Metabolite profiles reveal energy failure and impaired beta-oxidation in liver of mice with complex III deficiency due to a BCS1L mutation.

Metabolite profiles reveal energy failure and impaired beta-oxidation in liver of mice with complex III deficiency due to a BCS1L mutation.

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http://www.wikidata.org/entity/Q31076216
Respiratory chain complex III deficiency due to mutated BCS1L: a novel phenotype with encephalomyopathy, partially phenocopied in a Bcs1l mutant mouse model.Differential expression of genes related to mitochondrial biogenesis and bioenergetics in fatigued prostate cancer men receiving external beam radiation therapy.Differential proteomic profiling unveils new molecular mechanisms associated with mitochondrial complex III deficiency.Determination of protein carbonyls in plasma, cell extracts, tissue homogenates, isolated proteins: Focus on sample preparation and derivatization conditions.COX7A2L/SCAFI and Pre-Complex III Modify Respiratory Chain Supercomplex Formation in Different Mouse Strains with a Bcs1l Mutation.Metabolomic profiling reveals a role for caspase-2 in lipoapoptosisEffect of High-Carbohydrate Diet on Plasma Metabolome in Mice with Mitochondrial Respiratory Chain Complex III Deficiency.Complex I function and supercomplex formation are preserved in liver mitochondria despite progressive complex III deficiency.Interindividual variation in gene expression responses and metabolite formation in acetaminophen-exposed primary human hepatocytes.Ketogenic diet attenuates hepatopathy in mouse model of respiratory chain complex III deficiency caused by a Bcs1l mutation.
P2860

Metabolite profiles reveal energy failure and impaired beta-oxidation in liver of mice with complex III deficiency due to a BCS1L mutation.

Item
http://www.wikidata.org/entity/Q31076216
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2012 nî lūn-bûn
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2012 թուականի Յուլիսին հրատարակուած գիտական յօդուած
@hyw
2012 թվականի հուլիսին հրատարակված գիտական հոդված
@hy
2012年の論文
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2012年論文
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2012年論文
@zh-hant
2012年論文
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2012年論文
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2012年論文
@zh-tw
2012年论文
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name
Metabolite profiles reveal ene ...... iency due to a BCS1L mutation.
@ast
Metabolite profiles reveal ene ...... iency due to a BCS1L mutation.
@en
type
label
Metabolite profiles reveal ene ...... iency due to a BCS1L mutation.
@ast
Metabolite profiles reveal ene ...... iency due to a BCS1L mutation.
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prefLabel
Metabolite profiles reveal ene ...... iency due to a BCS1L mutation.
@ast
Metabolite profiles reveal ene ...... iency due to a BCS1L mutation.
@en
P1433
P1476
P2093
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Metabolite profiles reveal ene ...... iency due to a BCS1L mutation.
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P2093
P2860
P304
P31
P356
10.1371/JOURNAL.PONE.0041156
P407
P433
P478
P577
P5875
P698
P932