A Drosophila homolog of the polyglutamine disease gene SCA2 is a dosage-sensitive regulator of actin filament formation
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Ataxin-2 interacts with the DEAD/H-box RNA helicase DDX6 and interferes with P-bodies and stress granulesCell biology of spinocerebellar ataxiadAtaxin-2 mediates expanded Ataxin-1-induced neurodegeneration in a Drosophila model of SCA1Drosophila as an In Vivo Model for Human Neurodegenerative DiseaseTherapeutic prospects for spinocerebellar ataxia type 2 and 3.The RNA-binding protein ATX-2 regulates cytokinesis through PAR-5 and ZEN-4Molecular determinants of caste differentiation in the highly eusocial honeybee Apis melliferaPolyglutamine genes interact to modulate the severity and progression of neurodegeneration in Drosophila.Guide to understanding Drosophila models of neurodegenerative diseases.Ataxin-2: From RNA Control to Human Health and DiseaseDrosophila models of neurodegenerative diseaseHox gene expression leads to differential hind leg development between honeybee castes.Profilin 1 associates with stress granules and ALS-linked mutations alter stress granule dynamics.A noise-reduction GWAS analysis implicates altered regulation of neurite outgrowth and guidance in autism.Caenorhabditis elegans atx-2 promotes germline proliferation and the oocyte fate.Role of inositol 1,4,5-trisphosphate receptors in pathogenesis of Huntington's disease and spinocerebellar ataxiasRNA editing in Drosophila melanogaster: New targets and functional consequences.Both ubiquitin ligases FBXW8 and PARK2 are sequestrated into insolubility by ATXN2 PolyQ expansions, but only FBXW8 expression is dysregulated.The Ataxin-2 protein is required for microRNA function and synapse-specific long-term olfactory habituation.Neurogenetics: single gene disorders.Deranged calcium signaling in Purkinje cells and pathogenesis in spinocerebellar ataxia 2 (SCA2) and other ataxiasDrosophila models of proteinopathies: the little fly that could.Changes in Purkinje cell firing and gene expression precede behavioral pathology in a mouse model of SCA2Expression of expanded polyglutamine targets profilin for degradation and alters actin dynamicsTranscriptome Profiling Following Neuronal and Glial Expression of ALS-Linked SOD1 in Drosophila.Integrated signaling in flower senescence: an overview.Cell size and fat content of dietary-restricted Caenorhabditis elegans are regulated by ATX-2, an mTOR repressor.Genetic and molecular aspects of spinocerebellar ataxias.Inositol 1,4,5-tripshosphate receptor, calcium signaling, and polyglutamine expansion disorders.Deranged calcium signaling and neurodegeneration in spinocerebellar ataxia type 2.Drosophila ataxin-2 gene encodes two differentially expressed isoforms and its function in larval fat body is crucial for development of peripheral tissuesLocal RNA translation at the synapse and in disease.A Drosophila model of Huntington disease-like 2 exhibits nuclear toxicity and distinct pathogenic mechanisms from Huntington disease.Atxn2 Knockout and CAG42-Knock-in Cerebellum Shows Similarly Dysregulated Expression in Calcium Homeostasis Pathway.Spinocerebellar Ataxia Type 2: Clinicogenetic Aspects, Mechanistic Insights, and Management Approaches.Glial and neuronal functions of the Drosophila homolog of the human SWI/SNF gene ATR-X (DATR-X) and the jing zinc-finger gene specify the lateral positioning of longitudinal glia and axons.
P2860
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P2860
A Drosophila homolog of the polyglutamine disease gene SCA2 is a dosage-sensitive regulator of actin filament formation
description
2002 nî lūn-bûn
@nan
2002 թուականի Դեկտեմբերին հրատարակուած գիտական յօդուած
@hyw
2002 թվականի դեկտեմբերին հրատարակված գիտական հոդված
@hy
2002年の論文
@ja
2002年論文
@yue
2002年論文
@zh-hant
2002年論文
@zh-hk
2002年論文
@zh-mo
2002年論文
@zh-tw
2002年论文
@wuu
name
A Drosophila homolog of the po ...... or of actin filament formation
@ast
A Drosophila homolog of the po ...... or of actin filament formation
@en
A Drosophila homolog of the po ...... or of actin filament formation
@nl
type
label
A Drosophila homolog of the po ...... or of actin filament formation
@ast
A Drosophila homolog of the po ...... or of actin filament formation
@en
A Drosophila homolog of the po ...... or of actin filament formation
@nl
prefLabel
A Drosophila homolog of the po ...... or of actin filament formation
@ast
A Drosophila homolog of the po ...... or of actin filament formation
@en
A Drosophila homolog of the po ...... or of actin filament formation
@nl
P2093
P2860
P3181
P1433
P1476
A Drosophila homolog of the po ...... or of actin filament formation
@en
P2093
Leo J Pallanck
Stephen M Jackson
Terrence F Satterfield
P2860
P304
P3181
P407
P577
2002-12-01T00:00:00Z