The biology of desmin filaments: how do mutations affect their structure, assembly, and organisation?
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Myotubularin controls desmin intermediate filament architecture and mitochondrial dynamics in human and mouse skeletal muscle.A novel custom resequencing array for dilated cardiomyopathyDual color photoactivation localization microscopy of cardiomyopathy-associated desmin mutantsThe tumor inhibitor and antiangiogenic agent withaferin A targets the intermediate filament protein vimentinMechanistic basis of desmosome-targeted diseasesN-acetyl-L-cysteine prevents stress-induced desmin aggregation in cellular models of desminopathyImproved neurological outcome by intramuscular injection of human amniotic fluid derived stem cells in a muscle denervation model.Monitoring intermediate filament assembly by small-angle x-ray scattering reveals the molecular architecture of assembly intermediates.Nebulette is a powerful cytolinker organizing desmin and actin in mouse heartsProteomics identification of desmin as a potential oncofetal diagnostic and prognostic biomarker in colorectal cancer.The role of muscle cells in regulating cartilage matrix production.Withaferin A targets intermediate filaments glial fibrillary acidic protein and vimentin in a model of retinal gliosisαB-crystallin is a sensor for assembly intermediates and for the subunit topology of desmin intermediate filaments.Metallothionein as a clonable high-density marker for cryo-electron microscopy.Severe muscle disease-causing desmin mutations interfere with in vitro filament assembly at distinct stagesVimentin as an integral regulator of cell adhesion and endothelial sprouting.Two desmin gene mutations associated with myofibrillar myopathies in Polish familiesTissue specific dysregulated protein subnetworks in type 2 diabetic bladder urothelium and detrusor muscleDesmin-related cardiomyopathy: an unfolding storyArsenic exposure to killifish during embryogenesis alters muscle developmentRecurrent and founder mutations in the Netherlands: the cardiac phenotype of DES founder mutations p.S13F and p.N342D.Voltage-Dependent Anion Channel 1(VDAC1) Participates the Apoptosis of the Mitochondrial Dysfunction in Desminopathy.Desminopathies: pathology and mechanisms.Clinical and myopathological characteristics of desminopathy caused by a mutation in desmin tail domain.Desmin mediates TNF-alpha-induced aggregate formation and intercalated disk reorganization in heart failure.Primary desminopathiesTragedy in a heartbeat: malfunctioning desmin causes skeletal and cardiac muscle diseaseIntermediate filaments: primary determinants of cell architecture and plasticity.Molecular pathology of myofibrillar myopathies.Build it up-Tear it down: protein quality control in the cardiac sarcomere.Intermediate filament diseases: desminopathy.Desmosomes in the heart: a review of clinical and mechanistic analyses.Desmin Mutation in the C-Terminal Domain Impairs Traction Force Generation in Myoblasts.Tissue-engineered artificial oesophagus patch using three-dimensionally printed polycaprolactone with mesenchymal stem cells: a preliminary report.Vps34 regulates myofibril proteostasis to prevent hypertrophic cardiomyopathyFlow birefringence property of desmin filaments.Disassembly of myofibrils and potential imbalanced forces on Z-discs in cultured adult cardiomyocytes.Head and rod 1 interactions in vimentin: identification of contact sites, structure, and changes with phosphorylation using site-directed spin labeling and electron paramagnetic resonance.A missense mutation in desmin tail domain linked to human dilated cardiomyopathy promotes cleavage of the head domain and abolishes its Z-disc localization.Satellite cell number and cell cycle kinetics in response to acute myotrauma in humans: immunohistochemistry versus flow cytometry.
P2860
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P2860
The biology of desmin filaments: how do mutations affect their structure, assembly, and organisation?
description
2004 nî lūn-bûn
@nan
2004 թուականի Նոյեմբերին հրատարակուած գիտական յօդուած
@hyw
2004 թվականի նոյեմբերին հրատարակված գիտական հոդված
@hy
2004年の論文
@ja
2004年論文
@yue
2004年論文
@zh-hant
2004年論文
@zh-hk
2004年論文
@zh-mo
2004年論文
@zh-tw
2004年论文
@wuu
name
The biology of desmin filament ...... e, assembly, and organisation?
@ast
The biology of desmin filament ...... e, assembly, and organisation?
@en
The biology of desmin filament ...... e, assembly, and organisation?
@nl
type
label
The biology of desmin filament ...... e, assembly, and organisation?
@ast
The biology of desmin filament ...... e, assembly, and organisation?
@en
The biology of desmin filament ...... e, assembly, and organisation?
@nl
prefLabel
The biology of desmin filament ...... e, assembly, and organisation?
@ast
The biology of desmin filament ...... e, assembly, and organisation?
@en
The biology of desmin filament ...... e, assembly, and organisation?
@nl
P2093
P1476
The biology of desmin filament ...... e, assembly, and organisation?
@en
P2093
Gunnar Sjöberg
Harald Bär
Harald Herrmann
Sergei V Strelkov
P304
P356
10.1016/J.JSB.2004.04.003
P50
P577
2004-11-01T00:00:00Z