LRPPRC is necessary for polyadenylation and coordination of translation of mitochondrial mRNAs
about
Copper supplementation restores cytochrome c oxidase assembly defect in a mitochondrial disease model of COA6 deficiencyMitochondrial cytochrome c oxidase deficiencyRole of Energy Metabolism in the Brown Fat Gene ProgramThe human mitochondrial transcriptome and the RNA-binding proteins that regulate its expressionAccessorizing the human mitochondrial transcription machineryLoss of the RNA-binding protein TACO1 causes late-onset mitochondrial dysfunction in miceNSUN4 is a dual function mitochondrial protein required for both methylation of 12S rRNA and coordination of mitoribosomal assemblyStructural basis for the modular recognition of single-stranded RNA by PPR proteinsIdentification of LACTB2, a metallo-β-lactamase protein, as a human mitochondrial endoribonucleaseMitochondrial ribosomal RNA (rRNA) methyltransferase family members are positioned to modify nascent rRNA in foci near the mitochondrial DNA nucleoidTranscription-independent role for human mitochondrial RNA polymerase in mitochondrial ribosome biogenesisImbalanced OPA1 processing and mitochondrial fragmentation cause heart failure in miceAnalysis of 953 human proteins from a mitochondrial HEK293 fraction by complexome profilingp32/gC1qR is indispensable for fetal development and mitochondrial translation: importance of its RNA-binding abilityMutation in MRPS34 compromises protein synthesis and causes mitochondrial dysfunctionOverexpression of the mitochondrial methyltransferase TFB1M in the mouse does not impact mitoribosomal methylation status or hearing.Impaired complex IV activity in response to loss of LRPPRC function can be compensated by mitochondrial hyperfusion.The Schizosaccharomyces pombe PPR protein Ppr10 associates with a novel protein Mpa1 and acts as a mitochondrial translational activator.A biochemical framework for eIF4E-dependent mRNA export and nuclear recycling of the export machinery.Simultaneous processing and degradation of mitochondrial RNAs revealed by circularized RNA sequencingA combinatorial amino acid code for RNA recognition by pentatricopeptide repeat proteins.Knockdown of the cellular protein LRPPRC attenuates HIV-1 infection.A human mitochondrial poly(A) polymerase mutation reveals the complexities of post-transcriptional mitochondrial gene expression.MTERF3 regulates mitochondrial ribosome biogenesis in invertebrates and mammals.The respiratory chain supercomplex organization is independent of COX7a2l isoforms.Drosophila melanogaster LRPPRC2 is involved in coordination of mitochondrial translationTissue-specific responses to the LRPPRC founder mutation in French Canadian Leigh SyndromeFunctional genomic analysis of human mitochondrial RNA processing.Energizing Genetics and Epi-genetics: Role in the Regulation of Mitochondrial Function.NOA1, a novel ClpXP substrate, takes an unexpected nuclear detour prior to mitochondrial import.OXPHOS-Mediated Induction of NAD+ Promotes Complete Oxidation of Fatty Acids and Interdicts Non-Alcoholic Fatty Liver Disease.Mitochondrial Diseases Part II: Mouse models of OXPHOS deficiencies caused by defects in regulatory factors and other components required for mitochondrial function.Simultaneous DNA and RNA Mapping of Somatic Mitochondrial Mutations across Diverse Human Cancers.Impaired Mitochondrial Energy Production Causes Light-Induced Photoreceptor Degeneration Independent of Oxidative Stress.SLIRP Regulates the Rate of Mitochondrial Protein Synthesis and Protects LRPPRC from Degradation.Cross-strand binding of TFAM to a single mtDNA molecule forms the mitochondrial nucleoid.Mitochondrial transcript maturation and its disordersA Combination of Culture Conditions and Gene Expression Analysis Can Be Used to Investigate and Predict hES Cell Differentiation Potential towards Male Gonadal CellsThe Human Mitochondrial DEAD-Box Protein DDX28 Resides in RNA Granules and Functions in Mitoribosome AssemblySUV3 helicase is required for correct processing of mitochondrial transcripts.
P2860
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P248
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P2860
LRPPRC is necessary for polyadenylation and coordination of translation of mitochondrial mRNAs
description
2012 nî lūn-bûn
@nan
2012 թուականի Յունուարին հրատարակուած գիտական յօդուած
@hyw
2012 թվականի հունվարին հրատարակված գիտական հոդված
@hy
2012年の論文
@ja
2012年論文
@yue
2012年論文
@zh-hant
2012年論文
@zh-hk
2012年論文
@zh-mo
2012年論文
@zh-tw
2012年论文
@wuu
name
LRPPRC is necessary for polyad ...... slation of mitochondrial mRNAs
@ast
LRPPRC is necessary for polyad ...... slation of mitochondrial mRNAs
@en
LRPPRC is necessary for polyad ...... slation of mitochondrial mRNAs
@en-gb
LRPPRC is necessary for polyad ...... slation of mitochondrial mRNAs
@nl
type
label
LRPPRC is necessary for polyad ...... slation of mitochondrial mRNAs
@ast
LRPPRC is necessary for polyad ...... slation of mitochondrial mRNAs
@en
LRPPRC is necessary for polyad ...... slation of mitochondrial mRNAs
@en-gb
LRPPRC is necessary for polyad ...... slation of mitochondrial mRNAs
@nl
prefLabel
LRPPRC is necessary for polyad ...... slation of mitochondrial mRNAs
@ast
LRPPRC is necessary for polyad ...... slation of mitochondrial mRNAs
@en
LRPPRC is necessary for polyad ...... slation of mitochondrial mRNAs
@en-gb
LRPPRC is necessary for polyad ...... slation of mitochondrial mRNAs
@nl
P2093
P2860
P50
P921
P3181
P356
P1433
P1476
LRPPRC is necessary for polyad ...... slation of mitochondrial mRNAs
@en
P2093
Ana Bratic
Benedetta Ruzzenente
Chan Bae Park
Claes M Gustafsson
Rolf Wibom
Volker Zickermann
P2860
P304
P3181
P356
10.1038/EMBOJ.2011.392
P407
P50
P577
2012-01-18T00:00:00Z