Evidence for airway surface dehydration as the initiating event in CF airway disease.
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Chloride channels as drug targets.Reduced histone deacetylase 7 activity restores function to misfolded CFTR in cystic fibrosisOptimising inhaled mannitol for cystic fibrosis in an adult populationPotential of metabolomics to reveal Burkholderia cepacia complex pathogenesis and antibiotic resistanceInhaled hypertonic saline for cystic fibrosis: Reviewing the potential evidence for modulation of neutrophil signalling and functionMucus penetrating nanoparticles: biophysical tool and method of drug and gene deliveryCharacterization of defects in ion transport and tissue development in cystic fibrosis transmembrane conductance regulator (CFTR)-knockout ratsOrigins of cystic fibrosis lung diseaseRole of epithelial HCO3⁻ transport in mucin secretion: lessons from cystic fibrosisMuc5b is the major polymeric mucin in mucus from thoroughbred horses with and without airway mucus accumulationAdvances toward the elucidation of hypertonic saline effects on Pseudomonas aeruginosa from cystic fibrosis patientsBarriers to inhaled gene therapy of obstructive lung diseases: A reviewDefective CFTR increases synthesis and mass of sphingolipids that modulate membrane composition and lipid signaling.Heterozygosity for the F508del mutation in the cystic fibrosis transmembrane conductance regulator anion channel attenuates influenza severityVocal fold surface hydration: a review.Conditional deletion of dnaic1 in a murine model of primary ciliary dyskinesia causes chronic rhinosinusitisHuman cervicovaginal mucus contains an activity that hinders HIV-1 movement.Assessing mucociliary transport of single particles in vivo shows variable speed and preference for the ventral trachea in newborn pigsNitrous oxide production in sputum from cystic fibrosis patients with chronic Pseudomonas aeruginosa lung infectionCharacterizing Lung Disease in Cystic Fibrosis with Magnetic Resonance Imaging and Airway Physiology.Unfractionated heparin reduces the elasticity of sputum from patients with cystic fibrosis.A novel approach to analyze gene expression data demonstrates that the DeltaF508 mutation in CFTR downregulates the antigen presentation pathway.Pseudomonas aeruginosa biofilm infections in cystic fibrosis: insights into pathogenic processes and treatment strategies.Neutrophilic inflammation is associated with altered airway hydration in stable asthmaticsPseudomonas infection and mucociliary and absorptive clearance in the cystic fibrosis lung.Cystic fibrosis remodels the regulation of purinergic signaling by NTPDase1 (CD39) and NTPDase3Accumulation of metals in GOLD4 COPD lungs is associated with decreased CFTR levels.Acute inhalation of hypertonic saline does not improve mucociliary clearance in all children with cystic fibrosis.Airway basal stem cells: a perspective on their roles in epithelial homeostasis and remodeling.Denufosol tetrasodium in patients with cystic fibrosis and normal to mildly impaired lung function.A new role for bicarbonate in mucus formation.Inhaled hypertonic saline in infants and children younger than 6 years with cystic fibrosis: the ISIS randomized controlled trial.Altered ion transport by thyroid epithelia from CFTR(-/-) pigs suggests mechanisms for hypothyroidism in cystic fibrosis.State of progress in treating cystic fibrosis respiratory disease.MiR-101 and miR-144 regulate the expression of the CFTR chloride channel in the lungEmergent properties of proteostasis in managing cystic fibrosis.Measuring airway surface liquid depth in ex vivo mouse airways by x-ray imaging for the assessment of cystic fibrosis airway therapies.Rapid transport of muco-inert nanoparticles in cystic fibrosis sputum treated with N-acetyl cysteineDrug carrier nanoparticles that penetrate human chronic rhinosinusitis mucus.Using bacterial biomarkers to identify early indicators of cystic fibrosis pulmonary exacerbation onset
P2860
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P2860
Evidence for airway surface dehydration as the initiating event in CF airway disease.
description
2007 nî lūn-bûn
@nan
2007年の論文
@ja
2007年論文
@yue
2007年論文
@zh-hant
2007年論文
@zh-hk
2007年論文
@zh-mo
2007年論文
@zh-tw
2007年论文
@wuu
2007年论文
@zh
2007年论文
@zh-cn
name
Evidence for airway surface dehydration as the initiating event in CF airway disease.
@ast
Evidence for airway surface dehydration as the initiating event in CF airway disease.
@en
type
label
Evidence for airway surface dehydration as the initiating event in CF airway disease.
@ast
Evidence for airway surface dehydration as the initiating event in CF airway disease.
@en
prefLabel
Evidence for airway surface dehydration as the initiating event in CF airway disease.
@ast
Evidence for airway surface dehydration as the initiating event in CF airway disease.
@en
P1476
Evidence for airway surface dehydration as the initiating event in CF airway disease.
@en
P2093
Boucher RC
P356
10.1111/J.1365-2796.2006.01744.X
P407
P577
2007-01-01T00:00:00Z