Bone marrow transplantation only partially restores purine metabolites to normal in adenosine deaminase-deficient patients
about
Coordinate developmental regulation of purine catabolic enzyme expression in gastrointestinal and postimplantation reproductive tractsThe antiinflammatory mechanism of methotrexate. Increased adenosine release at inflamed sites diminishes leukocyte accumulation in an in vivo model of inflammation.The adenosine/neutrophil paradox resolved: human neutrophils possess both A1 and A2 receptors that promote chemotaxis and inhibit O2 generation, respectivelyAdenosine: an endogenous inhibitor of neutrophil-mediated injury to endothelial cells.Functional coupling of the Galpha(olf) variant XLGalpha(olf) with the human adenosine A2A receptor.Multicentric dermatofibrosarcoma protuberans in patients with adenosine deaminase-deficient severe combined immune deficiencyPathologic findings in adenosine deaminase-deficient severe combined immunodeficiency. I. Kidney, adrenal, and chondro-osseous tissue alterations.Somatic mosaicism for a newly identified splice-site mutation in a patient with adenosine deaminase-deficient immunodeficiency and spontaneous clinical recovery.Adenosine: a physiological modulator of superoxide anion generation by human neutrophils.Adenosine promotes neutrophil chemotaxis.Altered intracellular and extracellular signaling leads to impaired T-cell functions in ADA-SCID patients.Expression of human adenosine deaminase in murine hematopoietic cells.Renoprotective Effects of a Highly Selective A3 Adenosine Receptor Antagonist in a Mouse Model of Adriamycin-induced NephropathyDevelopment of gene therapy: potential in severe combined immunodeficiency due to adenosine deaminase deficiency.Insights into thymic purine metabolism and adenosine deaminase deficiency revealed by transgenic mice overexpressing ecto-5'-nucleotidase (CD73).Update on the safety and efficacy of retroviral gene therapy for immunodeficiency due to adenosine deaminase deficiency.Methotrexate and sulfasalazine promote adenosine release by a mechanism that requires ecto-5'-nucleotidase-mediated conversion of adenine nucleotides.Complete and partial adenosine deaminase deficiency. Relationship of immune function to metabolite concentrations, enzyme activity, and effects of therapy.Asthmatic patients have neutrophils that exhibit diminished responsiveness to adenosine.Purine deoxynucleosides and adenosine dialdehyde decrease 5-amino-4-imidazolecarboxamide (Z-base)-dependent purine nucleotide synthesis in cultured T and B lymphoblastsMicrodialysis of intercellular adenosine concentration in subcutaneous tissue in humans.Functional analysis of the human adenosine deaminase gene thymic regulatory region and its ability to generate position-independent transgene expression.Immune reconstitution in ADA-SCID after PBL gene therapy and discontinuation of enzyme replacement.Adenosine metabolism, immunity and joint health.
P2860
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P2860
Bone marrow transplantation only partially restores purine metabolites to normal in adenosine deaminase-deficient patients
description
1981 nî lūn-bûn
@nan
1981 թուականի Դեկտեմբերին հրատարակուած գիտական յօդուած
@hyw
1981 թվականի դեկտեմբերին հրատարակված գիտական հոդված
@hy
1981年の論文
@ja
1981年論文
@yue
1981年論文
@zh-hant
1981年論文
@zh-hk
1981年論文
@zh-mo
1981年論文
@zh-tw
1981年论文
@wuu
name
Bone marrow transplantation on ...... e deaminase-deficient patients
@ast
Bone marrow transplantation on ...... e deaminase-deficient patients
@en
Bone marrow transplantation on ...... e deaminase-deficient patients
@nl
type
label
Bone marrow transplantation on ...... e deaminase-deficient patients
@ast
Bone marrow transplantation on ...... e deaminase-deficient patients
@en
Bone marrow transplantation on ...... e deaminase-deficient patients
@nl
prefLabel
Bone marrow transplantation on ...... e deaminase-deficient patients
@ast
Bone marrow transplantation on ...... e deaminase-deficient patients
@en
Bone marrow transplantation on ...... e deaminase-deficient patients
@nl
P2093
P2860
P3181
P356
P1476
Bone marrow transplantation on ...... e deaminase-deficient patients
@en
P2093
L Kuritsky
R Hirschhorn
V Roegner-Maniscalco
P2860
P304
P3181
P356
10.1172/JCI110389
P407
P577
1981-12-01T00:00:00Z