about
Cervical lymph node diseases in childrenAn update on the use of immunoglobulin for the treatment of immunodeficiency disordersGlucocorticoids upregulate CD40 ligand expression and induce CD40L-dependent immunoglobulin isotype switching.Hyper IgM syndrome associated with defective CD40-mediated B cell activationCyclosporin A inhibits CD40 ligand expression in T lymphocytes.The relative contribution of the CD28 and gp39 costimulatory pathways in the clonal expansion and pathogenic acquisition of self-reactive T cells.Mapping of the X linked form of hyper IgM syndrome (HIGM1)Hypogammaglobulinaemia associated with normal or increased IgM (the hyper IgM syndrome): a case series review.Requirement of CD40-CD40 ligand interaction for elimination of Cryptosporidium parvum from mice.CD40L and Its Receptors in Atherothrombosis-An UpdatePotential roles of activation-induced cytidine deaminase in promotion or prevention of autoimmunity in humansDefects of T-cell effector function and post-thymic maturation in X-linked hyper-IgM syndromeRole of CD40 ligand in Mycobacterium avium infectionX-linked immunodeficiency with hyper-IgM (XHIM).Mutations of CD40 gene cause an autosomal recessive form of immunodeficiency with hyper IgM.The CD40/CD40 ligand interaction is required for resistance to toxoplasmic encephalitis.Mutations in PIK3CD can cause hyper IgM syndrome (HIGM) associated with increased cancer susceptibility.X inactivation and immunocompetence in female carriers of the X-linked hyper-IgM syndromeSignaling through CD40 rescues IgE but not IgG or IgA secretion in X-linked immunodeficiency with hyper-IgM.The random inactivation of the X chromosome carrying the defective gene responsible for X-linked hyper IgM syndrome (X-HIM) in female carriers of HIGM1.CD40-CD40L independent Ig gene hypermutation suggests a second B cell diversification pathway in humans.Organization of the human CD40L gene: implications for molecular defects in X chromosome-linked hyper-IgM syndrome and prenatal diagnosis.Molecular pathology of the X-linked hyper-immunoglobulin M syndrome: detection of wild-type transcripts in a patient with a complex splicing defect of the CD40 ligandPartial immune reconstitution of X-linked hyper IgM syndrome with recombinant CD40 ligandSomatic mutation of human immunoglobulin V genes in the X-linked HyperIgM syndrome.Aging murine B cells have decreased class switch induced by anti-CD40 or BAFFCD40 ligand-deficient mice generate a normal primary cytotoxic T-lymphocyte response but a defective humoral response to a viral infection.CD40-deficient mice generated by recombination-activating gene-2-deficient blastocyst complementation.CD40 agonist antibody mediated improvement of chronic Cryptosporidium infection in patients with X-linked hyper IgM syndrome.A primary immunodeficiency characterized by defective immunoglobulin class switch recombination and impaired DNA repair.Hyper IgM syndrome presenting as chronic suppurative lung diseaseIn vivo CD40-gp39 interactions are essential for thymus-dependent humoral immunity. II. Prolonged suppression of the humoral immune response by an antibody to the ligand for CD40, gp39.Memory B cell development but not germinal center formation is impaired by in vivo blockade of CD40-CD40 ligand interaction.gp39-CD40 interactions are essential for germinal center formation and the development of B cell memoryT cell clones from an X-linked hyper-immunoglobulin (IgM) patient induce IgE synthesis in vitro despite expression of nonfunctional CD40 ligand.An essential role for gp39, the ligand for CD40, in thymic selection.TRANCE, a tumor necrosis factor family member critical for CD40 ligand-independent T helper cell activationCD40 ligand is not essential for induction of type 1 cytokine responses or protective immunity after primary or secondary infection with histoplasma capsulatum.Immunoglobulin class switch recombination: study through human natural mutantsAnalysis of somatic hypermutation in X-linked hyper-IgM syndrome shows specific deficiencies in mutational targeting.
P2860
Q26865114-031AE012-9FCE-459A-848E-58CFA28B31BDQ27012785-6EE25010-1C49-4F07-B667-5A88684C8DDFQ28346560-C6032103-5CA5-4A37-A128-196D240E759DQ30449257-B0CA2070-D78E-4AE4-A68F-54F4B3FA800DQ30449273-6EE3D228-CC1F-4E51-A7ED-9CA2BFF3E06EQ30468363-A2E8D2DA-0299-4564-AC5B-32D95FF10E43Q33595078-1A9BB136-FF7B-4649-9496-7A40B5160794Q33624904-8E754DC8-5348-4821-897E-66D55E0937ACQ33750271-DEDDC1BE-2B2E-48D6-A507-264D342A06B4Q33814059-2F658BCA-FCFD-4FE3-A250-7F6061D0CF56Q33829729-3D699A06-FB68-4521-923F-D8629AB93687Q33849472-C4C8F330-FC0C-4B51-87A9-8D7C9B799F42Q33877154-DEFECE5A-AC6C-40D2-857F-34A579098F57Q33938151-6311F79B-A14A-4CFE-816B-29340228FBB5Q33947934-F7380C98-F2B5-4224-9039-35CEFD936784Q34003535-2BDF5F74-0502-4037-85E4-EFDE842C98F9Q34155068-EE12FE3E-0EC1-4342-93A7-371700972471Q34180659-C8D4F6FD-5AC6-4B27-A057-BB1A1A70B094Q34199490-A83B477E-9938-4BD1-8231-0ECD9225C5D6Q34228923-49D383BC-E156-4D4C-AAD5-C90EEA60A3A2Q34651496-434485D6-3FF4-4532-9530-B91CC0A8CBD6Q35093419-C23EB242-ABC2-4E84-9E9A-8DBC7843350BQ35228193-4A62EBE3-396E-47CD-ABDC-89AC6C7B95ABQ35346307-58D0A198-7D33-492B-9422-D7B026B2FEADQ35554322-D9314137-E16F-4CDA-960B-CB79F8E2071BQ35809431-E5F65A11-EFC4-4823-ABD9-690C05600C25Q35873254-71B5DE6D-A8B2-4136-B671-B7B4E8E42E71Q35962812-BBFB1289-B131-4CE1-B7C7-C6804E24D9CEQ36002320-1B541B87-A4D4-492D-9C46-90335546A9F6Q36229350-703F541B-937E-42D6-9372-95091CE70D3CQ36356256-9E3C8416-E425-4C3C-B0FD-39538431F632Q36362552-E3781A9A-C208-4168-9D2B-226ACC41E4C3Q36363287-B58B284E-A635-46DF-8A06-9C1CD35EC59EQ36363299-6558615F-E9A4-49C1-A7B5-68EA6F110F88Q36364016-70505247-8F8F-4021-8142-EF846FBC8296Q36365446-CA65D603-FE0B-4971-98A3-65296E59A4B6Q36368029-2E888B22-229B-48C5-970E-15C23FEA0F86Q36400640-2040D7FB-B6DD-4993-A95A-4C362AA0AED0Q37140490-F663AC2E-2013-493E-94AE-6C6611D6BD6FQ37162837-AA7A7B0E-0738-4BAE-AC9D-98E7BF05B3E9
P2860
description
1992 nî lūn-bûn
@nan
1992年の論文
@ja
1992年学术文章
@wuu
1992年学术文章
@zh-cn
1992年学术文章
@zh-hans
1992年学术文章
@zh-my
1992年学术文章
@zh-sg
1992年學術文章
@yue
1992年學術文章
@zh
1992年學術文章
@zh-hant
name
Immunodeficiency with hyper-IgM (HIM).
@ast
Immunodeficiency with hyper-IgM (HIM).
@en
type
label
Immunodeficiency with hyper-IgM (HIM).
@ast
Immunodeficiency with hyper-IgM (HIM).
@en
prefLabel
Immunodeficiency with hyper-IgM (HIM).
@ast
Immunodeficiency with hyper-IgM (HIM).
@en
P2093
P1476
Immunodeficiency with hyper-IgM (HIM).
@en
P2093
P304
P577
1992-01-01T00:00:00Z