Accurate Dystrophin Quantification in Mouse Tissue; Identification of New and Evaluation of Existing Methods.

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A dystrophic Duchenne mouse model for testing human antisense oligonucleotides.Use of capillary Western immunoassay (Wes) for quantification of dystrophin levels in skeletal muscle of healthy controls and individuals with Becker and Duchenne muscular dystrophy.

P2860

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Accurate Dystrophin Quantification in Mouse Tissue; Identification of New and Evaluation of Existing Methods.

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http://www.wikidata.org/entity/Q51323375

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2016 nî lūn-bûn

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2016年の論文

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2016年学术文章

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2016年学术文章

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2016年学术文章

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2016年学术文章

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2016年学术文章

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2016年学术文章

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2016年學術文章

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2016年學術文章

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name

Accurate Dystrophin Quantifica ...... valuation of Existing Methods.

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Accurate Dystrophin Quantifica ...... valuation of Existing Methods.

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Accurate Dystrophin Quantifica ...... valuation of Existing Methods.

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Accurate Dystrophin Quantifica ...... valuation of Existing Methods.

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Accurate Dystrophin Quantifica ...... valuation of Existing Methods.

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Accurate Dystrophin Quantifica ...... valuation of Existing Methods.

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P1476

Accurate Dystrophin Quantifica ...... valuation of Existing Methods.

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Laura van Vliet

http://www.w3.org/2001/XMLSchema#string

Maaike van Putten

http://www.w3.org/2001/XMLSchema#string

Margriet Hulsker

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A sensitive, reproducible and objective immunofluorescence analysis method of dystrophin in individual fibers in samples from patients with duchenne muscular dystrophy

Dystrophin: the protein product of the Duchenne muscular dystrophy locus

Low dystrophin levels increase survival and improve muscle pathology and function in dystrophin/utrophin double-knockout mice

Function and genetics of dystrophin and dystrophin-related proteins in muscle.

The effects of low levels of dystrophin on mouse muscle function and pathology

Cytokine detection by antibody-based proximity ligation.

European Medicines Agency review of ataluren for the treatment of ambulant patients aged 5 years and older with Duchenne muscular dystrophy resulting from a nonsense mutation in the dystrophin gene.

Ataluren treatment of patients with nonsense mutation dystrophinopathy.

Age-dependent dystrophin loss and genetic reconstitution establish a molecular link between dystrophin and heart performance during aging.

Diagnosis and management of Duchenne muscular dystrophy, part 1: diagnosis, and pharmacological and psychosocial management.

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77-90

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scholarly article

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10.3233/JND-150126

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P478

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Annemieke Aartsma-Rus

Ingrid Verhaart

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2016-03-01T00:00:00Z

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27854205

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Accurate Dystrophin Quantification in Mouse Tissue; Identification of New and Evaluation of Existing Methods.

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P2860

P2860

Accurate Dystrophin Quantification in Mouse Tissue; Identification of New and Evaluation of Existing Methods.

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type

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P1433

P1476

P2093

P2860

P304

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P356

P433

P478

P50

P577

P698

P356

P1433

P1476

P2093

P2860

P304

P31

P356

P433

P478

P50

P577

P698