about
Mechanisms of the noxious inflammatory cycle in cystic fibrosisCytoplasmic protein quality control degradation mediated by parallel actions of the E3 ubiquitin ligases Ubr1 and San1Increasing the Endoplasmic Reticulum Pool of the F508del Allele of the Cystic Fibrosis Transmembrane Conductance Regulator Leads to Greater Folding Correction by Small Molecule TherapeuticsThe Lamin B receptor is essential for cholesterol synthesis and perturbed by disease-causing mutationsThe ubiquitin system, disease, and drug discovery.Biological and structural basis for Aha1 regulation of Hsp90 ATPase activity in maintaining proteostasis in the human disease cystic fibrosis.Syntaxin 6 and CAL mediate the degradation of the cystic fibrosis transmembrane conductance regulator.Histone deacetylase inhibitors influence chemotherapy transport by modulating expression and trafficking of a common polymorphic variant of the ABCG2 efflux transporter.A chaperone trap contributes to the onset of cystic fibrosis.mRNA surveillance and endoplasmic reticulum quality control processes alter biogenesis of mutant GABAA receptor subunits associated with genetic epilepsies.Rescue of murine F508del CFTR activity in native intestine by low temperature and proteasome inhibitorsFBXO15 regulates P-glycoprotein/ABCB1 expression through the ubiquitin--proteasome pathway in cancer cells.Making sense of nonsense GABA(A) receptor mutations associated with genetic epilepsies.Novel class of potential therapeutics that target ricin retrograde translocation.Growth-based determination and biochemical confirmation of genetic requirements for protein degradation in Saccharomyces cerevisiaeDefective adenosine-stimulated cAMP production in cystic fibrosis airway epithelia: a novel role for CFTR in cell signaling.Sarcoglycanopathies: molecular pathogenesis and therapeutic prospectsFK506 binding protein 8 peptidylprolyl isomerase activity manages a late stage of cystic fibrosis transmembrane conductance regulator (CFTR) folding and stabilityHallmarks of therapeutic management of the cystic fibrosis functional landscape.A novel approach to recovery of function of mutant proteins by slowing down translation.TorsinA participates in endoplasmic reticulum-associated degradationUnravelling druggable signalling networks that control F508del-CFTR proteostasisCycloheximide Chase Analysis of Protein Degradation in Saccharomyces cerevisiaeTwo molecular pathways (NMD and ERAD) contribute to a genetic epilepsy associated with the GABA(A) receptor GABRA1 PTC mutation, 975delC, S326fs328XThe proteostasis boundary in misfolding diseases of membrane traffic.Peroxisome membrane proteins: multiple trafficking routes and multiple functions?Protein microarrays for the identification of praja1 e3 ubiquitin ligase substrates.Targeting the PI3K/Akt/mTOR signalling pathway in Cystic FibrosisMolecular Pathogenic Basis for GABRG2 Mutations Associated With a Spectrum of Epilepsy Syndromes, From Generalized Absence Epilepsy to Dravet Syndrome.Influence of cell background on pharmacological rescue of mutant CFTR.Control of cellular GADD34 levels by the 26S proteasome.Posttranslational negative regulation of glycosylated and non-glycosylated BCRP expression by Derlin-1.Proteostasis in pediatric pulmonary pathology.Cell Biology. The proteome in balanceThe ER Stress Surveillance (ERSU) pathway regulates daughter cell ER protein aggregate inheritance.Immunohystochemical analysis of CFTR in normal and disrupted spermatogenesis.A systematic atlas of chaperome deregulation topologies across the human cancer landscape.Heritable Skeletal Disorders Arising from Defects in Processing and Transport of Type I Procollagen from the ER: Perspectives on Possible Therapeutic Approaches.A chemical compound inhibiting the Aha1-Hsp90 chaperone complex.Peripheral Protein Quality Control as a Novel Drug Target for CFTR Stabilizer
P2860
Q21284420-5BD581C0-82AA-40C0-A719-40BB9D595D90Q27932129-8447AEDE-E9FE-49F3-AFAC-5FD7EA636DD1Q28554668-8565C04A-13B7-44FE-9AA1-937E18A9FAADQ28829592-2C565205-9EAE-4E13-A53A-D480D191AED0Q33384295-FB2C6AAC-C2CF-4080-B6C7-E7957950C14DQ33721206-CEEA8D74-0DEF-4280-AFF9-2997C2BF8A5FQ33761474-0B03D31E-2C42-4D79-A864-C751D8FAF00CQ34179757-1660BC43-7D05-4D52-BFCC-4026250758DBQ34305005-86E4A104-125C-45E4-9EE1-70246EDC6A6AQ34315858-59E5AF6B-38BC-4D85-8C49-899911276846Q34532897-FFB77FEB-E724-4EB0-B16A-D25770D194E3Q34610210-376CA416-61D5-44A2-9286-9FC0EB1B8F67Q34789999-8637BC65-3826-486E-80BD-3F4A97CA4E4CQ35074948-3A741546-4F28-493B-B8B1-6EDB45448E65Q35162247-DB1059D8-B301-422B-8E91-EC76D1995B2EQ35169502-878AFC2D-8223-420A-8707-3EF3AE5E290EQ35758335-DC9A6851-3B39-46E7-9A61-4B815CC0FD46Q36052432-205A942A-7A4B-469A-8377-75967607A5DEQ36279553-BC2CDFF7-8D22-4C6F-8E4C-76E22ADA8FF6Q36298394-09A7891A-75C6-4F73-B378-FE175018D572Q36487761-37656388-9F6F-4ABF-915B-A5B500013A80Q36568529-72E25CFB-76C9-4F81-A894-74A19D272536Q37087744-80B38C16-1EEC-40D4-A621-EBF3AEE4A297Q37204045-7BD97559-74E9-470A-B99B-333E176CFD43Q37587095-F3937808-B4FE-45A4-9FEB-CB8ECE34C4BAQ38098565-C3423939-2684-42D7-9A09-4E0DC60F2037Q38502781-C027E516-CCC2-4B33-875C-0F14BDD1217EQ38631561-94385041-3C64-4114-9645-34CE697BFB27Q38883198-59F6BEE8-0AA1-43FB-85FF-F45B5488E0EFQ39755118-57F3EDD1-BCF2-4D76-9265-4B1DC4D55EC3Q39939464-ADEB7C68-154A-4760-823A-22D29C48C54DQ42132520-08171A25-290E-48C1-A87A-23D88E85B896Q42429011-9465F9A6-66AD-4A67-AAF3-D052A33525D8Q42573517-CB3FFD35-8E7A-41CC-B780-49C0CCC6DEC9Q42580374-911A5C13-4BC6-4237-87B4-059CA6A79258Q44375903-4261BB15-67FC-4BCC-A178-730946C4CEC1Q47205509-40324A4E-7911-4B54-BE50-372C70D4B177Q47602229-465CE0E4-C646-4EF4-A666-710DC74C78ACQ47886847-5EF0027B-0750-4A93-8E33-58A3B2D01CB3Q57490973-7BEFD621-5ED4-44DA-9A4A-473A2721B15B
P2860
description
2007 nî lūn-bûn
@nan
2007 թուականի Նոյեմբերին հրատարակուած գիտական յօդուած
@hyw
2007 թվականի նոյեմբերին հրատարակված գիտական հոդված
@hy
2007年の論文
@ja
2007年論文
@yue
2007年論文
@zh-hant
2007年論文
@zh-hk
2007年論文
@zh-mo
2007年論文
@zh-tw
2007年论文
@wuu
name
The role of the UPS in cystic fibrosis.
@ast
The role of the UPS in cystic fibrosis.
@en
The role of the UPS in cystic fibrosis.
@nl
type
label
The role of the UPS in cystic fibrosis.
@ast
The role of the UPS in cystic fibrosis.
@en
The role of the UPS in cystic fibrosis.
@nl
prefLabel
The role of the UPS in cystic fibrosis.
@ast
The role of the UPS in cystic fibrosis.
@en
The role of the UPS in cystic fibrosis.
@nl
P2093
P2860
P921
P1433
P1476
The role of the UPS in cystic fibrosis.
@en
P2093
Douglas M Cyr
Emma L Turnbull
Meredith F N Rosser
P2860
P2888
P356
10.1186/1471-2091-8-S1-S11
P478
P5008
P577
2007-11-22T00:00:00Z
P6179
1031810548