Sarcolemmal nNOS anchoring reveals a qualitative difference between dystrophin and utrophin. - Wikidata - awgldk - TriplyDB

Sarcolemmal nNOS anchoring reveals a qualitative difference between dystrophin and utrophin.

Sarcolemmal nNOS anchoring reveals a qualitative difference between dystrophin and utrophin.

http://www.wikidata.org/entity/Q33891300

about

The potential of sarcospan in adhesion complex replacement therapeutics for the treatment of muscular dystrophy Hanging on for the ride: adhesion to the extracellular matrix mediates cellular responses in skeletal muscle morphogenesis and disease Identification of new dystroglycan complexes in skeletal muscle An intronic LINE-1 element insertion in the dystrophin gene aborts dystrophin expression and results in Duchenne-like muscular dystrophy in the corgi breed Muscle structure influences utrophin expression in mdx mice.iNOS ablation does not improve specific force of the extensor digitorum longus muscle in dystrophin-deficient mdx4cv mice.Molecular diagnosis of duchenne muscular dystrophy: past, present and future in relation to implementing therapies Biglycan recruits utrophin to the sarcolemma and counters dystrophic pathology in mdx mice Correlation of Utrophin Levels with the Dystrophin Protein Complex and Muscle Fibre Regeneration in Duchenne and Becker Muscular Dystrophy Muscle Biopsies.Myogenic Akt signaling attenuates muscular degeneration, promotes myofiber regeneration and improves muscle function in dystrophin-deficient mdx mice.Current status of pharmaceutical and genetic therapeutic approaches to treat DMD.Duchenne muscular dystrophy gene therapy: Lost in translation?Internal deletion compromises the stability of dystrophin Characterization of 65 epitope-specific dystrophin monoclonal antibodies in canine and murine models of duchenne muscular dystrophy by immunostaining and western blot.Nitric oxide signalling pathway in Duchenne muscular dystrophy mice: up-regulation of L-arginine transporters.In vitro stability of therapeutically relevant, internally truncated dystrophins.Novel mini-dystrophin gene dual adeno-associated virus vectors restore neuronal nitric oxide synthase expression at the sarcolemma Dystrophin-compromised sarcoglycan-δ-knockout diaphragm requires full wild-type embryonic stem cell reconstitution for correction.Porcine models of muscular dystrophy Sarcolemmal targeting of nNOSμ improves contractile function of mdx muscle.Absence of Dystrophin Disrupts Skeletal Muscle Signaling: Roles of Ca2+, Reactive Oxygen Species, and Nitric Oxide in the Development of Muscular Dystrophy.α2 and α3 helices of dystrophin R16 and R17 frame a microdomain in the α1 helix of dystrophin R17 for neuronal NOS binding.2015 William Allan Award.Progress in gene therapy of dystrophic heart disease.In vivo genome editing improves muscle function in a mouse model of Duchenne muscular dystrophy.Prospect of gene therapy for cardiomyopathy in hereditary muscular dystrophy.Dual AAV therapy ameliorates exercise-induced muscle injury and functional ischemia in murine models of Duchenne muscular dystrophy Current Challenges and Future Directions in Recombinant AAV-Mediated Gene Therapy of Duchenne Muscular Dystrophy.Molecular mechanism of sphingosine-1-phosphate action in Duchenne muscular dystrophy.Microtubule binding distinguishes dystrophin from utrophin.Progress in therapy for Duchenne muscular dystrophy.Advances in genetic therapeutic strategies for Duchenne muscular dystrophy.A new look at cytoskeletal NOS-1 and β-dystroglycan changes in developing muscle and brain in control and mdx dystrophic mice.Nanotherapy for Duchenne muscular dystrophy.Second-generation compound for the modulation of utrophin in the therapy of DMD.Functional improvement of dystrophic muscle by repression of utrophin: let-7c interaction.Therapy for Duchenne muscular dystrophy: renewed optimism from genetic approaches.Rescue of dystrophic skeletal muscle by PGC-1α involves restored expression of dystrophin-associated protein complex components and satellite cell signaling.Nitric oxide donors improve prednisone effects on muscular dystrophy in the mdx mouse diaphragm.Independent variability of microtubule perturbations associated with dystrophinopathy.

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Sarcolemmal nNOS anchoring reveals a qualitative difference between dystrophin and utrophin.

http://www.wikidata.org/entity/Q33891300

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2010 nî lūn-bûn

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2010 թուականի Մայիսին հրատարակուած գիտական յօդուած

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2010 թվականի մայիսին հրատարակված գիտական հոդված

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2010年の論文

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2010年論文

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2010年論文

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2010年論文

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Sarcolemmal nNOS anchoring rev ...... tween dystrophin and utrophin.

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Sarcolemmal nNOS anchoring rev ...... tween dystrophin and utrophin.

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Sarcolemmal nNOS anchoring rev ...... tween dystrophin and utrophin.

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Sarcolemmal nNOS anchoring rev ...... tween dystrophin and utrophin.

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Sarcolemmal nNOS anchoring rev ...... tween dystrophin and utrophin.

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Sarcolemmal nNOS anchoring rev ...... etween dystrophin and utrophin

@en

P2093

Akshay Bareja

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Dejia Li

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Jeffrey S Chamberlain

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Kay E Davies

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Luke Judge

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Rebecca Fairclough

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Yongping Yue

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P2860

Nitric oxide synthase complexed with dystrophin and absent from skeletal muscle sarcolemma in Duchenne muscular dystrophy

Utrophin-dystrophin-deficient mice as a model for Duchenne muscular dystrophy

In vivo requirement of the alpha-syntrophin PDZ domain for the sarcolemmal localization of nNOS and aquaporin-4

Absence of alpha-syntrophin leads to structurally aberrant neuromuscular synapses deficient in utrophin

Unexpected modes of PDZ domain scaffolding revealed by structure of nNOS-syntrophin complex

Solution structure of the extended neuronal nitric oxide synthase PDZ domain complexed with an associated peptide

Primary structure of dystrophin-related protein

An autosomal transcript in skeletal muscle with homology to dystrophin

Differential association of syntrophin pairs with the dystrophin complex

Membrane organization of the dystrophin-glycoprotein complex

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2008-2013

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10.1242/JCS.064808

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Pt 12

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123

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2010-05-18T00:00:00Z

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20483958

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2880012

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