Assembly and dynamics of proteins of the longitudinal and junctional sarcoplasmic reticulum in skeletal muscle cells
about
Calsequestrin (CASQ1) rescues function and structure of calcium release units in skeletal muscles of CASQ1-null miceN-WASP is required for Amphiphysin-2/BIN1-dependent nuclear positioning and triad organization in skeletal muscle and is involved in the pathophysiology of centronuclear myopathy.T-tubule biogenesis and triad formation in skeletal muscle and implication in human diseases.Obscurin is required for ankyrinB-dependent dystrophin localization and sarcolemma integrity.Transient receptor potential canonical type 1 (TRPC1) operates as a sarcoplasmic reticulum calcium leak channel in skeletal muscle.Organization of junctional sarcoplasmic reticulum proteins in skeletal muscle fibers.Distinct regions of triadin are required for targeting and retention at the junctional domain of the sarcoplasmic reticulum.The potential of obscurin as a therapeutic target in muscle disorders.Accumulation of STIM1 is associated with the degenerative muscle fibre phenotype in ALS and other neurogenic atrophies.The relationship between form and function throughout the history of excitation-contraction coupling.Transport of the alpha subunit of the voltage gated L-type calcium channel through the sarcoplasmic reticulum occurs prior to localization to triads and requires the beta subunit but not Stac3 in skeletal muscles.A proteolytic cleavage to separate the sarcolemma/T-tubule from the sarcoplasmic reticulum.
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Assembly and dynamics of proteins of the longitudinal and junctional sarcoplasmic reticulum in skeletal muscle cells
description
article científic
@ca
article scientifique
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articolo scientifico
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artigo científico
@pt
bilimsel makale
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scientific article published on 04 March 2009
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vedecký článok
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vetenskaplig artikel
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videnskabelig artikel
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vědecký článek
@cs
name
Assembly and dynamics of prote ...... culum in skeletal muscle cells
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Assembly and dynamics of prote ...... ulum in skeletal muscle cells.
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type
label
Assembly and dynamics of prote ...... culum in skeletal muscle cells
@en
Assembly and dynamics of prote ...... ulum in skeletal muscle cells.
@nl
prefLabel
Assembly and dynamics of prote ...... culum in skeletal muscle cells
@en
Assembly and dynamics of prote ...... ulum in skeletal muscle cells.
@nl
P2860
P356
P1476
Assembly and dynamics of prote ...... culum in skeletal muscle cells
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P2093
Francesca Pampinella
Vincenza Cusimano
P2860
P304
P356
10.1073/PNAS.0810243106
P407
P577
2009-03-04T00:00:00Z