Purkinje cell calcium dysregulation is the cellular mechanism that underlies catecholaminergic polymorphic ventricular tachycardia
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Role of Cytosolic Calcium Diffusion in Murine Cardiac Purkinje CellsGenetics of sudden cardiac death syndromesTargeting intracellular calcium cycling in catecholaminergic polymorphic ventricular tachycardia: a theoretical investigation.Syncope and exercise-related ventricular tachycardia.The role of dye affinity in optical measurements of Cai(2+) transients in cardiac muscleIn situ confocal imaging in intact heart reveals stress-induced Ca(2+) release variability in a murine catecholaminergic polymorphic ventricular tachycardia model of type 2 ryanodine receptor(R4496C+/-) mutationA model of canine purkinje cell electrophysiology and Ca(2+) cycling: rate dependence, triggered activity, and comparison to ventricular myocytes.Isolation and characterization of embryonic stem cell-derived cardiac Purkinje cellsThe ionic bases of the action potential in isolated mouse cardiac Purkinje cellOptogenetic determination of the myocardial requirements for extrasystoles by cell type-specific targeting of ChannelRhodopsin-2.The RyR2-P2328S mutation downregulates Nav1.5 producing arrhythmic substrate in murine ventricles.Accelerated sinus rhythm prevents catecholaminergic polymorphic ventricular tachycardia in mice and in patients.Decreased RyR2 refractoriness determines myocardial synchronization of aberrant Ca2+ release in a genetic model of arrhythmia.Constitutive Intracellular Na+ Excess in Purkinje Cells Promotes Arrhythmogenesis at Lower Levels of Stress Than Ventricular Myocytes From Mice With Catecholaminergic Polymorphic Ventricular TachycardiaInositol 1, 4, 5-trisphosphate receptors and human left ventricular myocytesNovel protective effects of pulsed electromagnetic field ischemia/reperfusion injury rats.Purkinje-related arrhythmias part ii: polymorphic ventricular tachycardia and ventricular fibrillation.Electrophysiological patterning of the heart.Species-Dependent Mechanisms of Cardiac Arrhythmia: A Cellular Focus.Calcium Signaling and Cardiac Arrhythmias.Notch-Mediated Epigenetic Regulation of Voltage-Gated Potassium Currents.Evoked centripetal Ca(2+) mobilization in cardiac Purkinje cells: insight from a model of three Ca(2+) release regions.Conditional ablation and conditional rescue models for Casq2 elucidate the role of development and of cell type specific expression of Casq2 in the CPVT2 phenotype.Fates Aligned: Origins and Mechanisms of Ventricular Conduction System and Ventricular Wall Development.Ryanodine receptors
P2860
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P2860
Purkinje cell calcium dysregulation is the cellular mechanism that underlies catecholaminergic polymorphic ventricular tachycardia
description
2010 nî lūn-bûn
@nan
2010年の論文
@ja
2010年論文
@yue
2010年論文
@zh-hant
2010年論文
@zh-hk
2010年論文
@zh-mo
2010年論文
@zh-tw
2010年论文
@wuu
2010年论文
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2010年论文
@zh-cn
name
Purkinje cell calcium dysregul ...... orphic ventricular tachycardia
@en
Purkinje cell calcium dysregul ...... orphic ventricular tachycardia
@nl
type
label
Purkinje cell calcium dysregul ...... orphic ventricular tachycardia
@en
Purkinje cell calcium dysregul ...... orphic ventricular tachycardia
@nl
prefLabel
Purkinje cell calcium dysregul ...... orphic ventricular tachycardia
@en
Purkinje cell calcium dysregul ...... orphic ventricular tachycardia
@nl
P2093
P2860
P1433
P1476
Purkinje cell calcium dysregul ...... orphic ventricular tachycardia
@en
P2093
Justus Anumonwo
Michelle L Milstein
Silvia G Priori
Todd J Herron
P2860
P304
P356
10.1016/J.HRTHM.2010.06.010
P50
P577
2010-06-09T00:00:00Z