The Role of Dipeptide Repeats in C9ORF72-Related ALS-FTD.
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The small heat shock protein B8 (HSPB8) efficiently removes aggregating species of dipeptides produced in C9ORF72-related neurodegenerative diseases.Failure to Deliver and Translate-New Insights into RNA Dysregulation in ALS.Widespread Translational Remodeling during Human Neuronal Differentiation.A zebrafish model for C9orf72 ALS reveals RNA toxicity as a pathogenic mechanism.Antisense oligonucleotides: the next frontier for treatment of neurological disorders.RNA-binding proteins in neurodegeneration: mechanisms in aggregate.Lost in Transportation: Nucleocytoplasmic Transport Defects in ALS and Other Neurodegenerative Diseases.CUG initiation and frameshifting enable production of dipeptide repeat proteins from ALS/FTD C9ORF72 transcripts.Unraveling the Role of RNA Mediated Toxicity of C9orf72 Repeats in C9-FTD/ALS.In Situ Structure of Neuronal C9orf72 Poly-GA Aggregates Reveals Proteasome Recruitment.mRNP assembly, axonal transport, and local translation in neurodegenerative diseases.Poly-GR dipeptide repeat polymers correlate with neurodegeneration and Clinicopathological subtypes in C9ORF72-related brain diseaseThe proline-arginine repeat protein linked to C9-ALS/FTD causes neuronal toxicity by inhibiting the DEAD-box RNA helicase-mediated ribosome biogenesisALS Yeast Models—Past Success Stories and New Opportunities
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P2860
The Role of Dipeptide Repeats in C9ORF72-Related ALS-FTD.
description
2017 nî lūn-bûn
@nan
2017年の論文
@ja
2017年論文
@yue
2017年論文
@zh-hant
2017年論文
@zh-hk
2017年論文
@zh-mo
2017年論文
@zh-tw
2017年论文
@wuu
2017年论文
@zh
2017年论文
@zh-cn
name
The Role of Dipeptide Repeats in C9ORF72-Related ALS-FTD.
@en
The Role of Dipeptide Repeats in C9ORF72-Related ALS-FTD.
@nl
type
label
The Role of Dipeptide Repeats in C9ORF72-Related ALS-FTD.
@en
The Role of Dipeptide Repeats in C9ORF72-Related ALS-FTD.
@nl
prefLabel
The Role of Dipeptide Repeats in C9ORF72-Related ALS-FTD.
@en
The Role of Dipeptide Repeats in C9ORF72-Related ALS-FTD.
@nl
P2860
P356
P1476
The Role of Dipeptide Repeats in C9ORF72-Related ALS-FTD.
@en
P2093
Brian D Freibaum
P2860
P356
10.3389/FNMOL.2017.00035
P577
2017-02-13T00:00:00Z