Shy1p is necessary for full expression of mitochondrial COX1 in the yeast model of Leigh's syndrome
about
Cytochrome c oxidase subassemblies in fibroblast cultures from patients carrying mutations in COX10, SCO1, or SURF1The conserved mitochondrial twin Cx9C protein Cmc2 Is a Cmc1 homologue essential for cytochrome c oxidase biogenesisMutations in MTO2 related to tRNA modification impair mitochondrial gene expression and protein synthesis in the presence of a paromomycin resistance mutation in mitochondrial 15 S rRNATruncated product of the bifunctional DLST gene involved in biogenesis of the respiratory chainMTG1 codes for a conserved protein required for mitochondrial translationYeast dihydroxybutanone phosphate synthase, an enzyme of the riboflavin biosynthetic pathway, has a second unrelated function in expression of mitochondrial respiration.Evidence for a pro-oxidant intermediate in the assembly of cytochrome oxidase.Mne1 is a novel component of the mitochondrial splicing apparatus responsible for processing of a COX1 group I intron in yeast.The Saccharomyces cerevisiae COQ10 gene encodes a START domain protein required for function of coenzyme Q in respiration.Yeast Cox11, a protein essential for cytochrome c oxidase assembly, is a Cu(I)-binding protein.The DEAD box protein Mrh4 functions in the assembly of the mitochondrial large ribosomal subunitThe putative GTPase encoded by MTG3 functions in a novel pathway for regulating assembly of the small subunit of yeast mitochondrial ribosomes.Mam33 promotes cytochrome c oxidase subunit I translation in Saccharomyces cerevisiae mitochondria.Analysis of Leigh syndrome mutations in the yeast SURF1 homolog reveals a new member of the cytochrome oxidase assembly factor familyATP22, a nuclear gene required for expression of the F0 sector of mitochondrial ATPase in Saccharomyces cerevisiae.Shy1 couples Cox1 translational regulation to cytochrome c oxidase assembly.Coa1 links the Mss51 post-translational function to Cox1 cofactor insertion in cytochrome c oxidase assembly.Ribosome-binding proteins Mdm38 and Mba1 display overlapping functions for regulation of mitochondrial translation.Cox25 teams up with Mss51, Ssc1, and Cox14 to regulate mitochondrial cytochrome c oxidase subunit 1 expression and assembly in Saccharomyces cerevisiaeMss51p and Cox14p jointly regulate mitochondrial Cox1p expression in Saccharomyces cerevisiae.Coa3 and Cox14 are essential for negative feedback regulation of COX1 translation in mitochondria.Coa2 is an assembly factor for yeast cytochrome c oxidase biogenesis that facilitates the maturation of Cox1.Cmc1p is a conserved mitochondrial twin CX9C protein involved in cytochrome c oxidase biogenesis.COX23, a homologue of COX17, is required for cytochrome oxidase assembly.Dual functions of Mss51 couple synthesis of Cox1 to assembly of cytochrome c oxidase in Saccharomyces cerevisiae mitochondriaMitochondria-specific RNA-modifying enzymes responsible for the biosynthesis of the wobble base in mitochondrial tRNAs. Implications for the molecular pathogenesis of human mitochondrial diseases.COX16 encodes a novel protein required for the assembly of cytochrome oxidase in Saccharomyces cerevisiae.The pentatricopeptide repeats present in Pet309 are necessary for translation but not for stability of the mitochondrial COX1 mRNA in yeast.Assembly of cytochrome-c oxidase in the absence of assembly protein Surf1p leads to loss of the active site hemeMitochondrial Cytochrome c Oxidase Biogenesis Is Regulated by the Redox State of a Heme-Binding Translational ActivatorEXOSC8 mutations alter mRNA metabolism and cause hypomyelination with spinal muscular atrophy and cerebellar hypoplasia.Spatio-temporal dynamics of yeast mitochondrial biogenesis: transcriptional and post-transcriptional mRNA oscillatory modules.The role of Coa2 in hemylation of yeast Cox1 revealed by its genetic interaction with Cox10Human COX20 cooperates with SCO1 and SCO2 to mature COX2 and promote the assembly of cytochrome c oxidase.Formation of the redox cofactor centers during Cox1 maturation in yeast cytochrome oxidase.Combination of the loss of cmnm5U34 with the lack of s2U34 modifications of tRNALys, tRNAGlu, and tRNAGln altered mitochondrial biogenesis and respiration.MTO1 mutations are associated with hypertrophic cardiomyopathy and lactic acidosis and cause respiratory chain deficiency in humans and yeast.Defects in mitochondrial fatty acid synthesis result in failure of multiple aspects of mitochondrial biogenesis in Saccharomyces cerevisiae.Biogenesis and assembly of eukaryotic cytochrome c oxidase catalytic core.A deubiquitylating complex required for neosynthesis of a yeast mitochondrial ATP synthase subunit
P2860
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P2860
Shy1p is necessary for full expression of mitochondrial COX1 in the yeast model of Leigh's syndrome
description
2002 nî lūn-bûn
@nan
2002年の論文
@ja
2002年論文
@yue
2002年論文
@zh-hant
2002年論文
@zh-hk
2002年論文
@zh-mo
2002年論文
@zh-tw
2002年论文
@wuu
2002年论文
@zh
2002年论文
@zh-cn
name
Shy1p is necessary for full ex ...... east model of Leigh's syndrome
@en
Shy1p is necessary for full ex ...... ast model of Leigh's syndrome.
@nl
type
label
Shy1p is necessary for full ex ...... east model of Leigh's syndrome
@en
Shy1p is necessary for full ex ...... ast model of Leigh's syndrome.
@nl
prefLabel
Shy1p is necessary for full ex ...... east model of Leigh's syndrome
@en
Shy1p is necessary for full ex ...... ast model of Leigh's syndrome.
@nl
P2093
P2860
P356
P1433
P1476
Shy1p is necessary for full ex ...... east model of Leigh's syndrome
@en
P2093
Alexander Tzagoloff
Antoni Barrientos
Daniel Korr
P2860
P356
10.1093/EMBOJ/21.1.43
P407
P577
2002-01-01T00:00:00Z