Oxidative stress in Fanconi anaemia: from cells and molecules towards prospects in clinical management.
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A never-ending story: the steadily growing family of the FA and FA-like genesImprovement of genetic stability in lymphocytes from Fanconi anemia patients through the combined effect of α-lipoic acid and N-acetylcysteine.Bone marrow cell transcripts from Fanconi anaemia patients reveal in vivo alterations in mitochondrial, redox and DNA repair pathways.Damaged mitochondria in Fanconi anemia - an isolated event or a general phenomenon?DNA damage responses and oxidative stress in dyskeratosis congenita.Oxidative Stress -a Phenotypic Hallmark of Fanconi Anemia and Down Syndrome: The Effect of AntioxidantsSlow Replication Fork Velocity of Homologous Recombination-Defective Cells Results from Endogenous Oxidative StressIn Vivo RNAi Screen Unveils PPARγ as a Regulator of Hematopoietic Stem Cell HomeostasisOxidative Stress in Cancer-Prone Genetic Diseases in Pediatric Age: The Role of Mitochondrial DysfunctionImpaired mitophagy in Fanconi anemia is dependent on mitochondrial fission.Maintenance of genome stability by Fanconi anemia proteins.Binding to WGR domain by salidroside activates PARP1 and protects hematopoietic stem cells from oxidative stress.Oxidative stress-associated protein tyrosine kinases and phosphatases in Fanconi anemiaDNA interstrand cross-link repair: understanding role of Fanconi anemia pathway and therapeutic implications.TNF-α signaling in Fanconi anemia.Fanconi Anemia: A DNA repair disorder characterized by accelerated decline of the hematopoietic stem cell compartment and other features of aging.IL-6, IL-8, MMP-2, MMP-9 are overexpressed in Fanconi anemia cells through a NF-κB/TNF-α dependent mechanism.New insights into redox response modulation in Fanconi's anemia cells by hydrogen peroxide and glutathione depletors.Damaged mitochondria and overproduction of ROS in Fanconi anemia cells.Hydroxyurea induces chromosomal damage in G2 and enhances the clastogenic effect of mitomycin C in Fanconi anemia cells.
P2860
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P2860
Oxidative stress in Fanconi anaemia: from cells and molecules towards prospects in clinical management.
description
article científic
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article scientifique
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articol științific
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articolo scientifico
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artigo científico
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artigo científico
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artigo científico
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artikel ilmiah
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artikull shkencor
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artículo científico
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name
Oxidative stress in Fanconi an ...... spects in clinical management.
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type
label
Oxidative stress in Fanconi an ...... spects in clinical management.
@en
prefLabel
Oxidative stress in Fanconi an ...... spects in clinical management.
@en
P2093
P2860
P356
P1433
P1476
Oxidative stress in Fanconi an ...... spects in clinical management.
@en
P2093
Adriana Zatterale
Annarita Aiello Talamanca
Federico V Pallardó
Giovanni Pagano
Giuseppe Castello
Paolo Degan
P2860
P356
10.1515/BC-2011-227
P577
2012-01-01T00:00:00Z