Therapeutic potential of cyclodextrins in the treatment of Niemann-Pick type C disease.
about
Pluronic based β-cyclodextrin polyrotaxanes for treatment of Niemann-Pick Type C disease.Systemic administration of 2-hydroxypropyl-β-cyclodextrin to symptomatic Npc1-deficient mice slows cholesterol sequestration in the major organs and improves liver functionElectrodiagnostic testing and histopathologic changes confirm peripheral nervous system myelin abnormalities in the feline model of niemann-pick disease type C.Ontogenic changes in lung cholesterol metabolism, lipid content, and histology in mice with Niemann-Pick type C disease.Ezetimibe markedly attenuates hepatic cholesterol accumulation and improves liver function in the lysosomal acid lipase-deficient mouse, a model for cholesteryl ester storage disease.Lysosomal-specific cholesterol reduction by biocleavable polyrotaxanes for ameliorating Niemann-Pick type C disease.Drug delivery by supramolecular design.Niemann-Pick type C disease - the tip of the iceberg? A review of neuropsychiatric presentation, diagnosis and treatment.Perturbed cholesterol and vesicular trafficking associated with dengue blocking in Wolbachia-infected Aedes aegypti cells.AAV9-NPC1 significantly ameliorates Purkinje cell death and behavioral abnormalities in mouse NPC disease.A Comparative Study on the Alterations of Endocytic Pathways in Multiple Lysosomal Storage Disorders.Increased Regenerative Capacity of the Olfactory Epithelium in Niemann-Pick Disease Type C1.2-Hydroxypropyl-beta-cyclodextrin (HPβCD) reduces age-related lipofuscin accumulation through a cholesterol-associated pathway.Effects of intracerebroventricular administration of 2-hydroxypropyl-β-cyclodextrin in a patient with Niemann-Pick Type C diseaseDifferential response of the liver to bile acid treatment in a mouse model of Niemann-Pick disease type C.Crystal structure of the inclusion complex of cholesterol in β-cyclodextrin and molecular dynamics studies.The susceptibility of cochlear outer hair cells to cyclodextrin is not related to their electromotile activity
P2860
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P2860
Therapeutic potential of cyclodextrins in the treatment of Niemann-Pick type C disease.
description
2012 nî lūn-bûn
@nan
2012 թուականի Յունիսին հրատարակուած գիտական յօդուած
@hyw
2012 թվականի հունիսին հրատարակված գիտական հոդված
@hy
2012年の論文
@ja
2012年論文
@yue
2012年論文
@zh-hant
2012年論文
@zh-hk
2012年論文
@zh-mo
2012年論文
@zh-tw
2012年论文
@wuu
name
Therapeutic potential of cyclodextrins in the treatment of Niemann-Pick type C disease.
@ast
Therapeutic potential of cyclodextrins in the treatment of Niemann-Pick type C disease.
@en
Therapeutic potential of cyclodextrins in the treatment of Niemann-Pick type C disease.
@nl
type
label
Therapeutic potential of cyclodextrins in the treatment of Niemann-Pick type C disease.
@ast
Therapeutic potential of cyclodextrins in the treatment of Niemann-Pick type C disease.
@en
Therapeutic potential of cyclodextrins in the treatment of Niemann-Pick type C disease.
@nl
prefLabel
Therapeutic potential of cyclodextrins in the treatment of Niemann-Pick type C disease.
@ast
Therapeutic potential of cyclodextrins in the treatment of Niemann-Pick type C disease.
@en
Therapeutic potential of cyclodextrins in the treatment of Niemann-Pick type C disease.
@nl
P2860
P356
P1433
P1476
Therapeutic potential of cyclodextrins in the treatment of Niemann-Pick type C disease.
@en
P2093
P2860
P304
P356
10.2217/CLP.12.31
P577
2012-06-01T00:00:00Z