Direct demonstration of binding of a lysosomal enzyme, alpha-L-iduronidase, to receptors on cultured fibroblasts
about
Lysosomal enzyme binding to mouse P388D1 macrophage membranes lacking the 215-kDa mannose 6-phosphate receptor: evidence for the existence of a second mannose 6-phosphate receptorBone marrow transplantation in canine mucopolysaccharidosis I. Effects within the central nervous system.Multistep autoactivation of asparaginyl endopeptidase in vitro and in vivo.Characterization of a membrane-associated receptor from bovine liver that binds phosphomannosyl residues of bovine testicular beta-galactosidase.Direct gene transfer to the CNS prevents emergence of neurologic disease in a murine model of mucopolysaccharidosis type I.Mucopolysaccharidosis type I subtypes. Presence of immunologically cross-reactive material and in vitro enhancement of the residual alpha-L-iduronidase activities.Determination of Biological Variance and Validation of a Fluorometric Assay for Measurement of α-l-Iduronidase Activity in Dried Blood Spots Samples: The First Experience in IranMorphologic and biochemical studies of canine mucopolysaccharidosis I.Canine alpha-L-iduronidase deficiency. A model of mucopolysaccharidosis I.Biosynthesis of lysosomal hydrolases: their synthesis in bound polysomes and the role of co- and post-translational processing in determining their subcellular distribution.Carbohydrate specificity of sea urchin sperm bindin: a cell surface lectin mediating sperm-egg adhesion.Recognition and receptor-mediated uptake of phosphorylated high mannose-type oligosaccharides by cultured human fibroblasts.Pathways involved in targeting and secretion of a lysosomal enzyme in Dictyostelium discoideum.Phosphomannosyl-derivatized beads detect a receptor involved in lymphocyte homingRegional assignment of the structural gene for human alpha-L-iduronidaseMutant of Chinese hamster ovary cells with altered mannose 6-phosphate receptor activity is unable to synthesize mannosylphosphoryldolichol.Synthesis of beta-hexosaminidase in cell-free translation and in intact fibroblasts: an insoluble precursor alpha chain in a rare form of Tay-Sachs disease.Morphologic study of the internalization of a lysosomal enzyme by the mannose 6-phosphate receptor in cultured Chinese hamster ovary cellsThe lysosomal proenzyme receptor that binds procathepsin L to microsomal membranes at pH 5 is a 43-kDa integral membrane protein.Biochemical and histopathological studies on patients with mucopolysaccharidoses, two of whom had been treated by fibroblast transplantationProperties of the Syrian hamster phosphomannosyl receptor: an aggregate of low molecular weight proteins.A canine model of human alpha-L-iduronidase deficiency.Role of endosomes and lysosomes in human disease.Progress toward improved therapies for inborn errors of metabolism.Lysosomal enzyme replacement therapies: Historical development, clinical outcomes, and future perspectives.Transplantation in inborn errors of metabolism: current considerations and future perspectives.Serum levels of glycosyltransferases and related glycoproteins as indicators of cancer: biological and clinical implications.Mannose 6-phosphate-independent Lysosomal Sorting of LIMP-2.Chloroquine inhibits lysosomal enzyme pinocytosis and enhances lysosomal enzyme secretion by impairing receptor recyclingAntibody to mannose 6-phosphate specific receptor induces receptor deficiency in human fibroblastsIodinated fibroblast beta-glucuronidase as a ligand for receptor-mediated endocytosis.Biosynthesis and turnover of the phosphomannosyl receptor in human fibroblasts.Effect of monensin on intracellular transport and receptor-mediated endocytosis of lysosomal enzymes.Increased longevity and metabolic correction following syngeneic BMT in a murine model of mucopolysaccharidosis type I.Incorporation of mannose 6-phosphate receptors into liposomes. Receptor topography and binding of alpha-mannosidase.Nanobody-triggered lockdown of VSRs reveals ligand reloading in the Golgi.
P2860
Q24609876-DDD57B33-5463-4729-847F-F3160A3A9EC3Q34165972-A1EB275F-58D3-4237-9276-205806E82EA6Q34214364-76084A6E-587F-44B0-896C-42A8782011B0Q35399911-147C6001-9D93-46EC-828E-44B1F4F1925CQ35559945-E7697242-C8C7-49B0-999B-6F9E50E69905Q35584723-110D955D-0234-4426-8D52-810A355E3FA4Q35747087-AEAC842C-C3EA-4844-BC4A-49A1BA11DFBEQ35858094-D78662C3-4ABE-4E19-84AC-B8326034CFF1Q35885212-042E7873-6D8F-4706-8A87-347E04F51251Q36206018-6EBA8651-CFF5-4170-B851-57F53827225DQ36206295-8EEAD003-1087-4C2E-ACE8-207C8343B420Q36207136-D468A77C-E60C-4CA1-B2F5-8C201AE6606CQ36213477-1072C263-C448-40C5-8765-C2C4D17E7E01Q36216483-4C6B88CB-889A-48E6-9785-93A0EC988478Q36249664-72BB8F42-F76A-44E2-AA67-CF3F4A2AE1BBQ36289835-D4D3BA09-9A94-4DB3-A939-1F9A07924A90Q36317143-D2832C12-35BA-4B41-B74D-C8D269DE50B6Q36379266-59E9D5A6-C332-40FA-8928-1FF07023E907Q36661989-F181EC11-0FB5-44AF-A39A-39D906571F23Q37170277-185BC9D5-7C59-4095-A44C-6AE3F29564C3Q37538984-1EBF22D6-E6FA-48B7-9DFD-C09461E2FC71Q37690504-7AF30C96-C181-4A32-9A49-ED59F87CC555Q37718121-7C8B355C-8C3B-495A-BEBA-C6E849E0F845Q38601073-B49A7FE8-F723-4EDA-A896-4FBA332779FEQ38684097-9D1580A8-D121-4965-98A0-DD733CB8A387Q39151620-8210790D-9947-4488-9C96-F703157FBCC7Q40218874-9DA43894-647F-4996-950C-1CB7690371BFQ40685291-78004EEC-DD9C-4EAD-9FC2-EBEA07C6EEBAQ41337499-0EAB1C6A-5FB6-4281-8E8C-48D77A9A12A2Q41573025-AB8DC2B5-4B74-419F-BC47-D7629F3A5858Q41849049-4E091C00-E7BD-42C0-BBD6-318550C5F2B8Q42070674-30D883A6-DF56-4207-A98E-B637D9C0D0F6Q42166819-FF87F7FB-8454-4111-8D35-4F7EE5479DE4Q42273263-0F7BFDFA-57BD-44FE-8AC6-6DE553F61F43Q42864950-E5DA65A4-5A51-4CF4-9B44-76728FBC58ECQ49166359-D25A4C71-1FEB-4C88-BBEC-A327065267AD
P2860
Direct demonstration of binding of a lysosomal enzyme, alpha-L-iduronidase, to receptors on cultured fibroblasts
description
article científic
@ca
article scientifique
@fr
articolo scientifico
@it
artigo científico
@pt
bilimsel makale
@tr
scientific article published on May 1979
@en
vedecký článok
@sk
vetenskaplig artikel
@sv
videnskabelig artikel
@da
vědecký článek
@cs
name
Direct demonstration of bindin ...... eptors on cultured fibroblasts
@en
Direct demonstration of bindin ...... ptors on cultured fibroblasts.
@nl
type
label
Direct demonstration of bindin ...... eptors on cultured fibroblasts
@en
Direct demonstration of bindin ...... ptors on cultured fibroblasts.
@nl
prefLabel
Direct demonstration of bindin ...... eptors on cultured fibroblasts
@en
Direct demonstration of bindin ...... ptors on cultured fibroblasts.
@nl
P2860
P356
P1476
Direct demonstration of bindin ...... eptors on cultured fibroblasts
@en
P2093
Neufeld EF
Weissmann B
P2860
P304
P356
10.1073/PNAS.76.5.2331
P407
P577
1979-05-01T00:00:00Z