Defects of T-cell effector function and post-thymic maturation in X-linked hyper-IgM syndrome
about
The molecular pathology of primary immunodeficienciesCD40-CD40 Ligand Interactions Promote Trafficking of CD8+ T Cells into the Brain and Protection against West Nile Virus EncephalitisFlow Cytometry, a Versatile Tool for Diagnosis and Monitoring of Primary ImmunodeficienciesSpecific missense mutations in NEMO result in hyper-IgM syndrome with hypohydrotic ectodermal dysplasiaCD154 and type-1 cytokine response: from hyper IgM syndrome to human immunodeficiency virus infectionIgM(+) memory B cell expression predicts HIV-associated cryptococcosis status.X-linked immunodeficiency with hyper-IgM (XHIM).A review on peripheral blood CD4+ T lymphocyte counts in healthy adult IndiansPartial immune reconstitution of X-linked hyper IgM syndrome with recombinant CD40 ligandEstablishment of adult peripheral blood lymphocyte subset reference range for an Asian population by single-platform flow cytometry: influence of age, sex, and race and comparison with other published studiesOsteopenia in X-linked hyper-IgM syndrome reveals a regulatory role for CD40 ligand in osteoclastogenesis.Impaired dendritic-cell function in ectodermal dysplasia with immune deficiency is linked to defective NEMO ubiquitinationCD40 agonist antibody mediated improvement of chronic Cryptosporidium infection in patients with X-linked hyper IgM syndrome.Analysis of somatic hypermutation in X-linked hyper-IgM syndrome shows specific deficiencies in mutational targeting.Hyper IgM Syndrome: a Report from the USIDNET RegistryHuman neonatal naive CD4+ T cells have enhanced activation-dependent signaling regulated by the microRNA miR-181a.The hyper IgM syndromes.Recent advances in transplantation for primary immune deficiency diseases: a comprehensive review.ICON: the early diagnosis of congenital immunodeficiencies.Liver Transplantation in a Patient With CD40 Ligand Deficiency and Hyper-IgM Syndrome: Clinical and Immunological Assessments.First report of the Hyper-IgM syndrome Registry of the Latin American Society for Immunodeficiencies: novel mutations, unique infections, and outcomes.Long-term outcomes of 176 patients with X-linked hyper-IgM syndrome treated with or without hematopoietic cell transplantation.A tissue-specific, activation-inducible, lentiviral vector regulated by human CD40L proximal promoter sequences.Clinical features and genetic analysis of 20 Chinese patients with X-linked hyper-IgM syndrome.X-linked Hyper IgM Syndrome Presenting as Pulmonary Alveolar Proteinosis.Adaptive Immunity to Cryptococcus neoformans Infections.Absence of CD40-CD40 ligand interactions in X-linked hyper-IgM syndrome does not affect differentiation of T helper cell subsets.CD40 ligand deficiency causes functional defects of peripheral neutrophils that are improved by exogenous IFN-γ.Disseminated Cutaneous Warts in X-Linked Hyper IgM Syndrome.
P2860
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P2860
Defects of T-cell effector function and post-thymic maturation in X-linked hyper-IgM syndrome
description
1999 nî lūn-bûn
@nan
1999 թուականի Ապրիլին հրատարակուած գիտական յօդուած
@hyw
1999 թվականի ապրիլին հրատարակված գիտական հոդված
@hy
1999年の論文
@ja
1999年論文
@yue
1999年論文
@zh-hant
1999年論文
@zh-hk
1999年論文
@zh-mo
1999年論文
@zh-tw
1999年论文
@wuu
name
Defects of T-cell effector fun ...... in X-linked hyper-IgM syndrome
@ast
Defects of T-cell effector fun ...... in X-linked hyper-IgM syndrome
@en
type
label
Defects of T-cell effector fun ...... in X-linked hyper-IgM syndrome
@ast
Defects of T-cell effector fun ...... in X-linked hyper-IgM syndrome
@en
prefLabel
Defects of T-cell effector fun ...... in X-linked hyper-IgM syndrome
@ast
Defects of T-cell effector fun ...... in X-linked hyper-IgM syndrome
@en
P2093
P2860
P356
P1476
Defects of T-cell effector fun ...... in X-linked hyper-IgM syndrome
@en
P2093
P2860
P304
P356
10.1172/JCI5891
P407
P577
1999-04-01T00:00:00Z