about
Contribution of the different modules in the utrophin carboxy-terminal region to the formation and regulation of the DAP complexSyntrophin binds to an alternatively spliced exon of dystrophinSmoothelin, a novel cytoskeletal protein specific for smooth muscle cellsIncreasing complexity of the dystrophin-associated protein complexZZ domain of dystrophin and utrophin: topology and mapping of a beta-dystroglycan interaction siteDown-regulation of a novel actin-binding molecule, skeletrophin, in malignant melanomaBrain dystrophin-glycoprotein complex: persistent expression of beta-dystroglycan, impaired oligomerization of Dp71 and up-regulation of utrophins in animal models of muscular dystrophyThe potential of sarcospan in adhesion complex replacement therapeutics for the treatment of muscular dystrophyCurrent understanding of molecular pathology and treatment of cardiomyopathy in duchenne muscular dystrophyHanging on for the ride: adhesion to the extracellular matrix mediates cellular responses in skeletal muscle morphogenesis and diseaseCloning and expression of full length mouse utrophin: the differential association of utrophin and dystrophin with AChR clustersIdentification of alpha-syntrophin binding to syntrophin triplet, dystrophin, and utrophinAssociation of aciculin with dystrophin and utrophinThe rsp5-domain is shared by proteins of diverse functionsExpression of agrin, dystroglycan, and utrophin in normal renal tissue and in experimental glomerulopathiesDrug discovery for Duchenne muscular dystrophy via utrophin promoter activation screeningProteomic analysis reveals new cardiac-specific dystrophin-associated proteinsChanges in mechanosensitive channel gating following mechanical stimulation in skeletal muscle myotubes from the mdx mouseIdentification and characterisation of transcript and protein of a new short N-terminal utrophin isoformDetermination of the critical residues responsible for cardiac myosin binding protein C's interactionsMicroutrophin delivery through rAAV6 increases lifespan and improves muscle function in dystrophic dystrophin/utrophin-deficient miceDisruption of the utrophin-actin interaction by monoclonal antibodies and prediction of an actin-binding surface of utrophin.Ets-2 repressor factor silences extrasynaptic utrophin by N-box mediated repression in skeletal muscle.Dystrophic Cardiomyopathy-Potential Role of Calcium in Pathogenesis, Treatment and Novel TherapiesHigh levels of sarcospan are well tolerated and act as a sarcolemmal stabilizer to address skeletal muscle and pulmonary dysfunction in DMD.Main clinical features of the three mapped autosomal recessive limb-girdle muscular dystrophies and estimated proportion of each form in 13 Brazilian families.Chronic administration of membrane sealant prevents severe cardiac injury and ventricular dilatation in dystrophic dogs.Utrophin binds laterally along actin filaments and can couple costameric actin with sarcolemma when overexpressed in dystrophin-deficient muscle.Dystrophin and utrophin: genetic analyses of their role in skeletal muscle.Regulation and functional significance of utrophin expression at the mammalian neuromuscular synapse.Sarcolemmal nNOS anchoring reveals a qualitative difference between dystrophin and utrophin.Dystrophins, utrophins, and associated scaffolding complexes: role in mammalian brain and implications for therapeutic strategies.Disease-causing missense mutations in actin binding domain 1 of dystrophin induce thermodynamic instability and protein aggregation.Overexpression of the cytotoxic T cell GalNAc transferase in skeletal muscle inhibits muscular dystrophy in mdx miceDeficiency of dystrophin-associated proteins in Duchenne muscular dystrophy patients lacking COOH-terminal domains of dystrophin.Abnormal expression of laminin suggests disturbance of sarcolemma-extracellular matrix interaction in Japanese patients with autosomal recessive muscular dystrophy deficient in adhalin.Harnessing the potential of dystrophin-related proteins for ameliorating Duchenne's muscular dystrophy.G-utrophin, the autosomal homologue of dystrophin Dp116, is expressed in sensory ganglia and brain.Differential heparin inhibition of skeletal muscle alpha-dystroglycan binding to laminins.Sarcospan integration into laminin-binding adhesion complexes that ameliorate muscular dystrophy requires utrophin and α7 integrin.
P2860
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P2860
description
1992 nî lūn-bûn
@nan
1992 թուականի Դեկտեմբերին հրատարակուած գիտական յօդուած
@hyw
1992 թվականի դեկտեմբերին հրատարակված գիտական հոդված
@hy
1992年の論文
@ja
1992年論文
@yue
1992年論文
@zh-hant
1992年論文
@zh-hk
1992年論文
@zh-mo
1992年論文
@zh-tw
1992年论文
@wuu
name
Primary structure of dystrophin-related protein
@ast
Primary structure of dystrophin-related protein
@en
Primary structure of dystrophin-related protein
@nl
type
label
Primary structure of dystrophin-related protein
@ast
Primary structure of dystrophin-related protein
@en
Primary structure of dystrophin-related protein
@nl
prefLabel
Primary structure of dystrophin-related protein
@ast
Primary structure of dystrophin-related protein
@en
Primary structure of dystrophin-related protein
@nl
P2093
P3181
P356
P1433
P1476
Primary structure of dystrophin-related protein
@en
P2093
A E Knight
G K Suthers
J Kendrick-Jones
J M Tinsley
U Fairbrother
P2888
P3181
P356
10.1038/360591A0
P407
P577
1992-12-10T00:00:00Z
P6179
1016013848