Clinical data and characterization of the liver conditional mouse model exclude neoplasia as a non-neurological manifestation associated with Friedreich's ataxia.

Clinical data and characterization of the liver conditional mouse model exclude neoplasia as a non-neurological manifestation associated with Friedreich's ataxia.

Item
http://www.wikidata.org/entity/Q34317949
Modeling diseases of noncoding unstable repeat expansions using mutant pluripotent stem cells.Iron homeostasis in peripheral nervous system, still a black box?A novel GAA-repeat-expansion-based mouse model of Friedreich's ataxiaMitochondrial Diseases Part II: Mouse models of OXPHOS deficiencies caused by defects in regulatory factors and other components required for mitochondrial function.Animal and cellular models of Friedreich ataxia.Clinical features of Friedreich's ataxia: classical and atypical phenotypes.Dysregulation of cellular iron metabolism in Friedreich ataxia: from primary iron-sulfur cluster deficit to mitochondrial iron accumulation.Friedreich Ataxia: current status and future prospects.Lentivirus-meditated frataxin gene delivery reverses genome instability in Friedreich ataxia patient and mouse model fibroblastsThe role of oxidative stress in Friedreich's ataxia.Drosophila melanogaster Models of Friedreich's Ataxia.Acute loss of iron-sulfur clusters results in metabolic reprogramming and generation of lipid droplets in mammalian cells.Adding a temporal dimension to the study of Friedreich's ataxia: the effect of frataxin overexpression in a human cell model.
P2860

Clinical data and characterization of the liver conditional mouse model exclude neoplasia as a non-neurological manifestation associated with Friedreich's ataxia.

Item
http://www.wikidata.org/entity/Q34317949
description
2012 nî lūn-bûn
@nan
2012 թուականի Յունիսին հրատարակուած գիտական յօդուած
@hyw
2012 թվականի հունիսին հրատարակված գիտական հոդված
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2012年の論文
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2012年論文
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2012年論文
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2012年論文
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2012年論文
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2012年論文
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2012年论文
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name
Clinical data and characteriza ...... ated with Friedreich's ataxia.
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Clinical data and characteriza ...... ated with Friedreich's ataxia.
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Clinical data and characteriza ...... ated with Friedreich's ataxia.
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Clinical data and characteriza ...... ated with Friedreich's ataxia.
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Clinical data and characteriza ...... ated with Friedreich's ataxia.
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Clinical data and characteriza ...... ated with Friedreich's ataxia.
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Clinical data and characteriza ...... ated with Friedreich's ataxia.
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Clinical data and characteriza ...... ated with Friedreich's ataxia.
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Clinical data and characteriza ...... ated with Friedreich's ataxia.
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Clinical data and characteriza ...... iated with Friedreich's ataxia
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P2093
P2860
P304
P31
P356
P433
P478
P50
P577
P5875
P698
P932