American Thoracic Society/European Respiratory Society statement: standards for the diagnosis and management of individuals with alpha-1 antitrypsin deficiency.
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Hereditary alpha-1-antitrypsin deficiency and its clinical consequencesAlpha-1 antitrypsin deficiency: a commonly overlooked cause of lung diseaseSERPINA2 is a novel gene with a divergent function from SERPINA1Genes and chronic obstructive pulmonary diseaseDeficient and Null Variants of SERPINA1 Are Proteotoxic in a Caenorhabditis elegans Model of α1-Antitrypsin DeficiencyExtracellular Vesicles in Chronic Obstructive Pulmonary DiseaseChallenges and Prospects for Alpha-1 Antitrypsin Deficiency Gene TherapyAlpha-1 antitrypsin deficiency targeted testing and augmentation therapy: a Canadian Thoracic Society clinical practice guidelineClinical utility gene card for: α-1-antitrypsin deficiencyAugmentation therapy for alpha-1 antitrypsin deficiency: towards a personalised approachFBG1 Is the Final Arbitrator of A1AT-Z DegradationMalfolded protein structure and proteostasis in lung diseases.Liver function in alpha-1-antitrypsin deficient individuals at 37 to 40 years of ageCausal and synthetic associations of variants in the SERPINA gene cluster with alpha1-antitrypsin serum levels.Alpha-1-antitrypsin augmentation therapy in deficient individuals enrolled in the Alpha-1 Foundation DNA and Tissue BankAlpha1-antitrypsin deficiency: forgotten etiology.Classifying married adults diagnosed with alpha-1 antitrypsin deficiency based on spousal communication patterns using latent class analysis: insights for interventionAmelioration of emphysema in mice through lentiviral transduction of long-lived pulmonary alveolar macrophages.Exogenous alpha 1-antitrypsin down-regulates SERPINA1 expressionSerum concentration of alpha-1 antitrypsin is significantly higher in colorectal cancer patients than in healthy controls.Hypersensitivity vasculitis with leukocytoclastic vasculitis associated with alpha-1-proteinase inhibitor.Pharmacokinetic comparability of Prolastin®-C to Prolastin® in alpha₁-antitrypsin deficiency: a randomized study.Long-term clinical outcomes following treatment with alpha 1-proteinase inhibitor for COPD associated with alpha-1 antitrypsin deficiency: a look at the evidence.Alpha-1-antitrypsin phenotypes in adult liver disease patients.Alpha-1 antitrypsin Pi*SZ genotype: estimated prevalence and number of SZ subjects worldwide.Chronic obstructive pulmonary disease: NHLBI Workshop on the Primary Prevention of Chronic Lung Diseases.Validation and development of an immunonephelometric assay for the determination of alpha-1 antitrypsin levels in dried blood spots from patients with COPD.Survival in severe alpha-1-antitrypsin deficiency (PiZZ).Determination of alpha-1 antitrypsin level in patients with severe asthma.Quantitative airway assessment on computed tomography in patients with alpha1-antitrypsin deficiency.Therapeutic efficacy of α-1 antitrypsin augmentation therapy on the loss of lung tissue: an integrated analysis of 2 randomised clinical trials using computed tomography densitometry.Hepatic progenitor cell proliferation and liver injury in α-1-antitrypsin deficiency.A review of augmentation therapy for alpha-1 antitrypsin deficiency.Reference and interpretive ranges for α(1)-antitrypsin quantitation by phenotype in adult and pediatric populations.Severe alpha-1 antitrypsin deficiency in composite heterozygotes inheriting a new splicing mutation QOMadridThe impact of social contexts in testing for alpha-1 antitrypsin deficiency: the roles of physicians and others.Improving the differential diagnosis of chronic obstructive pulmonary disease in primary care.The shapes of Z-α1-antitrypsin polymers in solution support the C-terminal domain-swap mechanism of polymerization.α1 Antitrypsin deficiency: current best practice in testing and augmentation therapy.Identification of a rare p.G320R alpha-1-antitrypsin variant in emphysema and lung cancer patients
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American Thoracic Society/European Respiratory Society statement: standards for the diagnosis and management of individuals with alpha-1 antitrypsin deficiency.
description
2003 nî lūn-bûn
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2003年の論文
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2003年学术文章
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2003年学术文章
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2003年学术文章
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2003年学术文章
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name
American Thoracic Society/Euro ...... lpha-1 antitrypsin deficiency.
@en
American Thoracic Society/Euro ...... lpha-1 antitrypsin deficiency.
@nl
type
label
American Thoracic Society/Euro ...... lpha-1 antitrypsin deficiency.
@en
American Thoracic Society/Euro ...... lpha-1 antitrypsin deficiency.
@nl
prefLabel
American Thoracic Society/Euro ...... lpha-1 antitrypsin deficiency.
@en
American Thoracic Society/Euro ...... lpha-1 antitrypsin deficiency.
@nl
P2860
P356
P1476
American Thoracic Society/Euro ...... lpha-1 antitrypsin deficiency.
@en
P2860
P304
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10.1164/RCCM.168.7.818
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P577
2003-10-01T00:00:00Z