Mislocated FUS is sufficient for gain-of-toxic-function amyotrophic lateral sclerosis phenotypes in mice.
about
Motor neuron intrinsic and extrinsic mechanisms contribute to the pathogenesis of FUS-associated amyotrophic lateral sclerosis.ALS-linked FUS exerts a gain of toxic function involving aberrant p38 MAPK activation.Expanding Axonal Transcriptome Brings New Functions for Axonally Synthesized Proteins in Health and Disease.Dendritic Homeostasis Disruption in a Novel Frontotemporal Dementia Mouse Model Expressing Cytoplasmic Fused in Sarcoma.De novo design of RNA-binding proteins with a prion-like domain related to ALS/FTD proteinopathies.RNA binding proteins and the pathological cascade in ALS/FTD neurodegeneration.To the end of the line: Axonal mRNA transport and local translation in health and neurodegenerative disease.Humanized mutant FUS drives progressive motor neuron degeneration without aggregation in 'FUSDelta14' knockin mice.Causative Genes in Amyotrophic Lateral Sclerosis and Protein Degradation Pathways: a Link to Neurodegeneration.Synaptic Paths to Neurodegeneration: The Emerging Role of TDP-43 and FUS in Synaptic Functions.Control of CNS functions by RNA-binding proteins in neurological diseasesgenetically interacts with the ALS-associated orthologue and mediates its toxicity
P2860
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P2860
Mislocated FUS is sufficient for gain-of-toxic-function amyotrophic lateral sclerosis phenotypes in mice.
description
2016 nî lūn-bûn
@nan
2016年の論文
@ja
2016年学术文章
@wuu
2016年学术文章
@zh
2016年学术文章
@zh-cn
2016年学术文章
@zh-hans
2016年学术文章
@zh-my
2016年学术文章
@zh-sg
2016年學術文章
@yue
2016年學術文章
@zh-hant
name
Mislocated FUS is sufficient f ...... sclerosis phenotypes in mice.
@en
Mislocated FUS is sufficient f ...... sclerosis phenotypes in mice.
@nl
type
label
Mislocated FUS is sufficient f ...... sclerosis phenotypes in mice.
@en
Mislocated FUS is sufficient f ...... sclerosis phenotypes in mice.
@nl
prefLabel
Mislocated FUS is sufficient f ...... sclerosis phenotypes in mice.
@en
Mislocated FUS is sufficient f ...... sclerosis phenotypes in mice.
@nl
P2093
P2860
P356
P1433
P1476
Mislocated FUS is sufficient f ...... sclerosis phenotypes in mice.
@en
P2093
Gen Shiihashi
Norihiro Suzuki
Taeko Ebine
Takuya Yagi
Yoshihiro Nihei
P2860
P304
P356
10.1093/BRAIN/AWW161
P407
P50
P577
2016-06-30T00:00:00Z