Microenvironmental regulation by fibrillin-1 - Wikidata - awgldk - TriplyDB

Microenvironmental regulation by fibrillin-1

Microenvironmental regulation by fibrillin-1

http://www.wikidata.org/entity/Q27335289

about

A disintegrin-like and metalloprotease domain containing thrombospondin type 1 motif-like 5 (ADAMTSL5) is a novel fibrillin-1-, fibrillin-2-, and heparin-binding member of the ADAMTS superfamily containing a netrin-like module The Function and Roles of ADAMTS-7 in Inflammatory Diseases Latent TGF-β-binding proteins Abnormal Activation of BMP Signaling Causes Myopathy in Fbn2 Null Mice ADAMTS proteins as modulators of microfibril formation and function Aurora kinases: novel therapy targets in cancers Elevated transforming growth factor β1 in plasma of primary open-angle glaucoma patients Fibrillin-1 mutations causing Weill-Marchesani syndrome and acromicric and geleophysic dysplasias disrupt heparan sulfate interactions Fibrillin-1, induced by Aurora-A but inhibited by BRCA2, promotes ovarian cancer metastasis Identification and molecular characterisation of a homozygous missense mutation in the ADAMTS10 gene in a patient with Weill-Marchesani syndrome.Is There a Relationship Between Pelvic Organ Prolapse and Tissue Fibrillin-1 Levels?Specificity of latent TGF-β binding protein (LTBP) incorporation into matrix: role of fibrillins and fibronectin ADAMTS-10 and -6 differentially regulate cell-cell junctions and focal adhesions.Copy number variants in patients with short stature.From tall to short: the role of TGFβ signaling in growth and its disorders.Extracellular metalloproteinases in neural crest development and craniofacial morphogenesis.The microfibril hypothesis of glaucoma: implications for treatment of elevated intraocular pressure.Molecular and cellular basis of scleroderma.Chondrodysplasias and TGFβ signaling.Immunolocalisation of fibrillin microfibrils in the calf metacarpal and vertebral growth plate.A microfibril assembly assay identifies different mechanisms of dominance underlying Marfan syndrome, stiff skin syndrome and acromelic dysplasias NMR spectroscopic and bioinformatic analyses of the LTBP1 C-terminus reveal a highly dynamic domain organisation.Fell-Muir Lecture: Fibrillin microfibrils: structural tensometers of elastic tissues?Progressive bundling of fibrillin microfibrils into oxytalan fibers in the chick presumptive dermis.Screening ADAMTS10 in dog populations supports Gly661Arg as the glaucoma-causing variant in beagles.Gene expression and protein distribution of ADAMTSL-4 in human iris, choroid and retina.LTBPs in biology and medicine: LTBP diseases.Mutations in LTBP3 cause acromicric dysplasia and geleophysic dysplasia.Novel mutations in ADAMTSL2 gene underlying geleophysic dysplasia in families from United Arab Emirates.Truncated C-terminus of fibrillin-1 induces Marfanoid-progeroid-lipodystrophy (MPL) syndrome in rabbit.Microfibril-associated glycoproteins MAGP-1 and MAGP-2 in disease.Multiscale Imaging Reveals the Hierarchical Organization of Fibrillin Microfibrils

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Microenvironmental regulation by fibrillin-1

http://www.wikidata.org/entity/Q27335289

description

2012 nî lūn-bûn

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2012 թուականի Յունուարին հրատարակուած գիտական յօդուած

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2012 թվականի հունվարին հրատարակված գիտական հոդված

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2012年の論文

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2012年論文

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2012年論文

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2012年論文

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2012年論文

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2012年論文

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2012年论文

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name

Microenvironmental regulation by fibrillin-1

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Microenvironmental regulation by fibrillin-1

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Microenvironmental regulation by fibrillin-1

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type

label

Microenvironmental regulation by fibrillin-1

@ast

Microenvironmental regulation by fibrillin-1

@en

Microenvironmental regulation by fibrillin-1

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prefLabel

Microenvironmental regulation by fibrillin-1

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Microenvironmental regulation by fibrillin-1

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Microenvironmental regulation by fibrillin-1

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JOURNAL.PGEN.1002425

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Microenvironmental regulation by fibrillin-1

@en

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Douglas R Keene

http://www.w3.org/2001/XMLSchema#string

Eric J Carlson

http://www.w3.org/2001/XMLSchema#string

Gerhard Sengle

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John H Fessler

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John R Samples

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Kiyotoshi Sekiguchi

http://www.w3.org/2001/XMLSchema#string

Ko Tsutsui

http://www.w3.org/2001/XMLSchema#string

Liselotte I Fessler

http://www.w3.org/2001/XMLSchema#string

Lynn Y Sakai

http://www.w3.org/2001/XMLSchema#string

Mary K Wirtz

http://www.w3.org/2001/XMLSchema#string

P2860

Evidence for a critical contribution of haploinsufficiency in the complex pathogenesis of Marfan syndrome

ADAMTS10 protein interacts with fibrillin-1 and promotes its deposition in extracellular matrix of cultured fibroblasts.

Latent transforming growth factor beta-binding protein 1 interacts with fibrillin and is a microfibril-associated protein

ADAMTSL2 mutations in geleophysic dysplasia demonstrate a role for ADAMTS-like proteins in TGF-beta bioavailability regulation

ADAMTS10 mutations in autosomal recessive Weill-Marchesani syndrome

Losartan, an AT1 antagonist, prevents aortic aneurysm in a mouse model of Marfan syndrome

Pathogenetic sequence for aneurysm revealed in mice underexpressing fibrillin-1

In frame fibrillin-1 gene deletion in autosomal dominant Weill-Marchesani syndrome

Latent TGF-β structure and activation

Targeting of bone morphogenetic protein growth factor complexes to fibrillin

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e1002425

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scholarly article

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2819077

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10.1371/JOURNAL.PGEN.1002425

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1

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8

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2012-01-01T00:00:00Z

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221744693

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22242013

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3252277

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