Mitochondrial COQ9 is a lipid-binding protein that associates with COQ7 to enable coenzyme Q biosynthesis
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Mitochondrial ADCK3 employs an atypical protein kinase-like fold to enable coenzyme Q biosynthesisFibrillin 5 Is Essential for Plastoquinone-9 Biosynthesis by Binding to Solanesyl Diphosphate Synthases in ArabidopsisIdentification of Coq11, a new coenzyme Q biosynthetic protein in the CoQ-synthome in Saccharomyces cerevisiaeMitochondrial Protein Interaction Mapping Identifies Regulators of Respiratory Chain FunctionDBSI server: DNA binding site identifier.Human COQ9 Rescues a coq9 Yeast Mutant by Enhancing Coenzyme Q Biosynthesis from 4-Hydroxybenzoic Acid and Stabilizing the CoQ-SynthomeThe clinical heterogeneity of coenzyme Q10 deficiency results from genotypic differences in the Coq9 gene.Yeast Coq9 controls deamination of coenzyme Q intermediates that derive from para-aminobenzoic acid.CLD1 Reverses the Ubiquinone Insufficiency of Mutant cat5/coq7 in a Saccharomyces cerevisiae Model System.Coenzyme Q deficiency causes impairment of the sulfide oxidation pathway.CoQ deficiency causes disruption of mitochondrial sulfide oxidation, a new pathomechanism associated with this syndrome.Fatal neonatal encephalopathy and lactic acidosis caused by a homozygous loss-of-function variant in COQ9.Biosynthesis of coenzyme Q in eukaryotes.Biochemical Assessment of Coenzyme Q10 Deficiency.Impact of Chemical Analogs of 4-Hydroxybenzoic Acid on Coenzyme Q Biosynthesis: From Inhibition to Bypass of Coenzyme Q Deficiency.Rescue of primary ubiquinone deficiency due to a novel COQ7 defect using 2,4-dihydroxybensoic acid.The Role of Sulfide Oxidation Impairment in the Pathogenesis of Primary CoQ Deficiency.Coq6 is responsible for the C4-deamination reaction in coenzyme Q biosynthesis in Saccharomyces cerevisiae.Balanced CoQ6 biosynthesis is required for lifespan and mitophagy in yeast.A Journey across Genomes Uncovers the Origin of Ubiquinone in Cyanobacteria.Multi-omics Reveal Specific Targets of the RNA-Binding Protein Puf3p and Its Orchestration of Mitochondrial Biogenesis.Biochemistry of Mitochondrial Coenzyme Q Biosynthesis.Mitochondrial CoQ deficiency is a common driver of mitochondrial oxidants and insulin resistance.COQ9 dimer:COQ7:Fe2+ hydroxylates DMQ10H2 to DeMQ10H2RNA-binding proteins regulate cell respiration and coenzyme Q biosynthesis by post-transcriptional regulation of COQ7.A path to the powerhouse: Systems-to-structure approaches for studying mitochondrial proteins.Reduction in the levels of CoQ biosynthetic proteins is related to an increase in lifespan without evidence of hepatic mitohormesis
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P2860
Mitochondrial COQ9 is a lipid-binding protein that associates with COQ7 to enable coenzyme Q biosynthesis
description
2014 nî lūn-bûn
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2014 թուականի Նոյեմբերին հրատարակուած գիտական յօդուած
@hyw
2014 թվականի նոյեմբերին հրատարակված գիտական հոդված
@hy
2014年の論文
@ja
2014年論文
@yue
2014年論文
@zh-hant
2014年論文
@zh-hk
2014年論文
@zh-mo
2014年論文
@zh-tw
2014年论文
@wuu
name
Mitochondrial COQ9 is a lipid- ...... enable coenzyme Q biosynthesis
@ast
Mitochondrial COQ9 is a lipid- ...... enable coenzyme Q biosynthesis
@en
Mitochondrial COQ9 is a lipid- ...... enable coenzyme Q biosynthesis
@en-gb
Mitochondrial COQ9 is a lipid- ...... enable coenzyme Q biosynthesis
@nl
type
label
Mitochondrial COQ9 is a lipid- ...... enable coenzyme Q biosynthesis
@ast
Mitochondrial COQ9 is a lipid- ...... enable coenzyme Q biosynthesis
@en
Mitochondrial COQ9 is a lipid- ...... enable coenzyme Q biosynthesis
@en-gb
Mitochondrial COQ9 is a lipid- ...... enable coenzyme Q biosynthesis
@nl
prefLabel
Mitochondrial COQ9 is a lipid- ...... enable coenzyme Q biosynthesis
@ast
Mitochondrial COQ9 is a lipid- ...... enable coenzyme Q biosynthesis
@en
Mitochondrial COQ9 is a lipid- ...... enable coenzyme Q biosynthesis
@en-gb
Mitochondrial COQ9 is a lipid- ...... enable coenzyme Q biosynthesis
@nl
P2093
P2860
P50
P921
P3181
P356
P1476
Mitochondrial COQ9 is a lipid- ...... enable coenzyme Q biosynthesis
@en
P2093
Adam Jochem
Arne Ulbrich
Catherine E Minogue
Danielle C Lohman
Emily T Beebe
Huang Wang
John K Everett
Jonathan A Stefely
Joshua J Coon
Julie C Mitchell
P2860
P304
P3181
P356
10.1073/PNAS.1413128111
P407
P577
2014-11-04T00:00:00Z