Lamin B1 mediates cell-autonomous neuropathology in a leukodystrophy mouse model. - sprookjes - yvandenbroek - TriplyDB

Lamin B1 mediates cell-autonomous neuropathology in a leukodystrophy mouse model.

Lamin B1 mediates cell-autonomous neuropathology in a leukodystrophy mouse model.

http://www.wikidata.org/entity/Q30540206

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The nuclear envelope: an intriguing focal point for neurogenetic disease Lamin B1 protein is required for dendrite development in primary mouse cortical neurons Defects of Lipid Synthesis Are Linked to the Age-Dependent Demyelination Caused by Lamin B1 Overexpression MicroRNA-23a promotes myelination in the central nervous system Lamin B1 levels modulate differentiation into neurons during embryonic corticogenesis Nuclear lamins and neurobiology.Nuclear envelope protein MAN1 regulates clock through BMAL1 Do lamin B1 and lamin B2 have redundant functions?A large genomic deletion leads to enhancer adoption by the lamin B1 gene: a second path to autosomal dominant adult-onset demyelinating leukodystrophy (ADLD)The contrasting roles of lamin B1 in cellular aging and human disease Regulation of Myelination in the Central Nervous System by Nuclear Lamin B1 and Non-coding RNAs.Diverse lamin-dependent mechanisms interact to control chromatin dynamics. Focus on laminopathies Nuclear lamina remodelling and its implications for human disease.The unfolded protein response and its potential role in Huntington's disease elucidated by a systems biology approach.Targeting human oligodendrocyte progenitors for myelin repair.Epigenetic control of oligodendrocyte development: adding new players to old keepers.Lamin B1 mediated demyelination: Linking Lamins, Lipids and Leukodystrophies.Messenger RNA processing is altered in autosomal dominant leukodystrophy An LMNB1 Duplication Caused Adult-Onset Autosomal Dominant Leukodystrophy in Chinese Family: Clinical Manifestations, Neuroradiology and Genetic Diagnosis.Nuclear envelopathies: a complex LINC between nuclear envelope and pathology.Neuroproteomic study of nitrated proteins in moderate traumatic brain injured rats treated with gamma glutamyl cysteine ethyl ester administration post injury: Insight into the role of glutathione elevation in nitrosative stress.The DYT6 Dystonia Protein THAP1 Regulates Myelination within the Oligodendrocyte Lineage.Soluble Neuregulin1 Down-Regulates Myelination Genes in Schwann Cells.

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Lamin B1 mediates cell-autonomous neuropathology in a leukodystrophy mouse model.

http://www.wikidata.org/entity/Q30540206

description

2013 nî lūn-bûn

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2013 թուականի Մայիսին հրատարակուած գիտական յօդուած

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2013 թվականի մայիսին հրատարակված գիտական հոդված

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2013年の論文

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2013年論文

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2013年論文

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2013年論文

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2013年論文

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2013年论文

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name

Lamin B1 mediates cell-autonomous neuropathology in a leukodystrophy mouse model.

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Lamin B1 mediates cell-autonomous neuropathology in a leukodystrophy mouse model.

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type

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Lamin B1 mediates cell-autonomous neuropathology in a leukodystrophy mouse model.

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Lamin B1 mediates cell-autonomous neuropathology in a leukodystrophy mouse model.

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Lamin B1 mediates cell-autonomous neuropathology in a leukodystrophy mouse model.

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Lamin B1 mediates cell-autonomous neuropathology in a leukodystrophy mouse model.

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Journal of Clinical Investigation

P1476

Lamin B1 mediates cell-autonomous neuropathology in a leukodystrophy mouse model.

@en

P2093

Jorge J Palop

http://www.w3.org/2001/XMLSchema#string

Louis J Ptáček

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Mary Y Heng

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Quasar S Padiath

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Sherry Kamiya

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Shu-Ting Lin

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Ying Tong

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Ying-Hui Fu

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Yong Huang

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P2860

Lamin B1 is required for mouse development and nuclear integrity

Inhibitory interneuron deficit links altered network activity and cognitive dysfunction in Alzheimer model.

Lamin B1 duplications cause autosomal dominant leukodystrophy

Late-onset neurodegeneration in mice with increased dosage of the proteolipid protein gene

Longitudinal evaluation of the Hdh(CAG)150 knock-in murine model of Huntington's disease

Dysregulation of the Wnt pathway inhibits timely myelination and remyelination in the mammalian CNS

Developments of a water-maze procedure for studying spatial learning in the rat

Control of memory formation through regulated expression of a CaMKII transgene

Nuclear lamins: laminopathies and their role in premature ageing.

Many neuronal and behavioral impairments in transgenic mouse models of Alzheimer's disease are independent of caspase cleavage of the amyloid precursor protein

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2719-2729

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10.1172/JCI66737

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123

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3668844

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