Mutant fibrinogen cleared from the endoplasmic reticulum via endoplasmic reticulum-associated protein degradation and autophagy: an explanation for liver disease.
about
Capitalizing on the autophagic response for treatment of liver disease caused by alpha-1-antitrypsin deficiency and other genetic diseasesTargeting autophagy for the treatment of liver diseasesThe delicate balance between secreted protein folding and endoplasmic reticulum-associated degradation in human physiologyHypofibrinogenemia and liver disease: a new case of Aguadilla fibrinogen and review of the literature.Hepatic fibrinogen storage disease due to the fibrinogen γ375 Arg → Trp mutation "fibrinogen Aguadilla" is present in ArabsRole of autophagy in liver physiology and pathophysiology.Endoplasmic reticulum stress regulation of the Kar2p/BiP chaperone alleviates proteotoxicity via dual degradation pathways.Linking of autophagy to ubiquitin-proteasome system is important for the regulation of endoplasmic reticulum stress and cell viability.Dissection of endoplasmic reticulum stress signaling in alcoholic and non-alcoholic liver injury.A picky eater: exploring the mechanisms of selective autophagy in human pathologies.Functions of autophagy in normal and diseased liver.Autophagy in the liver.Autophagy and ethanol-induced liver injury.Autophagic disposal of the aggregation-prone protein that causes liver inflammation and carcinogenesis in alpha-1-antitrypsin deficiency.alpha1-Antitrypsin deficiency, chronic obstructive pulmonary disease and the serpinopathies.Glycoprotein folding and quality-control mechanisms in protein-folding diseasesTau-focused immunotherapy for Alzheimer's disease and related tauopathies.α1-antitrypsin Deficiency: A Misfolded Secretory Protein Variant with Unique Effects on the Endoplasmic Reticulum.Autophagy in hepatic fibrosis.Hepatic fibrosis and carcinogenesis in α1-antitrypsin deficiency: a prototype for chronic tissue damage in gain-of-function disorders.α(1)-antitrypsin deficiency and inflammation.Endoplasmic reticulum and the unfolded protein response: dynamics and metabolic integrationBroad spectrum of hepatocyte inclusions in humans, animals, and experimental models.Mechanism and Regulation of Autophagy and Its Role in Neuronal Diseases.Targeting the autophagy pathway for cancer chemoprevention.Survival and death of endoplasmic-reticulum-stressed cells: Role of autophagy.Can the phenotype of inherited fibrinogen disorders be predicted?Hepatic fibrinogen storage disease: identification of two novel mutations (p.Asp316Asn, fibrinogen Pisa and p.Gly366Ser, fibrinogen Beograd) impacting on the fibrinogen γ-module.Reticulophagy and ribophagy: regulated degradation of protein production factories.Autophagy is dispensable to overcome ER stress in the filamentous fungus Aspergillus niger.Fibrinogen Gamma Chain Mutations Provoke Fibrinogen and Apolipoprotein B Plasma Deficiency and Liver Storage.Regulator of G Signaling 16 is a marker for the distinct endoplasmic reticulum stress state associated with aggregated mutant alpha1-antitrypsin Z in the classical form of alpha1-antitrypsin deficiency.
P2860
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P2860
Mutant fibrinogen cleared from the endoplasmic reticulum via endoplasmic reticulum-associated protein degradation and autophagy: an explanation for liver disease.
description
2006 nî lūn-bûn
@nan
2006 թուականի Ապրիլին հրատարակուած գիտական յօդուած
@hyw
2006 թվականի ապրիլին հրատարակված գիտական հոդված
@hy
2006年の論文
@ja
2006年論文
@yue
2006年論文
@zh-hant
2006年論文
@zh-hk
2006年論文
@zh-mo
2006年論文
@zh-tw
2006年论文
@wuu
name
Mutant fibrinogen cleared from ...... explanation for liver disease.
@ast
Mutant fibrinogen cleared from ...... explanation for liver disease.
@en
type
label
Mutant fibrinogen cleared from ...... explanation for liver disease.
@ast
Mutant fibrinogen cleared from ...... explanation for liver disease.
@en
prefLabel
Mutant fibrinogen cleared from ...... explanation for liver disease.
@ast
Mutant fibrinogen cleared from ...... explanation for liver disease.
@en
P2093
P2860
P1476
Mutant fibrinogen cleared from ...... explanation for liver disease.
@en
P2093
Brandan E Crum
Erin R Kaltenbrun
Peter M George
Stephen O Brennan
P2860
P304
1299-308; quiz 1404-5
P356
10.2353/AJPATH.2006.051097
P407
P577
2006-04-01T00:00:00Z