COX7A2L/SCAFI and Pre-Complex III Modify Respiratory Chain Supercomplex Formation in Different Mouse Strains with a Bcs1l Mutation.

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Respiratory chain supercomplexes: Structures, function and biogenesis.Lifetime imaging of GFP at CoxVIIIa reports respiratory supercomplex assembly in live cells.Clarifying the supercomplex: the higher-order organization of the mitochondrial electron transport chain.

P2860

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P2860

COX7A2L/SCAFI and Pre-Complex III Modify Respiratory Chain Supercomplex Formation in Different Mouse Strains with a Bcs1l Mutation.

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http://www.wikidata.org/entity/Q36229589

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2016 nî lūn-bûn

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2016年の論文

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2016年論文

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2016年論文

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2016年論文

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2016年論文

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2016年論文

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2016年论文

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2016年论文

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2016年论文

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name

COX7A2L/SCAFI and Pre-Complex ...... Strains with a Bcs1l Mutation.

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COX7A2L/SCAFI and Pre-Complex ...... Strains with a Bcs1l Mutation.

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type

Item

label

COX7A2L/SCAFI and Pre-Complex ...... Strains with a Bcs1l Mutation.

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COX7A2L/SCAFI and Pre-Complex ...... Strains with a Bcs1l Mutation.

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COX7A2L/SCAFI and Pre-Complex ...... Strains with a Bcs1l Mutation.

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COX7A2L/SCAFI and Pre-Complex ...... Strains with a Bcs1l Mutation.

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P1476

COX7A2L/SCAFI and Pre-Complex ...... Strains with a Bcs1l Mutation.

@en

P2093

Eva Hansson

http://www.w3.org/2001/XMLSchema#string

Heike Kotarsky

http://www.w3.org/2001/XMLSchema#string

P2860

Mitochondrial respiratory chain supercomplexes are destabilized in Barth Syndrome patients

Supercomplexes in the respiratory chains of yeast and mammalian mitochondria

GRACILE syndrome, a lethal metabolic disorder with iron overload, is caused by a point mutation in BCS1L

Identification of a protein mediating respiratory supercomplex stability

Rcf1 and Rcf2, members of the hypoxia-induced gene 1 protein family, are critical components of the mitochondrial cytochrome bc1-cytochrome c oxidase supercomplex.

Rcf1 mediates cytochrome oxidase assembly and respirasome formation, revealing heterogeneity of the enzyme complex.

A stabilizing factor for mitochondrial respiratory supercomplex assembly regulates energy metabolism in muscle

The GRACILE mutation introduced into Bcs1l causes postnatal complex III deficiency: a viable mouse model for mitochondrial hepatopathy

Supercomplex assembly determines electron flux in the mitochondrial electron transport chain

Metabolite profiles reveal energy failure and impaired beta-oxidation in liver of mice with complex III deficiency due to a BCS1L mutation.

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e0168774

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scholarly article

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10.1371/JOURNAL.PONE.0168774

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English

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P478

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Mina Davoudi

J Kallijärvi

Vineta Fellman

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2016-12-20T00:00:00Z

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27997587

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5173253

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COX7A2L/SCAFI and Pre-Complex III Modify Respiratory Chain Supercomplex Formation in Different Mouse Strains with a Bcs1l Mutation.

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P2860

P2860

COX7A2L/SCAFI and Pre-Complex III Modify Respiratory Chain Supercomplex Formation in Different Mouse Strains with a Bcs1l Mutation.

description

name

type

label

prefLabel

P1433

P1476

P2093

P2860

P304

P31

P356

P407

P433

P478

P50

P577

P698

P932

P356

P1433

P1476

P2093

P2860

P304

P31

P356

P407

P433

P478

P50

P577

P698

P932