Clinical and neuropathologic variation in neuronal intermediate filament inclusion disease
about
Abundant FUS-immunoreactive pathology in neuronal intermediate filament inclusion diseaseNeuropathology of non-Alzheimer degenerative disordersNeuronal intranuclear inclusions are ultrastructurally and immunologically distinct from cytoplasmic inclusions of neuronal intermediate filament inclusion diseaseEarly limited nitrosamine exposures exacerbate high fat diet-mediated type 2 diabetes and neurodegeneration.HDDD2 is a familial frontotemporal lobar degeneration with ubiquitin-positive, tau-negative inclusions caused by a missense mutation in the signal peptide of progranulinAnti-alpha-internexin autoantibody from neuropsychiatric lupus induce cognitive damage via inhibiting axonal elongation and promote neuron apoptosis.Neuropathologic diagnostic and nosologic criteria for frontotemporal lobar degeneration: consensus of the Consortium for Frontotemporal Lobar DegenerationFrequency of ubiquitin and FUS-positive, TDP-43-negative frontotemporal lobar degenerationFUS immunogold labeling TEM analysis of the neuronal cytoplasmic inclusions of neuronal intermediate filament inclusion disease: a frontotemporal lobar degeneration with FUS proteinopathy.FUS pathology defines the majority of tau- and TDP-43-negative frontotemporal lobar degeneration.Distinct pathological subtypes of FTLD-FUS.Frontotemporal lobar degeneration: epidemiology, pathophysiology, diagnosis and management.Caudate atrophy on MRI is a characteristic feature of FTLD-FUSThe spectrum and severity of FUS-immunoreactive inclusions in the frontal and temporal lobes of ten cases of neuronal intermediate filament inclusion disease.Neuronal degeneration in autonomic nervous system of Dystonia musculorum mice.Evaluation of subcortical pathology and clinical correlations in FTLD-U subtypes.Abnormalities of the nucleus and nuclear inclusions in neurodegenerative disease: a work in progress.Spatial patterns of FUS-immunoreactive neuronal cytoplasmic inclusions (NCI) in neuronal intermediate filament inclusion disease (NIFID).TDP-43 in familial and sporadic frontotemporal lobar degeneration with ubiquitin inclusions.Imaging signatures of molecular pathology in behavioral variant frontotemporal dementiaNuclear carrier and RNA-binding proteins in frontotemporal lobar degeneration associated with fused in sarcoma (FUS) pathological changes.The relationship between amyotrophic lateral sclerosis and frontotemporal dementia.Corticospinal tract degeneration associated with TDP-43 type C pathology and semantic dementiaFrontotemporal lobar degeneration: current concepts in the light of recent advances.Impact of very old age on the expression of cervical spinal cord cell markers in rats.Frontotemporal dementia and related disorders: deciphering the enigma.Composition of Rosenthal Fibers, the Protein Aggregate Hallmark of Alexander DiseaseNeuropsychological decline in frontotemporal lobar degeneration: a longitudinal analysis.Different molecular pathologies result in similar spatial patterns of cellular inclusions in neurodegenerative disease: a comparative study of eight disordersThe molecular basis of frontotemporal dementia.Novel types of frontotemporal lobar degeneration: beyond tau and TDP-43.Neuropathological background of phenotypical variability in frontotemporal dementia.Neuroimaging in frontotemporal lobar degeneration--predicting molecular pathology.Basophilic inclusions and neuronal intermediate filament inclusions in amyotrophic lateral sclerosis and frontotemporal lobar degeneration.The role of FUS gene variants in neurodegenerative diseases.Frontotemporal lobar degeneration: Pathogenesis, pathology and pathways to phenotype.Clinicopathological and genetic correlates of frontotemporal lobar degeneration and corticobasal degeneration.The most common type of FTLD-FUS (aFTLD-U) is associated with a distinct clinical form of frontotemporal dementia but is not related to mutations in the FUS gene.Parkinsonism, movement disorders and genetics in frontotemporal dementia.Molecular neuropathology of frontotemporal dementia: insights into disease mechanisms from postmortem studies.
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P2860
Clinical and neuropathologic variation in neuronal intermediate filament inclusion disease
description
2004 nî lūn-bûn
@nan
2004年の論文
@ja
2004年学术文章
@wuu
2004年学术文章
@zh-cn
2004年学术文章
@zh-hans
2004年学术文章
@zh-my
2004年学术文章
@zh-sg
2004年學術文章
@yue
2004年學術文章
@zh
2004年學術文章
@zh-hant
name
Clinical and neuropathologic v ...... ate filament inclusion disease
@ast
Clinical and neuropathologic v ...... ate filament inclusion disease
@en
type
label
Clinical and neuropathologic v ...... ate filament inclusion disease
@ast
Clinical and neuropathologic v ...... ate filament inclusion disease
@en
prefLabel
Clinical and neuropathologic v ...... ate filament inclusion disease
@ast
Clinical and neuropathologic v ...... ate filament inclusion disease
@en
P2093
P2860
P1433
P1476
Clinical and neuropathologic v ...... ate filament inclusion disease
@en
P2093
B Stankoff
C Duyckaerts
F F Cruz-Sanchez
I R A Mackenzie
P2860
P304
P356
10.1212/01.WNL.0000139809.16817.DD
P407
P577
2004-10-01T00:00:00Z