Residual plasmatic activity of ADAMTS13 is correlated with phenotype severity in congenital thrombotic thrombocytopenic purpura.
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Ten patient stories illustrating the extraordinarily diverse clinical features of patients with thrombotic thrombocytopenic purpura and severe ADAMTS13 deficiency.Novel ADAMTS13 mutations in an obstetric patient with Upshaw-Schulman syndrome.Multiple in silico tools predict phenotypic manifestations in congenital thrombotic thrombocytopenic purpura.An optimized fluorogenic ADAMTS13 assay with increased sensitivity for the investigation of patients with thrombotic thrombocytopenic purpura.Congenital thrombotic thrombocytopenic purpura with novel mutations in three unrelated Turkish children.Diagnostic and prognostic values of ADAMTS13 activity measured during daily plasma exchange therapy in patients with acquired thrombotic thrombocytopenic purpura.A case of congenital TTP presenting with microganiopathy in adulthood.Congenital and acquired ADAMTS13 deficiency: Two mechanisms, one patient.ADAMTS-13 in the Diagnosis and Management of Thrombotic Microangiopathies.Understanding organ dysfunction in thrombotic thrombocytopenic purpura.ADAMTS13 Secretion and Residual Activity among Patients with Congenital Thrombotic Thrombocytopenic Purpura with and without Renal Impairment.High prevalence of hereditary thrombotic thrombocytopenic purpura in central Norway: from clinical observation to evidence.Human neutrophil peptides and complement factor Bb in pathogenesis of acquired thrombotic thrombocytopenic purpuraRelapse of congenital thrombotic thrombocytopenic purpura, after spontaneous remission, in a second-trimester primigravida: case report and review of the literature.Current status in diagnosis and treatment of hereditary thrombotic thrombocytopenic purpura.Neutrophil Protease Cleavage of Von Willebrand Factor in Glomeruli - An Anti-thrombotic Mechanism in the Kidney.Structure-function and regulation of ADAMTS-13 protease.Human neutrophil peptides inhibit cleavage of von Willebrand factor by ADAMTS13: a potential link of inflammation to TTP.A first bout of thrombotic thrombocytopenic purpura triggered by herpes simplex infection in a 45-year-old nulliparous female with Upshaw-Schulman syndromeNext-generation sequencing study finds an excess of rare, coding single-nucleotide variants of ADAMTS13 in patients with deep vein thrombosis.Pathophysiology of thrombotic thrombocytopenic purpura.Congenital thrombotic thrombocytopenic purpura (Upshaw-Schulman syndrome) caused by novel ADAMTS13 mutations.Interaction between Multimeric von Willebrand Factor and Complement: A Fresh Look to the Pathophysiology of Microvascular Thrombosis.Thrombotic thrombocytopenic purpura
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P2860
Residual plasmatic activity of ADAMTS13 is correlated with phenotype severity in congenital thrombotic thrombocytopenic purpura.
description
2012 nî lūn-bûn
@nan
2012 թուականի Ապրիլին հրատարակուած գիտական յօդուած
@hyw
2012 թվականի ապրիլին հրատարակված գիտական հոդված
@hy
2012年の論文
@ja
2012年論文
@yue
2012年論文
@zh-hant
2012年論文
@zh-hk
2012年論文
@zh-mo
2012年論文
@zh-tw
2012年论文
@wuu
name
Residual plasmatic activity of ...... otic thrombocytopenic purpura.
@ast
Residual plasmatic activity of ...... otic thrombocytopenic purpura.
@en
type
label
Residual plasmatic activity of ...... otic thrombocytopenic purpura.
@ast
Residual plasmatic activity of ...... otic thrombocytopenic purpura.
@en
prefLabel
Residual plasmatic activity of ...... otic thrombocytopenic purpura.
@ast
Residual plasmatic activity of ...... otic thrombocytopenic purpura.
@en
P2093
P2860
P50
P1433
P1476
Residual plasmatic activity of ...... otic thrombocytopenic purpura.
@en
P2093
Agnes Veyradier
April Horne
Chantal Loirat
Haifeng M Wu
Ian J Mackie
Isabella Garagiola
Marie A Scully
Marina Noris
Paul Coppo
Ri Liesner
P2860
P304
P356
10.1182/BLOOD-2012-01-403113
P407
P577
2012-04-23T00:00:00Z