Altered intracellular and extracellular signaling leads to impaired T-cell functions in ADA-SCID patients.
about
High-throughput discovery and characterization of fetal protein trafficking in the blood of pregnant womenAdenosine Deaminase Deficiency - More Than Just an ImmunodeficiencyGenetics of SCIDEarly-onset stroke and vasculopathy associated with mutations in ADA2Autoimmune dysregulation and purine metabolism in adenosine deaminase deficiency.Adenosine deaminase enhances the immunogenicity of human dendritic cells from healthy and HIV-infected individuals.Integration profile of retroviral vector in gene therapy treated patients is cell-specific according to gene expression and chromatin conformation of target cellDefective B cell tolerance in adenosine deaminase deficiency is corrected by gene therapyStem cell-derived tissue-associated regulatory T cells ameliorate the development of autoimmunity.New insights into the metabolic and nutritional determinants of severe combined immunodeficiency.Development of gene therapy: potential in severe combined immunodeficiency due to adenosine deaminase deficiency.Elevated IgE and atopy in patients treated for early-onset ADA-SCID.How I treat ADA deficiency.PRMT5-Selective Inhibitors Suppress Inflammatory T Cell Responses and Experimental Autoimmune Encephalomyelitis.Primary immunodeficiency diseases associated with neurologic manifestations.Rational design of HIV vaccines and microbicides: report of the EUROPRISE network annual conference 2010.A map of human circular RNAs in clinically relevant tissues.Adenosine Deaminase (ADA)-Deficient Severe Combined Immune Deficiency (SCID): Molecular Pathogenesis and Clinical Manifestations.Hematopoietic stem cell gene therapy for adenosine deaminase-deficient severe combined immunodeficiency leads to long-term immunological recovery and metabolic correction.
P2860
Q24644940-A5F4F870-D402-4731-B805-7965D56A70C1Q26865373-A5858AD2-F156-46B8-A177-DC1528305193Q27499229-73586D82-020D-430B-91AB-E467C68CE1F3Q30410263-A1BC00AD-354F-4568-84AF-4E1AC88B80E5Q33403252-B3586488-B728-4181-A602-DDF1EF515B52Q34512293-450086FA-2443-4381-95FA-246C4BC58BAAQ34694796-08771975-BF0A-4E84-B47C-580E818FBEC5Q36005403-FD7F9361-43B2-4868-96EB-D096F591E544Q36548686-E1FCD6E1-BBAE-4ACD-AACF-ECD06AF5C949Q36756917-F7E8BC5C-1890-4C73-950E-4031FB38B1D2Q37194056-E3DE8843-E0A4-43C6-AC04-42E450267465Q37351214-7ABD3BED-60D6-465A-AC3A-4595E24601C2Q37398309-5C0DA6ED-2E8A-4E46-8BA4-9B80E71F2E73Q37625481-68692FF5-2057-45AC-B996-5BE7DEC25123Q37950942-E5737055-175E-4F0C-962C-72EAC45CDDD2Q42726161-0A9329FE-2A55-4F1E-AFF3-9A59096CD25FQ43061380-966A56D3-F628-4B76-888F-72003A0BD609Q45871226-AABDBD18-7221-4297-ABE2-1559FA1DF99EQ45872721-C4ABD00A-991C-41C7-B315-83C165C68E85
P2860
Altered intracellular and extracellular signaling leads to impaired T-cell functions in ADA-SCID patients.
description
2008 nî lūn-bûn
@nan
2008年の論文
@ja
2008年論文
@yue
2008年論文
@zh-hant
2008年論文
@zh-hk
2008年論文
@zh-mo
2008年論文
@zh-tw
2008年论文
@wuu
2008年论文
@zh
2008年论文
@zh-cn
name
Altered intracellular and extr ...... unctions in ADA-SCID patients.
@ast
Altered intracellular and extr ...... unctions in ADA-SCID patients.
@en
type
label
Altered intracellular and extr ...... unctions in ADA-SCID patients.
@ast
Altered intracellular and extr ...... unctions in ADA-SCID patients.
@en
prefLabel
Altered intracellular and extr ...... unctions in ADA-SCID patients.
@ast
Altered intracellular and extr ...... unctions in ADA-SCID patients.
@en
P2093
P2860
P1433
P1476
Altered intracellular and extr ...... unctions in ADA-SCID patients.
@en
P2093
Alessandro Aiuti
Antonella Tabucchi
Barbara Cassani
Federica Cattaneo
Filippo Carlucci
Maria Grazia Roncarolo
Massimiliano Mirolo
Michael Hershfield
Ulrike Benninghoff
P2860
P304
P356
10.1182/BLOOD-2007-05-092429
P407
P577
2008-01-24T00:00:00Z