SHY1, the yeast homolog of the mammalian SURF-1 gene, encodes a mitochondrial protein required for respiration.
about
The conserved mitochondrial twin Cx9C protein Cmc2 Is a Cmc1 homologue essential for cytochrome c oxidase biogenesisOnly one splice variant of the human TAZ gene encodes a functional protein with a role in cardiolipin metabolismPGC-1alpha/beta upregulation is associated with improved oxidative phosphorylation in cells harboring nonsense mtDNA mutationsMTO1 codes for a mitochondrial protein required for respiration in paromomycin-resistant mutants of Saccharomyces cerevisiae.Shy1p occurs in a high molecular weight complex and is required for efficient assembly of cytochrome c oxidase in yeast.Analysis of Leigh syndrome mutations in the yeast SURF1 homolog reveals a new member of the cytochrome oxidase assembly factor familyShy1 couples Cox1 translational regulation to cytochrome c oxidase assembly.Pet191 is a cytochrome c oxidase assembly factor in Saccharomyces cerevisiae.Mss51p and Cox14p jointly regulate mitochondrial Cox1p expression in Saccharomyces cerevisiae.Coa3 and Cox14 are essential for negative feedback regulation of COX1 translation in mitochondria.Cmc1p is a conserved mitochondrial twin CX9C protein involved in cytochrome c oxidase biogenesis.Dual functions of Mss51 couple synthesis of Cox1 to assembly of cytochrome c oxidase in Saccharomyces cerevisiae mitochondriaCOX16 encodes a novel protein required for the assembly of cytochrome oxidase in Saccharomyces cerevisiae.Expression and functional analysis of SURF1 in Leigh syndrome patients with cytochrome c oxidase deficiencyCytochrome c oxidase deficiencyMutations in the SURF1 gene associated with Leigh syndrome and cytochrome C oxidase deficiencyAssembly of cytochrome-c oxidase in the absence of assembly protein Surf1p leads to loss of the active site hemeRevolution in mitochondrial medicine.Mitochondrial disorders. A diagnostic challenge in clinical chemistry.Structure, function, and assembly of heme centers in mitochondrial respiratory complexes.Mutations of SURF-1 in Leigh disease associated with cytochrome c oxidase deficiencyDefects in cytochrome oxidase assembly in humans: lessons from yeast.Yeast as a system for modeling mitochondrial disease mechanisms and discovering therapies.Protein-mediated assembly of succinate dehydrogenase and its cofactorsSuppression mechanisms of COX assembly defects in yeast and human: insights into the COX assembly processPleiotropic effects of the yeast Sal1 and Aac2 carriers on mitochondrial function via an activity distinct from adenine nucleotide transport.Mss51p promotes mitochondrial Cox1p synthesis and interacts with newly synthesized Cox1p.Surf1, associated with Leigh syndrome in humans, is a heme-binding protein in bacterial oxidase biogenesisThe power of yeast to model diseases of the powerhouse of the cell.Integrative Approaches for Studying Mitochondrial and Nuclear Genome Co-evolution in Oxidative Phosphorylation.Inventory control: cytochrome c oxidase assembly regulates mitochondrial translation.Mechanisms of mitochondrial translational regulation.MITOP, the mitochondrial proteome database: 2000 update.Shy1p is necessary for full expression of mitochondrial COX1 in the yeast model of Leigh's syndromeA novel heme a insertion factor gene cotranscribes with the Thermus thermophilus cytochrome ba3 oxidase locusMss51 and Ssc1 facilitate translational regulation of cytochrome c oxidase biogenesis.The yeast Aac2 protein exists in physical association with the cytochrome bc1-COX supercomplex and the TIM23 machineryRegulation of the heme A biosynthetic pathway in Saccharomyces cerevisiae.Sequence conservation from human to prokaryotes of Surf1, a protein involved in cytochrome c oxidase assembly, deficient in Leigh syndrome.Coi1 is a novel assembly factor of the yeast complex III-complex IV supercomplex.
P2860
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P2860
SHY1, the yeast homolog of the mammalian SURF-1 gene, encodes a mitochondrial protein required for respiration.
description
1997 nî lūn-bûn
@nan
1997 թուականի Մայիսին հրատարակուած գիտական յօդուած
@hyw
1997 թվականի մայիսին հրատարակված գիտական հոդված
@hy
1997年の論文
@ja
1997年論文
@yue
1997年論文
@zh-hant
1997年論文
@zh-hk
1997年論文
@zh-mo
1997年論文
@zh-tw
1997年论文
@wuu
name
SHY1, the yeast homolog of the ...... tein required for respiration.
@ast
SHY1, the yeast homolog of the ...... tein required for respiration.
@en
SHY1, the yeast homolog of the ...... tein required for respiration.
@nl
type
label
SHY1, the yeast homolog of the ...... tein required for respiration.
@ast
SHY1, the yeast homolog of the ...... tein required for respiration.
@en
SHY1, the yeast homolog of the ...... tein required for respiration.
@nl
prefLabel
SHY1, the yeast homolog of the ...... tein required for respiration.
@ast
SHY1, the yeast homolog of the ...... tein required for respiration.
@en
SHY1, the yeast homolog of the ...... tein required for respiration.
@nl
P2093
P2860
P356
P1476
SHY1, the yeast homolog of the ...... tein required for respiration.
@en
P2093
P2860
P304
P356
10.1074/JBC.272.22.14356
P407
P577
1997-05-30T00:00:00Z