about
Comparison of lymphoblast mitochondria from normal subjects and patients with Barth syndrome using electron microscopic tomographyRole of calcium-independent phospholipase A2 in the pathogenesis of Barth syndromeQIL1 is a novel mitochondrial protein required for MICOS complex stability and cristae morphologyCharacterization of a transgenic short hairpin RNA-induced murine model of Tafazzin deficiencyFormation of molecular species of mitochondrial cardiolipin. 1. A novel transacylation mechanism to shuttle fatty acids between sn-1 and sn-2 positions of multiple phospholipid speciesThe cardiolipin transacylase, tafazzin, associates with two distinct respiratory components providing insight into Barth syndromeCharacterization of tafazzin splice variants from humans and fruit fliesMitochondrial dynamism and heart disease: changing shape and shaping changeModel organisms in the fight against muscular dystrophy: lessons from drosophila and ZebrafishCardiolipin and its different properties in mitophagy and apoptosisBarth syndrome.Mechanism for Remodeling of the Acyl Chain Composition of Cardiolipin Catalyzed by Saccharomyces cerevisiae TafazzinThe enzymatic function of tafazzinCardiolipin remodeling by TAZ/tafazzin is selectively required for the initiation of mitophagyLPS impairs oxygen utilization in epithelia by triggering degradation of the mitochondrial enzyme Alcat1Disorders of phospholipid metabolism: an emerging class of mitochondrial disease due to defects in nuclear genesCellular functions of cardiolipin in yeastCardiolipin remodeling: a regulatory hub for modulating cardiolipin metabolism and functionBacteria, yeast, worms, and flies: exploiting simple model organisms to investigate human mitochondrial diseasesCardiolipin, a critical determinant of mitochondrial carrier protein assembly and function.Mitochondrial dysfunction and reduced prostaglandin synthesis in skeletal muscle of Group VIB Ca2+-independent phospholipase A2gamma-deficient mice.Distinct effects of tafazzin deletion in differentiated and undifferentiated mitochondria.Targeted gain-of-function screening in Drosophila using GAL4-UAS and random transposon insertions.Metabolic biology of 3-methylglutaconic acid-uria: a new perspective.Neurologic dysfunction and male infertility in Drosophila porin mutants: a new model for mitochondrial dysfunction and disease.Shal/K(v)4 channels are required for maintaining excitability during repetitive firing and normal locomotion in Drosophila.Mitochondria-targeted antioxidant prevents cardiac dysfunction induced by tafazzin gene knockdown in cardiac myocytes.Orthologs of human disease associated genes and RNAi analysis of silencing insulin receptor gene in Bombyx mori.Barth syndrome without tetralinoleoyl cardiolipin deficiency: a possible ameliorated phenotype.Cardiolipin affects the supramolecular organization of ATP synthase in mitochondria.Manganese superoxide dismutase: guardian of the powerhouse.Linking aβ42-induced hyperexcitability to neurodegeneration, learning and motor deficits, and a shorter lifespan in an Alzheimer's modelMouse Tafazzin Is Required for Male Germ Cell Meiosis and Spermatogenesis.The role of mitochondria in the pathogenesis of type 2 diabetesDLGS97/SAP97 is developmentally upregulated and is required for complex adult behaviors and synapse morphology and function.Tafazzins from Drosophila and mammalian cells assemble in large protein complexes with a short half-life.Phosphatidylethanolamine deficiency in Mammalian mitochondria impairs oxidative phosphorylation and alters mitochondrial morphology.Coincidence of P-insertion sites and breakpoints of deletions induced by activating P elements in Drosophila.Substrate metabolism during basal and hyperinsulinemic conditions in adolescents and young-adults with Barth syndromeCardiolipin synthesis for the assembly of bacterial and mitochondrial membranes.
P2860
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P2860
description
2006 nî lūn-bûn
@nan
2006 թուականի Յուլիսին հրատարակուած գիտական յօդուած
@hyw
2006 թվականի հուլիսին հրատարակված գիտական հոդված
@hy
2006年の論文
@ja
2006年学术文章
@wuu
2006年学术文章
@zh-cn
2006年学术文章
@zh-hans
2006年学术文章
@zh-my
2006年学术文章
@zh-sg
2006年學術文章
@yue
name
A Drosophila model of Barth syndrome
@ast
A Drosophila model of Barth syndrome
@en
A Drosophila model of Barth syndrome
@nl
type
label
A Drosophila model of Barth syndrome
@ast
A Drosophila model of Barth syndrome
@en
A Drosophila model of Barth syndrome
@nl
prefLabel
A Drosophila model of Barth syndrome
@ast
A Drosophila model of Barth syndrome
@en
A Drosophila model of Barth syndrome
@nl
P2093
P2860
P356
P1476
A Drosophila model of Barth syndrome
@en
P2093
Heide Plesken
Irit Edelman-Novemsky
Jinping Ma
Mindong Ren
Morgan Condell
P2860
P304
11584-11588
P356
10.1073/PNAS.0603242103
P407
P577
2006-07-19T00:00:00Z