Familial autoinflammation with neutrophilic dermatosis reveals a regulatory mechanism of pyrin activation.
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The cell biology of inflammasomes: Mechanisms of inflammasome activation and regulationPyrin inflammasome activation and RhoA signaling in the autoinflammatory diseases FMF and HIDSPotential of IL-1, IL-18 and Inflammasome Inhibition for the Treatment of Inflammatory Skin Diseases.The discontinuity theory of immunityThe Yersinia pestis Effector YopM Inhibits Pyrin Inflammasome Activation.Autoinflammatory Skin Disorders: The Inflammasomme in Focus.Familial Mediterranean fever mutations lift the obligatory requirement for microtubules in Pyrin inflammasome activation.Monogenic Autoinflammatory Diseases with Mendelian Inheritance: Genes, Mutations, and Genotype/Phenotype Correlations.Geoepidemiology and Immunologic Features of Autoinflammatory Diseases: a Comprehensive Review.Autoinflammatory diseases: update on classification diagnosis and management.The burgeoning field of innate immune-mediated disease and autoinflammation.A motive for killing: effector functions of regulated lytic cell death.Lessons from characterization and treatment of the autoinflammatory syndromes.What do we know about the inflammasome in humans?The NLRP3 and Pyrin Inflammasomes: Implications in the Pathophysiology of Autoinflammatory Diseases.Molecular mechanisms and functions of pyroptosis, inflammatory caspases and inflammasomes in infectious diseases.Mechanisms governing inflammasome activation, assembly and pyroptosis induction.Posttranslational Modification as a Critical Determinant of Cytoplasmic Innate Immune Recognition.Genomics, Biology, and Human Illness: Advances in the Monogenic Autoinflammatory Diseases.The monogenic autoinflammatory diseases define new pathways in human innate immunity and inflammation.A novel Pyrin-Associated Autoinflammation with Neutrophilic Dermatosis mutation further defines 14-3-3 binding of pyrin and distinction to Familial Mediterranean Fever.R202Q/M694V as novel MEFV gene mutations in chronic periodontitis and familial Mediterranean fever.[Role of genetics in familial Mediterranean fever].IL-1β and Caspase-1 Drive Autoinflammatory Disease Independently of IL-1α or Caspase-8 in a Mouse Model of Familial Mediterranean Fever.NLRP3 inflammasome assembly is regulated by phosphorylation of the pyrin domain.The Yersinia Virulence Factor YopM Hijacks Host Kinases to Inhibit Type III Effector-Triggered Activation of the Pyrin Inflammasome.A dRAStic RHOAdblock of Pyrin inflammasome activation.Comprehensive analysis of mutations in the MEFV gene reveal that the location and not the substitution type determines symptom severity in FMF.The intra- and extracellular functions of ASC specks.Inflammasome activation and assembly at a glance.Recent advances in inflammasome biology.Familial Mediterranean fever mutations are hypermorphic mutations that specifically decrease the activation threshold of the Pyrin inflammasome.Activation of the Innate Immune Receptors: Guardians of the Micro Galaxy : Activation and Functions of the Innate Immune Receptors.Vasculitis and vasculitis-like manifestations in monogenic autoinflammatory syndromes.Function and mechanism of the pyrin inflammasome.Novel aspects of the assembly and activation of inflammasomes with focus on the NLRC4 inflammasome.The classification, genetic diagnosis and modelling of monogenic autoinflammatory disordersDynamics of Inflammatory Response in Autoinflammatory Disorders: Autonomous and Hyperinflammatory StatesApoptosis of intestinal epithelial cells restricts Clostridium difficile infection in a model of pseudomembranous colitis
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P2860
Familial autoinflammation with neutrophilic dermatosis reveals a regulatory mechanism of pyrin activation.
description
2016 nî lūn-bûn
@nan
2016年の論文
@ja
2016年学术文章
@wuu
2016年学术文章
@zh-cn
2016年学术文章
@zh-hans
2016年学术文章
@zh-my
2016年学术文章
@zh-sg
2016年學術文章
@yue
2016年學術文章
@zh
2016年學術文章
@zh-hant
name
Familial autoinflammation with ...... mechanism of pyrin activation.
@en
Familial autoinflammation with ...... mechanism of pyrin activation.
@en-gb
type
label
Familial autoinflammation with ...... mechanism of pyrin activation.
@en
Familial autoinflammation with ...... mechanism of pyrin activation.
@en-gb
prefLabel
Familial autoinflammation with ...... mechanism of pyrin activation.
@en
Familial autoinflammation with ...... mechanism of pyrin activation.
@en-gb
P2093
P2860
P50
P6366
P1154
2-s2.0-84962744592
P1476
Familial autoinflammation with ...... mechanism of pyrin activation
@en
P2093
Adrian Liston
Andre Megarbane
Andrew I Webb
Bruno Copin
Emanuela Pasciuto
Emmanuelle Cochet
Fiona Moghaddas
Isabelle Jéru
Josselyn E Garcia-Perez
Julia Ruuth-Praz
P2860
P304
P356
10.1126/SCITRANSLMED.AAF1471
P407
P50
P5530
P577
2016-03-01T00:00:00Z
P5875
P6179
1034917132
P6366
2324425986