Targeted disruption of nebulette protein expression alters cardiac myofibril assembly and function
about
Nebulette mutations are associated with dilated cardiomyopathy and endocardial fibroelastosisIdentification of Xin-repeat proteins as novel ligands of the SH3 domains of nebulin and nebulette and analysis of their interaction during myofibril formation and remodelingThe Nebulin family: an actin support groupNebulin binding impedes mutant desmin filament assembly.Nebulette is a powerful cytolinker organizing desmin and actin in mouse heartsLinkage analysis of three families with arrythmogenic right ventricular cardiomyopathy in India.Jasplakinolide reduces actin and tropomyosin dynamics during myofibrillogenesisAlternatively Spliced Homologous Exons Have Ancient Origins and Are Highly Expressed at the Protein Level.Genetics of inherited cardiomyopathies.Nebulette knockout mice have normal cardiac function, but show Z-line widening and up-regulation of cardiac stress markers.α-Actinin2 is required for the lateral alignment of Z discs and ventricular chamber enlargement during zebrafish cardiogenesis.Nebulin regulates the assembly and lengths of the thin filaments in striated muscleMutations in NEBL encoding the cardiac Z-disk protein nebulette are associated with various cardiomyopathies.Altered regional cardiac wall mechanics are associated with differential cardiomyocyte calcium handling due to nebulette mutations in preclinical inherited dilated cardiomyopathy.Assembly and maintenance of the sarcomere night and day.Thin filament length regulation in striated muscle sarcomeres: pointed-end dynamics go beyond a nebulin ruler.Role of the sarcomeric Z-disc in the pathogenesis of cardiomyopathy.The interactome of LIM domain proteins: the contributions of LIM domain proteins to heart failure and heart development.A two-segment model for thin filament architecture in skeletal muscle.Does Nebulin Make Tropomyosin Less Dynamic in Mature Myofibrils in Cross-Striated Myocytes?Animal Models of Congenital Cardiomyopathies Associated With Mutations in Z-Line Proteins.Identification of six new genetic loci associated with atrial fibrillation in the Japanese population.Myofilaments: Movers and Rulers of the Sarcomere.Overview of the Muscle Cytoskeleton.New insights to the MLL recombinome of acute leukemias.Transcription repression and blocks in cell cycle progression in hypoplastic left heart syndrome.
P2860
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P2860
Targeted disruption of nebulette protein expression alters cardiac myofibril assembly and function
description
2002 nî lūn-bûn
@nan
2002 թուականի Փետրուարին հրատարակուած գիտական յօդուած
@hyw
2002 թվականի փետրվարին հրատարակված գիտական հոդված
@hy
2002年の論文
@ja
2002年論文
@yue
2002年論文
@zh-hant
2002年論文
@zh-hk
2002年論文
@zh-mo
2002年論文
@zh-tw
2002年论文
@wuu
name
Targeted disruption of nebulet ...... yofibril assembly and function
@ast
Targeted disruption of nebulet ...... yofibril assembly and function
@en
Targeted disruption of nebulet ...... yofibril assembly and function
@en-gb
Targeted disruption of nebulet ...... yofibril assembly and function
@nl
type
label
Targeted disruption of nebulet ...... yofibril assembly and function
@ast
Targeted disruption of nebulet ...... yofibril assembly and function
@en
Targeted disruption of nebulet ...... yofibril assembly and function
@en-gb
Targeted disruption of nebulet ...... yofibril assembly and function
@nl
prefLabel
Targeted disruption of nebulet ...... yofibril assembly and function
@ast
Targeted disruption of nebulet ...... yofibril assembly and function
@en
Targeted disruption of nebulet ...... yofibril assembly and function
@en-gb
Targeted disruption of nebulet ...... yofibril assembly and function
@nl
P3181
P356
P1476
Targeted disruption of nebulet ...... yofibril assembly and function
@en
P2093
Carole L Moncman
P304
P3181
P356
10.1006/EXCR.2001.5423
P407
P577
2002-02-15T00:00:00Z