Association of dystrophin-related protein with dystrophin-associated proteins in mdx mouse muscle
about
A method of utrophin up-regulation through RNAi-mediated knockdown of the transcription factor EN1Voltage-gated ion channel dysfunction precedes cardiomyopathy development in the dystrophic heartHypernitrosylated ryanodine receptor calcium release channels are leaky in dystrophic muscleSyntrophin binds to an alternatively spliced exon of dystrophinCloning of human basic A1, a distinct 59-kDa dystrophin-associated protein encoded on chromosome 8q23-24Increasing complexity of the dystrophin-associated protein complexA high-coverage genome sequence from an archaic Denisovan individualThe dystroglycan complex is necessary for stabilization of acetylcholine receptor clusters at neuromuscular junctions and formation of the synaptic basement membraneBrain dystrophin-glycoprotein complex: persistent expression of beta-dystroglycan, impaired oligomerization of Dp71 and up-regulation of utrophins in animal models of muscular dystrophyThe biochemical and mass spectrometric profiling of the dystrophin complexome from skeletal muscleThe potential of sarcospan in adhesion complex replacement therapeutics for the treatment of muscular dystrophyProteomic profiling of the dystrophin-deficient mdx phenocopy of dystrophinopathy-associated cardiomyopathyHanging on for the ride: adhesion to the extracellular matrix mediates cellular responses in skeletal muscle morphogenesis and diseaseDifferential targeting of components of the dystrophin complex to the postsynaptic membraneIdentification of alpha-syntrophin binding to syntrophin triplet, dystrophin, and utrophinAssociation of aciculin with dystrophin and utrophinA role of dystroglycan in schwannoma cell adhesion to lamininDystroglycan is a binding protein of laminin and merosin in peripheral nerveAbsence of alpha 7 integrin in dystrophin-deficient mice causes a myopathy similar to Duchenne muscular dystrophyCytoplasmic gamma-actin expression in diverse animal models of muscular dystrophyExpression of agrin, dystroglycan, and utrophin in normal renal tissue and in experimental glomerulopathiesDrug discovery for Duchenne muscular dystrophy via utrophin promoter activation screeningIdentification of new dystroglycan complexes in skeletal muscleMetabolic dysfunction and altered mitochondrial dynamics in the utrophin-dystrophin deficient mouse model of duchenne muscular dystrophyLocalization of cranin (dystroglycan) at sites of cell-matrix and cell-cell contact: recruitment to focal adhesions is dependent upon extracellular ligandsIsolation and characterization of distinct domains of sarcolemma and T-tubules from rat skeletal muscleIdentification of Dp71 isoforms in the platelet membrane cytoskeleton. Potential role in thrombin-mediated platelet adhesionDifferential targeting of components of the dystrophin complex to the postsynaptic membraneMicroutrophin delivery through rAAV6 increases lifespan and improves muscle function in dystrophic dystrophin/utrophin-deficient miceTranscriptional and functional differences in stem cell populations isolated from extraocular and limb muscles.Ets-2 repressor factor silences extrasynaptic utrophin by N-box mediated repression in skeletal muscle.Skeletal muscle-specific ablation of gamma(cyto)-actin does not exacerbate the mdx phenotype.Blastocyst injection of wild type embryonic stem cells induces global corrections in mdx mice.High levels of sarcospan are well tolerated and act as a sarcolemmal stabilizer to address skeletal muscle and pulmonary dysfunction in DMD.Chronic administration of membrane sealant prevents severe cardiac injury and ventricular dilatation in dystrophic dogs.Utrophin binds laterally along actin filaments and can couple costameric actin with sarcolemma when overexpressed in dystrophin-deficient muscle.Plasma membrane cytoskeleton of muscle: a fine structural analysis.Dystrophin and utrophin: genetic analyses of their role in skeletal muscle.Regulation and functional significance of utrophin expression at the mammalian neuromuscular synapse.Differential requirement for utrophin in the induced pluripotent stem cell correction of muscle versus fat in muscular dystrophy mice.
P2860
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P2860
Association of dystrophin-related protein with dystrophin-associated proteins in mdx mouse muscle
description
1992 թուականի Դեկտեմբերին հրատարակուած գիտական յօդուած
@hyw
1992 թվականի դեկտեմբերին հրատարակված գիտական հոդված
@hy
article publié dans la revue scientifique Nature
@fr
artículu científicu espublizáu en 1992
@ast
scientific journal article
@en
vedecký článok (publikovaný 1992/12/10)
@sk
vědecký článek publikovaný v roce 1992
@cs
wetenschappelijk artikel (gepubliceerd op 1992/12/10)
@nl
наукова стаття, опублікована в грудні 1992
@uk
مقالة علمية (نشرت في 10-12-1992)
@ar
name
Association of dystrophin-rela ...... d proteins in mdx mouse muscle
@ast
Association of dystrophin-rela ...... d proteins in mdx mouse muscle
@en
Association of dystrophin-rela ...... d proteins in mdx mouse muscle
@nl
type
label
Association of dystrophin-rela ...... d proteins in mdx mouse muscle
@ast
Association of dystrophin-rela ...... d proteins in mdx mouse muscle
@en
Association of dystrophin-rela ...... d proteins in mdx mouse muscle
@nl
prefLabel
Association of dystrophin-rela ...... d proteins in mdx mouse muscle
@ast
Association of dystrophin-rela ...... d proteins in mdx mouse muscle
@en
Association of dystrophin-rela ...... d proteins in mdx mouse muscle
@nl
P2093
P3181
P356
P1433
P1476
Association of dystrophin-rela ...... d proteins in mdx mouse muscle
@en
P2093
J. M. Ervasti
K. Matsumura
K. Ohlendieck
K. P. Campbell
P2888
P304
P3181
P356
10.1038/360588A0
P407
P50
P577
1992-12-10T00:00:00Z
P5875
P6179
1022764889