Light-induced exacerbation of retinal degeneration in a rat model of Smith-Lemli-Opitz syndrome.
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Lipid biomarkers of oxidative stress in a genetic mouse model of Smith-Lemli-Opitz syndrome7-Dehydrocholesterol-derived oxysterols and retinal degeneration in a rat model of Smith-Lemli-Opitz syndromeHaploinsufficiency of RanBP2 is neuroprotective against light-elicited and age-dependent degeneration of photoreceptor neuronsThe Effect of Small Molecules on Sterol Homeostasis: Measuring 7-Dehydrocholesterol in Dhcr7-Deficient Neuro2a Cells and Human FibroblastsQuantitative proteomics analysis of inborn errors of cholesterol synthesis: identification of altered metabolic pathways in DHCR7 and SC5D deficiencyOxysterols from free radical chain oxidation of 7-dehydrocholesterol: product and mechanistic studies.Cone ERG responses in patients with Smith-Lemli-Opitz Syndrome (SLOS).Biological activities of 7-dehydrocholesterol-derived oxysterols: implications for Smith-Lemli-Opitz syndromeElevated Autophagy and Mitochondrial Dysfunction in the Smith-Lemli-Opitz Syndrome.Pathogenesis, Epidemiology, Diagnosis and Clinical Aspects of Smith-Lemli-Opitz Syndrome.Novel oxysterols observed in tissues and fluids of AY9944-treated rats: a model for Smith-Lemli-Opitz syndrome.The susceptibility of the retina to photochemical damage from visible light.Free radical oxidation of cholesterol and its precursors: Implications in cholesterol biosynthesis disorders.Partial rescue of retinal function and sterol steady-state in a rat model of Smith-Lemli-Opitz syndrome.Retinal light damage: mechanisms and protection.Probes for protein adduction in cholesterol biosynthesis disorders: Alkynyl lanosterol as a viable sterol precursor.Retinal degeneration in a rat model of Smith-Lemli-Opitz Syndrome: thinking beyond cholesterol deficiency.Treatment of Smith-Lemli-Opitz syndrome and other sterol disordersLight-induced photoreceptor and RPE degeneration involve zinc toxicity and are attenuated by pyruvate, nicotinamide, or cyclic light.Lipid hydroperoxide formation in the retina: correlation with retinal degeneration and light damage in a rat model of Smith-Lemli-Opitz syndrome.Smith-Lemli-Opitz syndrome.Antioxidants: The Missing Key to Improved Therapeutic Intervention in Smith-Lemli-Opitz Syndrome?A reduced zinc diet or zinc transporter 3 knockout attenuate light induced zinc accumulation and retinal degeneration.Pulmonary vein stenosis in patients with Smith-Lemli-Opitz syndrome.Prevention of Retinal Degeneration in a Rat Model of Smith-Lemli-Opitz Syndrome.Oxysterols and Retinal Degeneration in a Rat Model of Smith-Lemli-Opitz Syndrome: Implications for an Improved Therapeutic Intervention
P2860
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P2860
Light-induced exacerbation of retinal degeneration in a rat model of Smith-Lemli-Opitz syndrome.
description
2005 nî lūn-bûn
@nan
2005 թուականի Դեկտեմբերին հրատարակուած գիտական յօդուած
@hyw
2005 թվականի դեկտեմբերին հրատարակված գիտական հոդված
@hy
2005年の論文
@ja
2005年論文
@yue
2005年論文
@zh-hant
2005年論文
@zh-hk
2005年論文
@zh-mo
2005年論文
@zh-tw
2005年论文
@wuu
name
Light-induced exacerbation of ...... of Smith-Lemli-Opitz syndrome.
@ast
Light-induced exacerbation of ...... of Smith-Lemli-Opitz syndrome.
@en
type
label
Light-induced exacerbation of ...... of Smith-Lemli-Opitz syndrome.
@ast
Light-induced exacerbation of ...... of Smith-Lemli-Opitz syndrome.
@en
prefLabel
Light-induced exacerbation of ...... of Smith-Lemli-Opitz syndrome.
@ast
Light-induced exacerbation of ...... of Smith-Lemli-Opitz syndrome.
@en
P2093
P2860
P1476
Light-induced exacerbation of ...... of Smith-Lemli-Opitz syndrome.
@en
P2093
Blake Buchan
Dana K Vaughan
Michael J Richards
Neal S Peachey
Steven J Fliesler
P2860
P304
P356
10.1016/J.EXER.2005.08.008
P577
2005-12-19T00:00:00Z