Large induces functional glycans in an O-mannosylation dependent manner and targets GlcNAc terminals on alpha-dystroglycan
about
LARGE2 generates the same xylose- and glucuronic acid-containing glycan structures as LARGEAdeno-associated virus-mediated overexpression of LARGE rescues α-dystroglycan function in dystrophic mice with mutations in the fukutin-related protein.Differential glycosylation of α-dystroglycan and proteins other than α-dystroglycan by like-glycosyltransferaseHigh throughput screening for compounds that alter muscle cell glycosylation identifies new role for N-glycans in regulating sarcolemmal protein abundance and laminin bindingIdentification of antithrombin-modulating genes. Role of LARGE, a gene encoding a bifunctional glycosyltransferase, in the secretion of proteins?Identification of mutations in TMEM5 and ISPD as a cause of severe cobblestone lissencephalyLaminins in basement membrane assemblyMissense mutations in β-1,3-N-acetylglucosaminyltransferase 1 (B3GNT1) cause Walker-Warburg syndrome.LARGE2-dependent glycosylation confers laminin-binding ability on proteoglycans.Mammalian O-mannosylation pathway: glycan structures, enzymes, and protein substrates.Second international workshop for glycosylation defects in muscular dystrophies, 11-12 November, 2010, Charlotte, USA.
P2860
Q28591175-7BA0AF15-B2D6-4F72-870F-02B63C12A3E7Q34013566-69E813B0-90CC-4072-BD00-394DBB7E32E0Q34217566-D24DE432-2425-4263-B83C-F2EF75E79763Q34262912-739A2C56-D852-420E-B981-C3AA2E7F8D32Q34738273-24E42774-9518-4190-A5C0-866CE47E0542Q36451494-BAE4DC4A-11BA-4700-A24A-617DC03557C8Q36531811-19502A5A-602F-455C-A1BA-815DD094252AQ36731388-8E3576AB-395F-4468-8836-C37A913BD07BQ37472546-72922C46-21AC-438B-8B1B-D60258C5AE31Q38208557-8FC62512-2CAF-4634-85C5-08BF0F4C4A65Q53154898-13BBE33B-DBD5-4711-ABB5-7A2F259E72A7
P2860
Large induces functional glycans in an O-mannosylation dependent manner and targets GlcNAc terminals on alpha-dystroglycan
description
2011 nî lūn-bûn
@nan
2011 թուականի Փետրուարին հրատարակուած գիտական յօդուած
@hyw
2011 թվականի փետրվարին հրատարակված գիտական հոդված
@hy
2011年の論文
@ja
2011年論文
@yue
2011年論文
@zh-hant
2011年論文
@zh-hk
2011年論文
@zh-mo
2011年論文
@zh-tw
2011年论文
@wuu
name
Large induces functional glyca ...... erminals on alpha-dystroglycan
@ast
Large induces functional glyca ...... erminals on alpha-dystroglycan
@en
type
label
Large induces functional glyca ...... erminals on alpha-dystroglycan
@ast
Large induces functional glyca ...... erminals on alpha-dystroglycan
@en
prefLabel
Large induces functional glyca ...... erminals on alpha-dystroglycan
@ast
Large induces functional glyca ...... erminals on alpha-dystroglycan
@en
P2093
P2860
P1433
P1476
Large induces functional glyca ...... erminals on alpha-dystroglycan
@en
P2093
Xiaohua Wu
Zhi-fang Li
P2860
P304
P356
10.1371/JOURNAL.PONE.0016866
P407
P577
2011-02-09T00:00:00Z