Expression of cystic fibrosis transmembrane conductance regulator corrects defective chloride channel regulation in cystic fibrosis airway epithelial cells
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Taking stock of gene therapy for cystic fibrosisPathophysiology of gene-targeted mouse models for cystic fibrosisExpression and regulation of the cystic fibrosis gene during rat liver regenerationProduct review. New mammalian expression vectorsRectal forceps biopsy procedure in cystic fibrosis: technical aspects and patients perspective for clinical trials feasibility.Lack of CFTR in skeletal muscle predisposes to muscle wasting and diaphragm muscle pump failure in cystic fibrosis miceDisruption of interleukin-1β autocrine signaling rescues complex I activity and improves ROS levels in immortalized epithelial cells with impaired cystic fibrosis transmembrane conductance regulator (CFTR) function.Proteomic identification of calumenin as a G551D-CFTR associated protein.An ABC-transporter from Streptomyces longisporoflavus confers resistance to the polyether-ionophore antibiotic tetronasin.Uncoupling substrate transport from ATP hydrolysis in the Escherichia coli maltose transporter.The mitochondrial complex I activity is reduced in cells with impaired cystic fibrosis transmembrane conductance regulator (CFTR) function.Cystic fibrosis transmembrane conductance regulator with a shortened R domain rescues the intestinal phenotype of CFTR-/- mice.Functional apical large conductance, Ca2+-activated, and voltage-dependent K+ channels are required for maintenance of airway surface liquid volume.Efficient intratracheal delivery of airway epithelial cells in mice and pigsThe phenotypic consequences of CFTR mutations.Ion channel activity and transmembrane signaling in lymphocytes.Altered protein folding may be the molecular basis of most cases of cystic fibrosis.Concepts and strategies for human gene therapy.A role for two-pore K⁺ channels in modulating Na⁺ absorption and Cl⁻ secretion in normal human bronchial epithelial cellsIn vivo activation of the cystic fibrosis transmembrane conductance regulator mutant deltaF508 in murine nasal epitheliumTargeted Integration of a Super-Exon into the CFTR Locus Leads to Functional Correction of a Cystic Fibrosis Cell Line Model.Efficient expression of CFTR function with adeno-associated virus vectors that carry shortened CFTR genes.CFTR mediates bicarbonate-dependent activation of miR-125b in preimplantation embryo development.In silico search for modifier genes associated with pancreatic and liver disease in Cystic FibrosisInfluence of the cystic fibrosis transmembrane conductance regulator on expression of lipid metabolism-related genes in dendritic cellsCystic fibrosis transmembrane conductance regulator and caveolin-1 regulate epithelial cell internalization of Pseudomonas aeruginosa.Intrinsic predisposition of naïve cystic fibrosis T cells to differentiate towards a Th17 phenotype.Modulation of Treg function improves adenovirus vector-mediated gene expression in the airway.Vaccinia virus: a tool for research and vaccine development.Targeting F508del-CFTR to develop rational new therapies for cystic fibrosis.Proteases, cystic fibrosis and the epithelial sodium channel (ENaC).Detrimental effects of secondhand smoke exposure on infants with cystic fibrosis.Cystic fibrosis: need for mass deployable screening methods.Progress towards next-generation therapeutics for cystic fibrosis.Quantitative expression patterns of multidrug-resistance P-glycoprotein (MDR1) and differentially spliced cystic-fibrosis transmembrane-conductance regulator mRNA transcripts in human epithelia.Personalized medicine for cystic fibrosis: establishing human model systems.Serum Phospholipid Fatty Acid Composition in Cystic Fibrosis Patients with and without Liver Cirrhosis.Altering intracellular pH reveals the kinetic basis of intraburst gating in the CFTR Cl- channel.The CF-modifying gene EHF promotes p.Phe508del-CFTR residual function by altering protein glycosylation and trafficking in epithelial cells.Impact of gene editing on the study of cystic fibrosis.
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Expression of cystic fibrosis transmembrane conductance regulator corrects defective chloride channel regulation in cystic fibrosis airway epithelial cells
description
article publié dans la revue scientifique Nature
@fr
scientific article published in Nature
@en
wetenschappelijk artikel
@nl
наукова стаття, опублікована в Nature у вересні 1990
@uk
name
Expression of cystic fibrosis ...... brosis airway epithelial cells
@en
Expression of cystic fibrosis ...... brosis airway epithelial cells
@nl
type
label
Expression of cystic fibrosis ...... brosis airway epithelial cells
@en
Expression of cystic fibrosis ...... brosis airway epithelial cells
@nl
prefLabel
Expression of cystic fibrosis ...... brosis airway epithelial cells
@en
Expression of cystic fibrosis ...... brosis airway epithelial cells
@nl
P2093
P356
P1433
P1476
Expression of cystic fibrosis ...... brosis airway epithelial cells
@en
P2093
Anderson MP
Gregory RJ
Jefferson DM
Klinger KW
P2888
P304
P356
10.1038/347358A0
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P577
1990-09-01T00:00:00Z
P6179
1035172743