Mitochondrial dysfunction and apoptosis in myopathic mice with collagen VI deficiency. - Wikidata - awgldk - TriplyDB

Mitochondrial dysfunction and apoptosis in myopathic mice with collagen VI deficiency.

Mitochondrial dysfunction and apoptosis in myopathic mice with collagen VI deficiency.

http://www.wikidata.org/entity/Q44661085

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Three novel collagen VI chains, alpha4(VI), alpha5(VI), and alpha6(VI)Monoamine oxidase B prompts mitochondrial and cardiac dysfunction in pressure overloaded hearts Physical exercise stimulates autophagy in normal skeletal muscles but is detrimental for collagen VI-deficient muscles Cyclosporin A corrects mitochondrial dysfunction and muscle apoptosis in patients with collagen VI myopathies Collagen VI related muscle disorders The mitochondrial fission protein hFis1 requires the endoplasmic reticulum gateway to induce apoptosis The beneficial role of proteolysis in skeletal muscle growth and stress adaptation Role of Inflammation in Muscle Homeostasis and Myogenesis A TALEN-Exon Skipping Design for a Bethlem Myopathy Model in Zebrafish Remodeling of Mitochondrial Flashes in Muscular Development and Dystrophy in Zebrafish Photo-induction and automated quantification of reversible mitochondrial permeability transition pore opening in primary mouse myotubes Muscle-specific Drp1 overexpression impairs skeletal muscle growth via translational attenuation.Genetic evidence in the mouse solidifies the calcium hypothesis of myofiber death in muscular dystrophy Insights into the key roles of proteoglycans in breast cancer biology and translational medicine Hanging on for the ride: adhesion to the extracellular matrix mediates cellular responses in skeletal muscle morphogenesis and disease The OPA1-dependent mitochondrial cristae remodeling pathway controls atrophic, apoptotic, and ischemic tissue damage A novel deletion in the GTPase domain of OPA1 causes defects in mitochondrial morphology and distribution, but not in function COL4A1 mutations cause ocular dysgenesis, neuronal localization defects, and myopathy in mice and Walker-Warburg syndrome in humans A method for the direct identification of differentiating muscle cells by a fluorescent mitochondrial dye A mouse model for dominant collagen VI disorders: heterozygous deletion of Col6a3 Exon 16 Modulation of F0F1-ATP synthase activity by cyclophilin D regulates matrix adenine nucleotide levels Recent advances using zebrafish animal models for muscle disease drug discovery Phosphate is essential for inhibition of the mitochondrial permeability transition pore by cyclosporin A and by cyclophilin D ablation Selective actions of mitochondrial fission/fusion genes on metabolism-secretion coupling in insulin-releasing cells Correlated three-dimensional light and electron microscopy reveals transformation of mitochondria during apoptosis.Proteomics analysis of human skeletal muscle reveals novel abnormalities in obesity and type 2 diabetes.Collagen VI protects neurons against Abeta toxicity.Chronic inhibition of phosphodiesterase 5 with tadalafil attenuates mitochondrial dysfunction in type 2 diabetic hearts: potential role of NO/SIRT1/PGC-1α signaling.Monoamine oxidases as sources of oxidants in the heart Adipocyte-derived collagen VI affects early mammary tumor progression in vivo, demonstrating a critical interaction in the tumor/stroma microenvironment Human adipose-derived stem cell transplantation as a potential therapy for collagen VI-related congenital muscular dystrophy Distinct functions of junD in cardiac hypertrophy and heart failure Mechanical and electrophysiological properties of the sarcolemma of muscle fibers in two murine models of muscle dystrophy: col6a1-/- and mdx Zebrafish models of collagen VI-related myopathies A systems biology approach identifies molecular networks defining skeletal muscle abnormalities in chronic obstructive pulmonary disease Cancer stem cells from epithelial ovarian cancer patients privilege oxidative phosphorylation, and resist glucose deprivation.The intriguing regulators of muscle mass in sarcopenia and muscular dystrophy.Chronic treatment with long acting phosphodiesterase-5 inhibitor tadalafil alters proteomic changes associated with cytoskeletal rearrangement and redox regulation in Type 2 diabetic hearts.The collagen VI-related myopathies Ullrich congenital muscular dystrophy and Bethlem myopathy.Monoamine oxidase inhibition prevents mitochondrial dysfunction and apoptosis in myoblasts from patients with collagen VI myopathies.

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Mitochondrial dysfunction and apoptosis in myopathic mice with collagen VI deficiency.

http://www.wikidata.org/entity/Q44661085

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2003 nî lūn-bûn

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2003年の論文

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2003年学术文章

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2003年学术文章

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2003年学术文章

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2003年学术文章

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2003年学术文章

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2003年學術文章

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2003年學術文章

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name

Mitochondrial dysfunction and apoptosis in myopathic mice with collagen VI deficiency.

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Mitochondrial dysfunction and apoptosis in myopathic mice with collagen VI deficiency.

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type

label

Mitochondrial dysfunction and apoptosis in myopathic mice with collagen VI deficiency.

@en

Mitochondrial dysfunction and apoptosis in myopathic mice with collagen VI deficiency.

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prefLabel

Mitochondrial dysfunction and apoptosis in myopathic mice with collagen VI deficiency.

@en

Mitochondrial dysfunction and apoptosis in myopathic mice with collagen VI deficiency.

@nl

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Nature Genetics

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Mitochondrial dysfunction and apoptosis in myopathic mice with collagen VI deficiency

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Carlo Reggiani

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Dino Volpin

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Giorgio M Bressan

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Natascha Bergamin

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Paolo Bonaldo

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Patrizia Sabatelli

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William A Irwin

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367-371

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scholarly article

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10.1038/NG1270

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4

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35

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Luciano Merlini

Paola Braghetta

Marta Columbaro

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2003-11-16T00:00:00Z

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9001068

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14625552

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