases TRPV1 channel expression and cellular stabilityEarly and Late Loss of the Cytoskeletal Scaffolding Protein, Ankyrin G Reveals Its Role in Maturation and Maintenance of Nodes of Ranvier in Myelinated Axons.Activity-dependent formation and location of voltage-gated sodium channel clusters at a CNS nerve terminal during postnatal development.Simultaneous Ablation of Neuronal Neurofascin and Ankyrin G in Young and Adult Mice Reveals Age-Dependent Increase in Nodal Stability in Myelinated Axons and Differential Effects on the Lifespan.
P2860
Q28257430-257E8CD5-6149-4A7A-9507-E01FEFE1F1CBQ30367896-11E8C702-B789-4B99-A241-0B913091EEF9Q30389509-43A49BA2-7B4B-4B18-90D9-8F2140854839Q30837291-B5629ADE-05FD-47A8-A1B8-C2B570E30719Q34552548-256CF044-637D-4DCF-BA73-D6311AA9247DQ34999362-94FE2810-C7A9-4479-A367-03DBA4852964Q35171092-F2AE2D22-1FDE-4DA7-991C-B908FED0FB53Q38859584-97FAA4F9-FDE5-414C-81EE-7DC877BF7FF6Q41468748-1F4FCB5A-7A48-4740-B6DF-76FCACF81218Q42010808-DA4F35AC-9B6A-44B2-8A92-D5C42EA9D1CCQ48434298-7228F136-C990-4766-BA5B-09FA75DFAAE2Q55360507-6E37AB43-8C58-490C-82C4-52C5FD2B08C0
P2860
Whirlin, a cytoskeletal scaffolding protein, stabilizes the paranodal region and axonal cytoskeleton in myelinated axons
description
2013 թուականի Սեպտեմբերին հրատարակուած գիտական յօդուած
@hyw
2013 թվականի սեպտեմբերին հրատարակված գիտական հոդված
@hy
artículu científicu espublizáu en 2013
@ast
scientific journal article
@en
vedecký článok (publikovaný 2013/09/06)
@sk
vědecký článek publikovaný v roce 2013
@cs
wetenschappelijk artikel (gepubliceerd op 2013/09/06)
@nl
наукова стаття, опублікована у вересні 2013
@uk
مقالة علمية (نشرت في 6-9-2013)
@ar
name
Whirlin, a cytoskeletal scaffo ...... toskeleton in myelinated axons
@ast
Whirlin, a cytoskeletal scaffo ...... toskeleton in myelinated axons
@en
Whirlin, a cytoskeletal scaffo ...... toskeleton in myelinated axons
@nl
type
label
Whirlin, a cytoskeletal scaffo ...... toskeleton in myelinated axons
@ast
Whirlin, a cytoskeletal scaffo ...... toskeleton in myelinated axons
@en
Whirlin, a cytoskeletal scaffo ...... toskeleton in myelinated axons
@nl
prefLabel
Whirlin, a cytoskeletal scaffo ...... toskeleton in myelinated axons
@ast
Whirlin, a cytoskeletal scaffo ...... toskeleton in myelinated axons
@en
Whirlin, a cytoskeletal scaffo ...... toskeleton in myelinated axons
@nl
P2093
P2860
P921
P356
P1433
P1476
Whirlin, a cytoskeletal scaffo ...... toskeleton in myelinated axons
@en
P2093
Bechara Kachar
James A Green
P2860
P2888
P356
10.1186/1471-2202-14-96
P577
2013-09-06T00:00:00Z
P5875
P6179
1009128445