Generation and characterization of a delta F508 cystic fibrosis mouse model. - Wikidata - awgldk - TriplyDB

Generation and characterization of a delta F508 cystic fibrosis mouse model.

Generation and characterization of a delta F508 cystic fibrosis mouse model.

http://www.wikidata.org/entity/Q52207066

about

Correctors (specific therapies for class II CFTR mutations) for cystic fibrosis Instability of the insertional mutation in CftrTgH(neoim)Hgu cystic fibrosis mouse model Epithelial Anion Transport as Modulator of Chemokine Signaling Animal Models of Cystic Fibrosis Pathology: Phenotypic Parallels and Divergences Cancer predisposition caused by elevated mitotic recombination in Bloom mice Modulation of Ca2+-activated Cl- secretion by basolateral K+ channels in human normal and cystic fibrosis airway epithelia Production of CFTR-null and CFTR-DeltaF508 heterozygous pigs by adeno-associated virus-mediated gene targeting and somatic cell nuclear transfer Pathophysiology of gene-targeted mouse models for cystic fibrosis Assessment of CFTR chloride channel openers in intact normal and cystic fibrosis murine epithelia Barriers to inhaled gene therapy of obstructive lung diseases: A review The role of the UPS in cystic fibrosis.DeltaF508 CFTR protein expression in tissues from patients with cystic fibrosis.Salmonella typhi uses CFTR to enter intestinal epithelial cells.Variation in MSRA modifies risk of neonatal intestinal obstruction in cystic fibrosis.Electrolyte transport in the mammalian colon: mechanisms and implications for disease.Hypersusceptibility of cystic fibrosis mice to chronic Pseudomonas aeruginosa oropharyngeal colonization and lung infection.The mousetrap: what we can learn when the mouse model does not mimic the human disease.Cystic fibrosis transmembrane conductance regulator is an epithelial cell receptor for clearance of Pseudomonas aeruginosa from the lung.Marked repression of CFTR mRNA in the transgenic Cftr(tm1kth) mouse model.Chloride channels in the kidney: lessons learned from knockout animals.Characteristic multiorgan pathology of cystic fibrosis in a long-living cystic fibrosis transmembrane regulator knockout murine model.Azithromycin reduces spontaneous and induced inflammation in DeltaF508 cystic fibrosis mice.Targeting genes for self-excision in the germ line Cystic fibrosis growth retardation is not correlated with loss of Cftr in the intestinal epithelium.Regulation of chemokine expression by NaCl occurs independently of cystic fibrosis transmembrane conductance regulator in macrophages.Processing and function of CFTR-DeltaF508 are species-dependent.Analysis of ClC-2 channels as an alternative pathway for chloride conduction in cystic fibrosis airway cells.In vivo activation of the cystic fibrosis transmembrane conductance regulator mutant deltaF508 in murine nasal epithelium Generation and characterization of a complete null estrogen receptor alpha mouse using Cre/LoxP technology.Lentiviral vector gene transfer to porcine airways.Novel role for CFTR in fluid absorption from the distal airspaces of the lung Cystic fibrosis mouse models.Comparative biology of cystic fibrosis animal models Feline immunodeficiency virus vectors persistently transduce nondividing airway epithelia and correct the cystic fibrosis defect What have we learned from mouse models for cystic fibrosis?Generation of a conditional null allele for Cftr in mice.Animal models of chronic lung infection with Pseudomonas aeruginosa: useful tools for cystic fibrosis studies.Pathophysiological basis of liver disease in cystic fibrosis employing a DeltaF508 mouse model Impaired estrogen feedback and infertility in female mice with pituitary-specific deletion of estrogen receptor alpha (ESR1).Animal models of human disease for gene therapy

P2860

Q24200710-CA550B5B-531C-499E-A3D1-81CD93EE933F Q24802906-E0F9C793-AB30-413F-AC9B-9516B933F681 Q26744381-4AB14F76-1E32-4EDD-938C-98B64616C672 Q26747210-BB552E2D-C826-430E-9CE8-725ED21F3126 Q28139170-5215E439-162A-4084-AFB1-9648FFD24BFB Q28213143-85E8524A-5989-48FE-A1B5-067F1B7FDE7F Q28271767-18B7E26D-7289-4DAF-AFFA-3C09FFF3391D Q28295602-AF7C7164-C127-4808-B47C-2793BED6D7FC Q28346466-D3B7B62A-8449-45E8-A723-C53076C06CC8 Q29248141-786E98D9-033C-41E4-8E9F-A1CBD5858D7F Q33307871-EFB19013-5EF8-4C36-AD86-F196E0478D16 Q33854446-20F3601E-2317-420C-B442-050F3D17DD3C Q34066552-F76ED955-38EC-4887-81D5-31CD6E969CBA Q34205956-E2637B13-7032-4B05-8ED1-384C6750DE65 Q34482550-5A20304B-92AF-4624-A100-ACA8EBFA96D2 Q34531184-D1DC0715-662F-44BA-9D49-A50223746EA1 Q34578759-A520CCDE-DD15-45BE-99B7-02FA00BA95C2 Q34743353-80581F1A-4304-4138-AFC8-AD2D8603C737 Q34989078-328046F6-2143-4632-ABC3-C60DEC968B8F Q34993939-B79FC5F7-D50E-4458-AEBF-05699042E730 Q35097413-9F947F37-1478-422B-AD71-7D8FB7D97D39 Q35132254-0EC17A24-947C-430A-8EF0-E6C1B711F357 Q35199729-8B4B9812-5CBA-4032-BD80-3D721BCA6A85 Q35216745-7C81FE4F-5314-4139-A512-53693D9E6FC3 Q35221848-C5FF6668-752D-43E9-8442-E8DCBD0F350B Q35991100-B5204E80-352E-4DAA-9D2B-04BC36695C60 Q36011771-C5329EE2-A5DA-43AF-9D3D-950181A52AA2 Q36051784-06F16106-3968-400D-B947-A0962735C886 Q36418639-25C56624-D0CF-42F9-8983-3D8660A0D011 Q36438300-73F94021-BA77-4A7C-AA40-B583B2B81AE7 Q36445092-6089C44B-B430-47A9-9A83-6E267A151997 Q36556391-4F6D9EAB-E447-410E-BF39-1A3D02B71E11 Q36744020-A2500E90-C790-4601-993C-70F0C33DC251 Q36807130-993EDB5E-0088-4EA7-A175-97CCC1BAB483 Q36874346-B57A5962-EC04-4447-8865-CD57C0763DDC Q37263623-9C636B77-9BA7-45F8-8AA5-E90B399547E4 Q37265316-A4189E91-5057-4968-9CB0-32BFA34E2348 Q37269561-FFBE4214-CA88-4995-997E-3CC02875738C Q37318643-566079E9-EA81-45DA-8EE7-EF1AE17DEF24 Q37352252-C1916B5D-E12C-4E98-AC1C-C31A4B050A74

P2860

Generation and characterization of a delta F508 cystic fibrosis mouse model.

http://www.wikidata.org/entity/Q52207066

description

1995 nî lūn-bûn

@nan

1995年の論文

@ja

1995年学术文章

@wuu

1995年学术文章

@zh

1995年学术文章

@zh-cn

1995年学术文章

@zh-hans

1995年学术文章

@zh-my

1995年学术文章

@zh-sg

1995年學術文章

@yue

1995年學術文章

@zh-hant

name

Generation and characterization of a delta F508 cystic fibrosis mouse model.

@en

Generation and characterization of a delta F508 cystic fibrosis mouse model.

@nl

type

label

Generation and characterization of a delta F508 cystic fibrosis mouse model.

@en

Generation and characterization of a delta F508 cystic fibrosis mouse model.

@nl

prefLabel

Generation and characterization of a delta F508 cystic fibrosis mouse model.

@en

Generation and characterization of a delta F508 cystic fibrosis mouse model.

@nl

P1433

Q52207066-A7156321-FE2F-4245-8C05-4EABD4F8A761

P1476

Q52207066-386B1EDA-0396-4DCC-933C-2FD5B2AA3050

P2093

Q52207066-15005B3E-04B4-48F8-BB64-A60EAE347A87

Q52207066-24578F61-C6B1-489F-B6B3-E6B672915ABF

Q52207066-2C9D6569-11C7-438A-86FD-9E9DC7634281

Q52207066-3599CBBE-0FC8-4E0B-AB74-D334D729CD5E

Q52207066-5C0FC7C3-E99F-497B-8CA8-579A80AAE689

Q52207066-60F4F676-1962-4C0C-A353-1496FB3F8925

Q52207066-708D0580-67B9-488B-AB75-E5E4C4672B78

Q52207066-B06AD9D7-E6EB-41C6-AB1B-D8DB3C1275F2

Q52207066-F47E89D9-DC32-45B7-A0DC-526102EF142C

P2860

Q52207066-0CDD14D5-436B-46D1-B418-9B7C00AE3381

Q52207066-0EA8DBAA-9AC3-4AA7-B4F7-B3D776682C44

Q52207066-1EDCD27B-8CE3-428D-9BA6-D7E03A5B2E59

Q52207066-555091D9-E89E-4F07-91BF-753C8CBB226B

Q52207066-56BDA216-DBB8-4EBA-8087-D272BFC37254

Q52207066-68FBDDCC-BF26-4C10-AA9C-31AAB499B139

Q52207066-6C9C2838-5851-450B-8529-4AAA77E22758

Q52207066-907A0645-9C7E-45F7-96AE-2FB1F2A2045B

Q52207066-90E0BEAE-9537-4206-92FF-A45ADA5C600E

Q52207066-D44E8378-8B95-479A-B8EE-A0781094FA85

P2888

Q52207066-FF3DEB04-57D9-4DFD-BD8E-9C6C2CFDF87E

P304

Q52207066-878C1FDB-B6F4-4FB5-B3CB-1FB3857A3A80

P31

Q52207066-9F9D1903-313A-4EB7-A81E-05F989A51B3D

P356

Q52207066-5C9111FA-7169-4772-9269-F8749697AF79

P407

Q52207066-90E715AD-D0D7-472E-AB2E-9F005CC9E799

P433

Q52207066-F1D6C3CE-D6D6-4525-A977-1EA506295D2E

P478

Q52207066-9D39026B-8F51-4676-B2D6-C6670BF2A152

P50

Q52207066-D5C35467-2141-45DD-B901-55B5203E5830

P577

Q52207066-206D6A55-3CCB-47B2-BFF9-FB759E1A89CD

P5875

Q52207066-50F6EE28-ED90-4714-800A-2DEA70B46CFD

P698

Q52207066-09E3C371-8CFF-486E-9185-42809F9C2817

P921

Q52207066-42B08DDE-0C62-402A-B8BE-AD18237E4869

P356

P1433

Nature Genetics

P1476

Generation and characterization of a delta F508 cystic fibrosis mouse model.

@en

P2093

Anderson JR

http://www.w3.org/2001/XMLSchema#string

Cheng SH

http://www.w3.org/2001/XMLSchema#string

Colledge WH

http://www.w3.org/2001/XMLSchema#string

Cuthbert AW

http://www.w3.org/2001/XMLSchema#string

Evans MJ

http://www.w3.org/2001/XMLSchema#string

Jiang C

http://www.w3.org/2001/XMLSchema#string

MacVinish LJ

http://www.w3.org/2001/XMLSchema#string

Ratcliff R

http://www.w3.org/2001/XMLSchema#string

Southern KW

http://www.w3.org/2001/XMLSchema#string

P2860

The genetic advantage hypothesis in cystic fibrosis heterozygotes: a murine study

Single-Step Method of RNA Isolation by Acid Guanidinium Thiocyanate–Phenol–Chloroform Extraction

Correction of the ion transport defect in cystic fibrosis transgenic mice by gene therapy

A potential animal model for Lesch-Nyhan syndrome through introduction of HPRT mutations into mice

Purification and functional reconstitution of the cystic fibrosis transmembrane conductance regulator (CFTR).

The cystic fibrosis mutation (delta F508) does not influence the chloride channel activity of CFTR.

Efficiency of gene transfer for restoration of normal airway epithelial function in cystic fibrosis.

Defective intracellular transport and processing of CFTR is the molecular basis of most cystic fibrosis.

Inefficient gene transfer by adenovirus vector to cystic fibrosis airway epithelia of mice and humans.

Processing of mutant cystic fibrosis transmembrane conductance regulator is temperature-sensitive.

P2888

P304

445-452

http://www.w3.org/2001/XMLSchema#string

P31

scholarly article

P356

10.1038/NG0895-445

http://www.w3.org/2001/XMLSchema#string

P407

P433

4

http://www.w3.org/2001/XMLSchema#string

P478

10

http://www.w3.org/2001/XMLSchema#string

P50

Benjamin S Abella

P577

1995-08-01T00:00:00Z

http://www.w3.org/2001/XMLSchema#dateTime

P5875

15652610

http://www.w3.org/2001/XMLSchema#string

P698

7545494

http://www.w3.org/2001/XMLSchema#string

P921

cystic fibrosis