The intracellular Ca²⁺ channel MCOLN1 is required for sarcolemma repair to prevent muscular dystrophy.
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VAMP7 regulates constitutive membrane incorporation of the cold-activated channel TRPM8.Above the fray: Surface remodeling by secreted lysosomal enzymes leads to endocytosis-mediated plasma membrane repairBiphasic regulation of lysosomal exocytosis by oxidative stressA Fine Balance of Dietary Lipids Improves Pathology of a Murine Model of VCP-Associated Multisystem ProteinopathyLysosomal physiology.Two-Pore Channels: Catalyzers of Endolysosomal Transport and Function.Role of TRP channels in the cardiovascular system.S100 and annexin proteins identify cell membrane damage as the Achilles heel of metastatic cancer cells.Organellar channels and transporters.Chronic Dosing with Membrane Sealant Poloxamer 188 NF Improves Respiratory Dysfunction in Dystrophic Mdx and Mdx/Utrophin-/- MicePlasma Membrane Repair Is Regulated Extracellularly by Proteases Released from Lysosomes.Membrane Repair: Mechanisms and Pathophysiology.Membrane fusion in muscle development and repair.Fusion of lysosomes with secretory organelles leads to uncontrolled exocytosis in the lysosomal storage disease mucolipidosis type IV.Regulation of heme biosynthesis and transport in metazoa.Calcium signaling in membrane repair.Inhibition of Transient Receptor Potential Channel Mucolipin-1 (TRPML1) by Lysosomal Adenosine Involved in Severe Combined Immunodeficiency Diseases.ROS and intracellular ion channels.A molecular mechanism to regulate lysosome motility for lysosome positioning and tubulation.A fragmented form of annexin A1 is secreted from C2C12 myotubes by electric pulse-induced contraction.The Phosphoinositide-Gated Lysosomal Ca(2+) Channel, TRPML1, Is Required for Phagosome Maturation.BK channel agonist represents a potential therapeutic approach for lysosomal storage diseases.A melanosomal two-pore sodium channel regulates pigmentation.Structure of mammalian endolysosomal TRPML1 channel in nanodiscs.Lysosomal Calcium in Neurodegeneration.The lysosomal Ca2+ release channel TRPML1 regulates lysosome size by activating calmodulin.Cryo-EM structures of the human endolysosomal TRPML3 channel in three distinct states.Robust lysosomal calcium signaling through channel TRPML1 is impaired by lysosomal lipid accumulation.Co-deficiency of Lysosomal Mucolipins 3 and 1 in Cochlear Hair Cells Diminishes Outer Hair Cell Longevity and Accelerates Age-Related Hearing Loss.Novel degenerative and developmental defects in a zebrafish model of mucolipidosis type IV.Lysosomal Ca2+ Signaling is Essential for Osteoclastogenesis and Bone Remodeling.Muscle Cells Fix Breaches by Orchestrating a Membrane Repair Ballet.Treating pediatric neuromuscular disorders: The future is now.
P2860
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P2860
The intracellular Ca²⁺ channel MCOLN1 is required for sarcolemma repair to prevent muscular dystrophy.
description
2014 nî lūn-bûn
@nan
2014 թուականի Սեպտեմբերին հրատարակուած գիտական յօդուած
@hyw
2014 թվականի սեպտեմբերին հրատարակված գիտական հոդված
@hy
2014年の論文
@ja
2014年論文
@yue
2014年論文
@zh-hant
2014年論文
@zh-hk
2014年論文
@zh-mo
2014年論文
@zh-tw
2014年论文
@wuu
name
The intracellular Ca²⁺ channel ...... to prevent muscular dystrophy.
@ast
The intracellular Ca²⁺ channel ...... to prevent muscular dystrophy.
@en
The intracellular Ca²⁺ channel ...... to prevent muscular dystrophy.
@nl
type
label
The intracellular Ca²⁺ channel ...... to prevent muscular dystrophy.
@ast
The intracellular Ca²⁺ channel ...... to prevent muscular dystrophy.
@en
The intracellular Ca²⁺ channel ...... to prevent muscular dystrophy.
@nl
prefLabel
The intracellular Ca²⁺ channel ...... to prevent muscular dystrophy.
@ast
The intracellular Ca²⁺ channel ...... to prevent muscular dystrophy.
@en
The intracellular Ca²⁺ channel ...... to prevent muscular dystrophy.
@nl
P2093
P2860
P50
P356
P1433
P1476
The intracellular Ca²⁺ channel ...... to prevent muscular dystrophy
@en
P2093
Abigail G Garrity
Haoxing Xu
James Dowling
Libing Dong
Marc Ferrer
Marlene Azar
Mohammad Ali Samie
Wai Lok Tsang
Xiang Wang
P2860
P2888
P304
P356
10.1038/NM.3611
P407
P577
2014-09-14T00:00:00Z