Functional characteristics of dystrophic skeletal muscle: insights from animal models.
about
A role for nephrin, a renal protein, in vertebrate skeletal muscle cell fusionApoptosis repressor with a CARD domain (ARC) restrains Bax-mediated pathogenesis in dystrophic skeletal muscleSIK1 is a class II HDAC kinase that promotes survival of skeletal myocytesThe nebulin SH3 domain is dispensable for normal skeletal muscle structure but is required for effective active load bearing in mouse.Dissecting muscle and neuronal disorders in a Drosophila model of muscular dystrophy.Musculoskeletal simulation can help explain selective muscle degeneration in Duchenne muscular dystrophy.Microutrophin delivery through rAAV6 increases lifespan and improves muscle function in dystrophic dystrophin/utrophin-deficient miceGait disturbances in dystrophic hamsters.Proteome analysis of the dystrophin-deficient MDX diaphragm reveals a drastic increase in the heat shock protein cvHSP.Functional deficits in nNOSmu-deficient skeletal muscle: myopathy in nNOS knockout miceProteomic profiling of antisense-induced exon skipping reveals reversal of pathobiochemical abnormalities in dystrophic mdx diaphragm.Muscle inactivation of mTOR causes metabolic and dystrophin defects leading to severe myopathy.Dystrophin glycoprotein complex-associated Gbetagamma subunits activate phosphatidylinositol-3-kinase/Akt signaling in skeletal muscle in a laminin-dependent manner.Uncoordinated transcription and compromised muscle function in the lmna-null mouse model of Emery- Emery-Dreyfuss muscular dystrophy.Excitation-contraction coupling alterations in mdx and utrophin/dystrophin double knockout mice: a comparative study.Decreased proliferation kinetics of mouse myoblasts overexpressing FRG1.Improvement of the mdx mouse dystrophic phenotype by systemic in utero AAV8 delivery of a minidystrophin gene.Angiotensin II infusion induces marked diaphragmatic skeletal muscle atrophyDisruption of both nesprin 1 and desmin results in nuclear anchorage defects and fibrosis in skeletal muscle.Non-invasive optical imaging of muscle pathology in mdx mice using cathepsin caged near-infrared imagingACE2 is augmented in dystrophic skeletal muscle and plays a role in decreasing associated fibrosis.Delineating the role of alterations in lipid metabolism to the pathogenesis of inherited skeletal and cardiac muscle disorders: Thematic Review Series: Genetics of Human Lipid Diseases.Prednisolone treatment and restricted physical activity further compromise bone of mdx mice.Absence of Dystrophin Disrupts Skeletal Muscle Signaling: Roles of Ca2+, Reactive Oxygen Species, and Nitric Oxide in the Development of Muscular Dystrophy.Unloaded speed of shortening in voltage-clamped intact skeletal muscle fibers from wt, mdx, and transgenic minidystrophin mice using a novel high-speed acquisition system.Functional overloading of dystrophic mice enhances muscle-derived stem cell contribution to muscle contractile capacity.Dystrophic skeletal muscle fibers display alterations at the level of calcium microdomains.Adeno-associated virus-mediated microdystrophin expression protects young mdx muscle from contraction-induced injury.Muscle stem cells and model systems for their investigation.Sub-physiological sarcoglycan expression contributes to compensatory muscle protection in mdx miceRole of beta-adrenoceptor signaling in skeletal muscle: implications for muscle wasting and disease.Intracellular energetic units in healthy and diseased heartsSkeletal muscle as a paradigm for regenerative biology and medicine.Essential and separable roles for Syndecan-3 and Syndecan-4 in skeletal muscle development and regeneration.AAV-directed muscular dystrophy gene therapy.Proteomic profiling of animal models mimicking skeletal muscle disorders.A concise review of common animal models for the study of limb regeneration.In vivo optical imaging of acute cell death using a near-infrared fluorescent zinc-dipicolylamine probe.Drastic reduction of sarcalumenin in Dp427 (dystrophin of 427 kDa)-deficient fibres indicates that abnormal calcium handling plays a key role in muscular dystrophy.Upregulation of the creatine synthetic pathway in skeletal muscles of mature mdx mice.
P2860
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P2860
Functional characteristics of dystrophic skeletal muscle: insights from animal models.
description
2002 nî lūn-bûn
@nan
2002 թուականի Օգոստոսին հրատարակուած գիտական յօդուած
@hyw
2002 թվականի օգոստոսին հրատարակված գիտական հոդված
@hy
2002年の論文
@ja
2002年論文
@yue
2002年論文
@zh-hant
2002年論文
@zh-hk
2002年論文
@zh-mo
2002年論文
@zh-tw
2002年论文
@wuu
name
Functional characteristics of dystrophic skeletal muscle: insights from animal models.
@ast
Functional characteristics of dystrophic skeletal muscle: insights from animal models.
@en
Functional characteristics of dystrophic skeletal muscle: insights from animal models.
@nl
type
label
Functional characteristics of dystrophic skeletal muscle: insights from animal models.
@ast
Functional characteristics of dystrophic skeletal muscle: insights from animal models.
@en
Functional characteristics of dystrophic skeletal muscle: insights from animal models.
@nl
prefLabel
Functional characteristics of dystrophic skeletal muscle: insights from animal models.
@ast
Functional characteristics of dystrophic skeletal muscle: insights from animal models.
@en
Functional characteristics of dystrophic skeletal muscle: insights from animal models.
@nl
P2093
P1476
Functional characteristics of dystrophic skeletal muscle: insights from animal models.
@en
P2093
Eric P Hoffman
Jon F Watchko
Terrence L O'Day
P304
P356
10.1152/JAPPLPHYSIOL.01242.2001
P407
P577
2002-08-01T00:00:00Z