Low levels of Survival Motor Neuron protein are sufficient for normal muscle function in the SMNΔ7 mouse model of SMA.
about
Protective effects of butyrate-based compounds on a mouse model for spinal muscular atrophy.SMN expression is required in motor neurons to rescue electrophysiological deficits in the SMNΔ7 mouse model of SMA.Chronic Treatment with the AMPK Agonist AICAR Prevents Skeletal Muscle Pathology but Fails to Improve Clinical Outcome in a Mouse Model of Severe Spinal Muscular Atrophy.Efficacy and biodistribution analysis of intracerebroventricular administration of an optimized scAAV9-SMN1 vector in a mouse model of spinal muscular atrophy.Cross-disease comparison of amyotrophic lateral sclerosis and spinal muscular atrophy reveals conservation of selective vulnerability but differential neuromuscular junction pathology.Antisense Oligonucleotide-Based Therapy for Neuromuscular Disease.Advances in modeling and treating spinal muscular atrophyA Stem Cell Model of the Motor Circuit Uncouples Motor Neuron Death from Hyperexcitability Induced by SMN Deficiency.
P2860
Q30743508-D8ADA569-5C27-49A1-9C7E-4A070BF97284Q36065456-956CEE26-2F61-4BC2-AB46-2F588A8F7A52Q36484406-26609F92-CF79-4522-BF26-275B0D5F0BA3Q37255468-5038237B-52BF-4ED7-AFFD-9BABCA39DFBAQ37337195-023BA029-FD67-4713-ACC6-D279EBFA963CQ38734734-7D9A6561-9B90-4DC8-BE63-80D3175366E6Q38912516-D7AB1545-C89F-43F6-A60F-982376427604Q41885598-C09ACE15-3E36-407C-9E1B-F532168F44DD
P2860
Low levels of Survival Motor Neuron protein are sufficient for normal muscle function in the SMNΔ7 mouse model of SMA.
description
2015 nî lūn-bûn
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2015年の論文
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2015年学术文章
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2015年学术文章
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2015年学术文章
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name
Low levels of Survival Motor N ...... the SMNΔ7 mouse model of SMA.
@ast
Low levels of Survival Motor N ...... the SMNΔ7 mouse model of SMA.
@en
type
label
Low levels of Survival Motor N ...... the SMNΔ7 mouse model of SMA.
@ast
Low levels of Survival Motor N ...... the SMNΔ7 mouse model of SMA.
@en
prefLabel
Low levels of Survival Motor N ...... the SMNΔ7 mouse model of SMA.
@ast
Low levels of Survival Motor N ...... the SMNΔ7 mouse model of SMA.
@en
P2093
P2860
P356
P1476
Low levels of Survival Motor N ...... the SMNΔ7 mouse model of SMA.
@en
P2093
Chitra C Iyer
Jason D Murray
Kevin D Foust
Phillip G Zaworski
Sara E Gombash
Vicki L McGovern
P2860
P304
P356
10.1093/HMG/DDV332
P577
2015-08-13T00:00:00Z