Human alpha-N-acetylglucosaminidase. 1. Purification and properties
about
The molecular basis of Sanfilippo syndrome type BCorrection of mucopolysaccharidosis type IIIb fibroblasts by lentiviral vector-mediated gene transferSanfilippo syndrome type C: deficiency of acetyl-CoA:alpha-glucosaminide N-acetyltransferase in skin fibroblastsSanfilippo syndrome: causes, consequences, and treatmentsRecognition of human urine alpha-N-acetylglucosaminidase by rat hepatocytes. Involvement of receptors specific for galactose, mannose 6-phosphate and mannoseTurnover of matrix proteins in mammalian mitochondriaBiosynthesis and maturation of alpha-N-acetylglucosaminidase in normal and Sanfilippo B-fibroblasts.Sanfilippo disease type D: deficiency of N-acetylglucosamine-6-sulfate sulfatase required for heparan sulfate degradation.Phosphorylated oligosaccharides in lysosomal enzymes: identification of alpha-N-acetylglucosamine(1)phospho(6)mannose diester groups.Juvenile and adult metachromatic leukodystrophy: partial restoration of arylsulfatase A (cerebroside sulfatase) activity by inhibitors of thiol proteinases.The intramembrane proteases signal Peptide peptidase-like 2a and 2b have distinct functions in vivoEndocytosis of lysosomal enzymes by non-parenchymal rat liver cells. Comparative study of lysosomal-enzyme uptake by hepatocytes and non-parenchymal liver cells.Purification and properties of N-acetylgalactosamine 6-sulphate sulphatase from human placenta.Comparative studies of lipoteichoic acids from several Bacillus strains.N-acetylmannosaminyl(1----4)N-acetylglucosamine, a linkage unit between glycerol teichoic acid and peptidoglycan in cell walls of several Bacillus strains.Morquio syndrome (mucopolysaccharidosis IV B) associated with beta-galactosidase deficiency. Report of two cases.Evidence for lysosomal enzyme recognition by human fibroblasts via a phosphorylated carbohydrate moiety.An alternative hypothesis of cellular transport of lysosomal enzymes in fibroblasts. Effect of inhibitors of lysosomal enzyme endocytosis on intra- and extra-cellular lysosomal enzyme activities.Functional characterization of the lysosomal membrane protein TMEM192 in mice.Biosynthesis and transport of cathepsin D in cultured human fibroblasts.Myeloperoxidase is synthesized as larger phosphorylated precursor.Restoration of arylsulphatase B activity in human mucopolysaccharidosis-type-VI fibroblasts by retroviral-vector-mediated gene transfer.Degradation of keratan sulphate by beta-N-acetylhexosaminidases A and B.Immunochemical detection of CoA-modified mitochondrial matrix proteins.Studies on secretion and endocytosis of macromolecules by cultivated skin fibroblasts. Effects of anti-microtubular agents on secretion and endocytosis of lysosomal hydrolases and of sulphated glycosaminoglycans.Inhibition by cyanate of the processing of lysosomal enzymes.Mortality in patients with Sanfilippo syndrome.Molecular forms of beta-hexosaminidase and cathepsin D in serum and urine of healthy subjects and patients with elevated activity of lysosomal enzymes.Sociobiology: Sense or nonsense?External genitalia hypertrophy in an adolescent girl with Sanfilippo syndrome.
P2860
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P2860
Human alpha-N-acetylglucosaminidase. 1. Purification and properties
description
1977 nî lūn-bûn
@nan
1977 թուականի Նոյեմբերին հրատարակուած գիտական յօդուած
@hyw
1977 թվականի նոյեմբերին հրատարակված գիտական հոդված
@hy
1977年の論文
@ja
1977年論文
@yue
1977年論文
@zh-hant
1977年論文
@zh-hk
1977年論文
@zh-mo
1977年論文
@zh-tw
1977年论文
@wuu
name
Human alpha-N-acetylglucosaminidase. 1. Purification and properties
@ast
Human alpha-N-acetylglucosaminidase. 1. Purification and properties
@en
Human alpha-N-acetylglucosaminidase. 1. Purification and properties
@nl
type
label
Human alpha-N-acetylglucosaminidase. 1. Purification and properties
@ast
Human alpha-N-acetylglucosaminidase. 1. Purification and properties
@en
Human alpha-N-acetylglucosaminidase. 1. Purification and properties
@nl
prefLabel
Human alpha-N-acetylglucosaminidase. 1. Purification and properties
@ast
Human alpha-N-acetylglucosaminidase. 1. Purification and properties
@en
Human alpha-N-acetylglucosaminidase. 1. Purification and properties
@nl
P1433
P1476
Human alpha-N-acetylglucosaminidase. 1. Purification and properties
@en
P2093
K von Figura
P304
P356
10.1111/J.1432-1033.1977.TB11908.X
P407
P577
1977-11-01T00:00:00Z