alpha-keto acids accumulating in maple syrup urine disease stimulate lipid peroxidation and reduce antioxidant defences in cerebral cortex from young rats.
about
Branched-chain amino acids in metabolic signalling and insulin resistanceLens metabolomic profiling as a tool to understand cataractogenesis in Atlantic salmon and rainbow trout reared at optimum and high temperatureBrain-blood amino acid correlates following protein restriction in murine maple syrup urine disease.Profiling of oxidative stress in patients with inborn errors of metabolism.Oxidative stress in phenylketonuria: what is the evidence?Neurological damage in MSUD: the role of oxidative stress.New insights into the role of the branched-chain aminotransferase proteins in the human brain.Alloisoleucine differentiates the branched-chain aminoacidemia of Zucker and dietary obese ratsSerum Markers of Neurodegeneration in Maple Syrup Urine Disease.Intracerebroventricular administration of α-ketoisocaproic acid decreases brain-derived neurotrophic factor and nerve growth factor levels in brain of young rats.L-carnitine Prevents Oxidative Stress in the Brains of Rats Subjected to a Chemically Induced Chronic Model of MSUD.Investigation of inflammatory profile in MSUD patients: benefit of L-carnitine supplementation.Hepatocyte transplantation (HTx) corrects selected neurometabolic abnormalities in murine intermediate maple syrup urine disease (iMSUD).In vivo neuroprotective effect of L-carnitine against oxidative stress in maple syrup urine disease.Effect of leucine administration to female rats during pregnancy and lactation on oxidative stress and enzymes activities of phosphoryltransfer network in cerebral cortex and hippocampus of the offspring.Evaluation of dynamic thiol/disulphide homeostasis as a novel indicator of oxidative stress in maple syrup urine disease patients under treatment.Apoptotic signaling pathways induced by acute administration of branched-chain amino acids in an animal model of maple syrup urine disease.Evaluation of acetylcholinesterase in an animal model of maple syrup urine disease.Acute and long-term effects of intracerebroventricular administration of α-ketoisocaproic acid on oxidative stress parameters and cognitive and noncognitive behaviors.(1) H NMR-based metabolomics exploring urinary biomarkers correlated with proteinuria in focal segmental glomerulosclerosis: a pilot study.Impaired Hematopoiesis and Disrupted Monocyte/Macrophage Homeostasis in Mucopolysaccharidosis Type I Mice.Altered Redox Homeostasis in Branched-Chain Amino Acid Disorders, Organic Acidurias, and Homocystinuria.
P2860
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P2860
alpha-keto acids accumulating in maple syrup urine disease stimulate lipid peroxidation and reduce antioxidant defences in cerebral cortex from young rats.
description
2005 nî lūn-bûn
@nan
2005年の論文
@ja
2005年学术文章
@wuu
2005年学术文章
@zh
2005年学术文章
@zh-cn
2005年学术文章
@zh-hans
2005年学术文章
@zh-my
2005年学术文章
@zh-sg
2005年學術文章
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2005年學術文章
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name
alpha-keto acids accumulating ...... rebral cortex from young rats.
@en
alpha-keto acids accumulating ...... rebral cortex from young rats.
@nl
type
label
alpha-keto acids accumulating ...... rebral cortex from young rats.
@en
alpha-keto acids accumulating ...... rebral cortex from young rats.
@nl
prefLabel
alpha-keto acids accumulating ...... rebral cortex from young rats.
@en
alpha-keto acids accumulating ...... rebral cortex from young rats.
@nl
P2093
P1476
alpha-keto acids accumulating ...... erebral cortex from young rats
@en
P2093
Carlos Severo Dutra-Filho
Clóvis M D Wannmacher
César A Braun
Eduardo G Lissi
Giovanni K Zorzi
Moacir Wajner
P2860
P2888
P304
P356
10.1007/S11011-005-4152-8
P50
P577
2005-06-01T00:00:00Z