Paroxysmal nocturnal hemoglobinuria: deficiency in factor H-like functions of the abnormal erythrocytes.
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Characterization of the complement sensitivity of paroxysmal nocturnal hemoglobinuria erythrocytes.Self-nonself discrimination by the complement system.Heightened complement sensitivity of acquired immunodeficiency syndrome lymphocytes related to diminished expression of decay-accelerating factor.Synthesis of aberrant decay-accelerating factor proteins by affected paroxysmal nocturnal hemoglobinuria leukocytesAltered expression of gangliosides in erythrocytes of paroxysmal nocturnal hemoglobinuriaInteractions of the platelets in paroxysmal nocturnal hemoglobinuria with complement. Relationship to defects in the regulation of complement and to platelet survival in vivo.Abnormality of glycophorin-alpha on paroxysmal nocturnal hemoglobinuria erythrocytes.Relationship between decay accelerating factor deficiency, diminished acetylcholinesterase activity, and defective terminal complement pathway restriction in paroxysmal nocturnal hemoglobinuria erythrocytesDistribution of decay-accelerating factor in the peripheral blood of normal individuals and patients with paroxysmal nocturnal hemoglobinuria.Decay-accelerating factor is present on paroxysmal nocturnal hemoglobinuria erythroid progenitors and lost during erythropoiesis in vitroDecay-accelerating factor is present on cultured human umbilical vein endothelial cells.Identification of the complement decay-accelerating factor (DAF) on epithelium and glandular cells and in body fluidsEnhanced reactive lysis of paroxysmal nocturnal hemoglobinuria erythrocytes. Studies on C9 binding and incorporation into high molecular weight complexes.Membrane-bound C4b interacts endogenously with complement receptor CR1 of human red cells.Deficiency of the homologous restriction factor in paroxysmal nocturnal hemoglobinuria.Decay-accelerating factor. Genetic polymorphism and linkage to the RCA (regulator of complement activation) gene cluster in humansDeficiency of lymphocyte function-associated antigen 3 (LFA-3) in paroxysmal nocturnal hemoglobinuria. Functional correlates and evidence for a phosphatidylinositol membrane anchor.Paroxysmal nocturnal hemoglobinuria and glycosyl phosphatidylinositol anchored proteins that regulate complement.Deficiency of an erythrocyte membrane protein with complement regulatory activity in paroxysmal nocturnal hemoglobinuria.Evasion of alternative complement pathway by Trypanosoma cruzi results from inefficient binding of factor B.Amelioration of lytic abnormalities of paroxysmal nocturnal hemoglobinuria with decay-accelerating factorAnti-Complement Treatment in Paroxysmal Nocturnal Hemoglobinuria: Where we Stand and Where we are Going.Accelerated decay of C3b to iC3b when C3b is bound to the Cryptococcus neoformans capsule.Paroxysmal nocturnal hemoglobinuria type III. Lack of an erythrocyte membrane protein restricting the lysis by C5b-9.Cell-surface regulation of the human alternative pathway of complement. Sheep but not rabbit erythrocytes express factor I-dependent cofactor activity.Hemolysis of human erythrocytes is a new bioactivity of gangliosides.Studies on the defect which causes absence of decay accelerating factor (DAF) from the peripheral blood cells of an individual with the Inab phenotype.Erythrocytes transfused into patients with SLE and haemolytic anaemia lose complement receptor type 1 from their cell surface
P2860
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P2860
Paroxysmal nocturnal hemoglobinuria: deficiency in factor H-like functions of the abnormal erythrocytes.
description
1983 nî lūn-bûn
@nan
1983年の論文
@ja
1983年論文
@yue
1983年論文
@zh-hant
1983年論文
@zh-hk
1983年論文
@zh-mo
1983年論文
@zh-tw
1983年论文
@wuu
1983年论文
@zh
1983年论文
@zh-cn
name
Paroxysmal nocturnal hemoglobi ...... of the abnormal erythrocytes.
@en
Paroxysmal nocturnal hemoglobi ...... of the abnormal erythrocytes.
@nl
type
label
Paroxysmal nocturnal hemoglobi ...... of the abnormal erythrocytes.
@en
Paroxysmal nocturnal hemoglobi ...... of the abnormal erythrocytes.
@nl
prefLabel
Paroxysmal nocturnal hemoglobi ...... of the abnormal erythrocytes.
@en
Paroxysmal nocturnal hemoglobi ...... of the abnormal erythrocytes.
@nl
P2093
P2860
P356
P1476
Paroxysmal nocturnal hemoglobi ...... of the abnormal erythrocytes.
@en
P2093
H J Müller-Eberhard
J S Trombold
M K Pangburn
R D Schreiber
P2860
P304
P356
10.1084/JEM.157.6.1971
P407
P577
1983-06-01T00:00:00Z